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1. 抗糸球体基底膜疾患（グッドパスチャー病）：発症機序、臨床症状、診断anti gbm goodpasture disease pathogenesis clinical manifestations and diagnosis [show details]
… for anti-GBM and anti-myeloperoxidase (MPO-ANCA) and has features of concurrent vasculitis . Other variants of atypical anti-GBM disease have been reported. The presentation of anti-GBM disease is similar …
2. Anti-GBM (Goodpasture) disease: Treatment and prognosisanti gbm goodpasture disease treatment and prognosis [show details]
… of patients with biopsy-proven anti-GBM disease may have undetectable circulating anti-GBM antibodies due to false-negative testing. If the suspicion for anti-GBM disease is high in such patients based …
3. 抗GBM病（グッドパスチャー症候群）：移植後の再発anti gbm goodpasture disease recurrence after transplantation [show details]
… recurrent anti-GBM disease in the literature . A related phenomenon is the development of de novo anti-GBM disease in patients with Alport syndrome (also known as Alport posttransplant anti-GBM nephritis) …
4. 急速進行性（半月形）糸球体腎炎の分類および治療の概要overview of the classification and treatment of rapidly progressive crescentic glomerulonephritis [show details]
… (as seen with hydralazine). Some patients have features of both ANCA-positive RPGN and anti-GBM disease. This has also been called "double-antibody" positive disease. Other ANCA-positive crescentic …
5. アルポート症候群（遺伝性腎炎）の臨床症状、診断、治療clinical manifestations diagnosis and treatment of alport syndrome hereditary nephritis [show details]
… predominant target of anti-GBM antibodies is the alpha-3(IV) chain . Patients with autosomal dominant Alport syndrome do not appear to be at increased risk for de novo anti-GBM disease after kidney transplantation …

Japanese Journal

日本のガイドラインと世界のガイドライン急速進行性糸球体腎炎の治療 (第5土曜特集腎臓病のすべて) -- (腎臓病各論 : 診断とエビデンスに基づいた治療)

臼井丈一,山縣邦弘
医学のあゆみ 249(9), 812-816, 2014-05-31
NAID 40020071497

急速進行性糸球体腎炎

臼井丈一,山縣邦弘
日本内科学会雑誌 103(10), 2587-2593, 2014
急速進行性糸球体腎炎（rapidly progressive glomerulonephritis：RPGN）は予後不良な腎不全症候群であり，本来数多くの原因疾患が含まれる．典型的なRPGNの病態は腎血管炎であり，原因疾患として抗好中球細胞質抗体（anti-neutrophil cytoplasmic antibody：ANCA）関連血管炎と抗糸球体基底膜（glomerular basement …
NAID 130005102716

抗GBM病診療の実際 (第1土曜特集血管炎の診断と治療 : 新分類CHCC2012に沿って) -- (小型血管炎)

山縣邦弘
医学のあゆみ 246(1), 59-64, 2013-07-06
NAID 40019681692

「血管炎」

　　[★]

英: angiitis
関: 脈管炎 vasculitis　vasculitides、血管内膜炎、血管炎症候群

分類

CHCC2012

large vessel vasculitis LVV 大型血管炎	Takayasu arteritis TAK 高安動脈炎
	giant cell arteritis GCA 巨細胞性動脈炎
medium vessel vasculitis MVV 中型血管炎	polyarteritis nodosa PAN 結節性多発動脈炎
	Kawasaki disease KD 川崎病
small vessel vasculitis SVV 小型血管炎	antineutrophil cytoplasmic antibody-associated vasculitis AAV 抗好中球細胞質抗体関連血管炎	microscopic polyangiitis MPA 顕微鏡的多発血管炎
		granulomatosis with polyangiitis GPA 多発血管炎性肉芽腫症(Wegener肉芽腫症)
		eosinophilic granulomatosis with polyangiitis EGPA 好酸球性多発血管炎性肉芽腫症(Churg-Strauss症候群)
	immune complex SVV 免疫複合体性小型血管炎	anti-glomerular basement membrane disease 抗糸球体基底膜抗体病(抗GBM病)
		cryoglobulinemic vasculitis CV クリオグロブリン血症性血管炎
		IgA vasculitis IgAV IgA血管炎(Henoch-Schonlein紫斑病)
		hypocomplementemic urticarial vasculitis HUV 低補体血症性蕁麻疹様血管炎(抗C1q血管炎)
variable vessel vasculitis VVV 多様な血管を侵す血管炎	Behcet's disease BD Behcet病
	Cogan's syndrome CS Cogan症候群
single-organ vasculitis SOV 単一臓器血管炎	cutaneous leukocytoclastic angiitis 皮膚白血球破砕性血管炎
	cutaneous arteritis 皮膚動脈炎
	primary central nervous system vasculitis 原発性中枢神経系血管炎
	isolated aortitis 限局性大動脈炎
vasculitis associated with systemic disease 全身性疾患関連血管炎	lupus vasculitis ループス血管炎
	rheumatoid vasculitis リウマトイド血管炎
	sarcoid vasculitis サルコイド血管炎
vasculitis associated with probable etiology 推定病因を有する血管炎	hepatitis C virus-associated cryoglobulinemic vasculitis C型肝炎ウイルス関連クリオグロブリン血症性血管炎
	hepatitis B virus-associated vasculitis B型肝炎ウイルス関連血管炎
	syphilis-associated aortitis 梅毒関連大動脈炎
	drug-associated immune complex vasculitis 薬剤関連免疫複合体性血管炎
	drug-associated ANCA-associated vasculitis 薬剤関連ANCA関連血管炎
	cancer-associated vasculitis がん関連血管炎