総肺静脈還流異常症 TAPVR
WordNet
- submit (a report, etc.) to someone in authority; "submit a bill to a legislative body"
- the income or profit arising from such transactions as the sale of land or other property; "the average return was about 5%" (同)issue, take, takings, proceeds, yield, payoff
- a coming to or returning home; "on his return from Australia we gave him a welcoming party" (同)homecoming
- a reciprocal group action; "in return we gave them as good as we got" (同)paying back, getting even
- (American football) the act of running back the ball after a kickoff or punt or interception or fumble
- a tennis stroke that sends the ball back to the other player; "he won the point on a cross-court return"
- the act of going back to a prior location; "they set out on their return to the base camp"
- the occurrence of a change in direction back in the opposite direction (同)coming back
- bring back to the point of departure (同)take_back, bring back
- go or come back to place, condition, or activity where one has been before; "return to your native land"; "the professor returned to his teaching position after serving as Dean"
- make a return; "return a kickback"
- return in kind; "return a compliment"; "return her love"
- return to a previous position; in mathematics; "The point returned to the interior of the figure"
- determine the sum of; "Add all the people in this town to those of the neighboring town" (同)tot, tot up, sum, sum_up, summate, tote up, add, add together, tally, add up
- damage beyond the point of repair; "My son totaled our new car"; "the rock star totals his guitar at every concert"
- add up in number or quantity; "The bills amounted to $2,000"; "The bill came to $2,000" (同)number, add up, come, amount
- deviating from the general or common order or type; "advanced forms of life may be anomalous in the universe"
- a small amount (especially of a drink); "a tot of rum"
- of or contained in or performing the function of the veins; "venous inflammation"; "venous blood as contrasted with arterial blood"; "venous circulation"
PrepTutorEJDIC
- (…から元の場所・状態などに)『帰る』,戻る《+from+名+to+『名』》 / 再び起こる,再発する / (元の持ち主・場所・状態に)…‘を'『返す』,戻す《+『名』+『to』+『名』》 / (同じようなやり方で)(…に対して)…‘を'『お返しする』,…‘で'こたえる《+『名』+『for』+『名』》 / …‘を'公式に報告する,答申する / 〈利子・利益など〉‘を'生む,生ずる / (国会議員などに)…‘を'選出する / 《しばしば引用節を従えて》…‘と'言葉を返す,返答する / 〈C〉(…から…べ)『帰って来ること』,帰還《+『from』+『名』+『to』+『名』》 / 〈U〉〈C〉(…が)再び起ること(来ること);(病気の)再発《+『of』+『名』》 / 〈U〉(…を)戻すこと,(…の)返却《+『fo』+『名』》 / 〈U〉〈C〉(…に対する)返礼,返報《+『for』+『名』》 / 〈C〉公式の報告[書],答申,(所得の)申告 / 〈C〉《しばしば複数形で》収入;利潤 / 《英》(国会議員などの)選挙 / 《米》『帰りの』;《英》往復の(《米》round・trip)) / 返しの,返報の
- 『総計の』,全体の / 『全くの』,完全な(absolute) / 『合計』,総額,総数,総量(sum) / …‘を'合計する / 合計…‘に'なる,総額が…‘に'のぼる(amount to)
- 変則的な(irregular) / 異常な(abnormal)
- 幼児,小児 / (特に酒類の)少量,一杯,一口
- …‘を'合計する《+up+名,+名+up》 / 合計(…に)なる《+up to+名》
- 静脈[血]の / 葉脈の多い
UpToDate Contents
全文を閲覧するには購読必要です。 To read the full text you will need to subscribe.
English Journal
- Scimitar syndrome in association with intrapulmonary sequestration.
- Gonzalez M, Bize P, Ris HB, Krueger T.SourceService of Thoracic and Vascular Surgery, Centre Hospitalier Universitaire Vaudois Lausanne, Switzerland.
- European journal of cardio-thoracic surgery : official journal of the European Association for Cardio-thoracic Surgery.Eur J Cardiothorac Surg.2011 Jul;40(1):273. Epub 2011 Jan 11.
- PMID 21227712
- Early Outcomes of Primary Sutureless Repair of the Pulmonary Veins.
- Azakie A, Lavrsen MJ, Johnson NC, Sapru A.SourceUCSF Benioff Children's Hospital, University of California-San Francisco, San Francisco, California; Department of Surgery, University of California-San Francisco, San Francisco, California; Department of Pediatrics, University of California-San Francisco, San Francisco, California.
- The Annals of thoracic surgery.Ann Thorac Surg.2011 Jun 24. [Epub ahead of print]
- BACKGROUND: The "sutureless" repair technique has improved outcomes for post-repair pulmonary vein (PV) stenosis. The purpose of this study is to determine the early outcomes of primary sutureless repair of pulmonary venoocclusive disease in infants with congenital PV stenosis-hypoplasia or PVs at h
- PMID 21704970
Japanese Journal
- 総肺静脈還流異常症(TAPVR) (特集 これが大切! 1カ月以内の新生児疾患) -- (見落としてはならない重症疾患・対応に迷う疾患)
- 米坂 勧
- 日本小児循環器学会雑誌 = Acta cardiologica paediatrica Japonica 26(1), 83-84, 2010-01-01
- NAID 10026282028
Related Links
- Total anomalous pulmonary venous connection (TAPVC), also known as total anomalous pulmonary venous drainage (TAPVD) and total anomalous pulmonary venous return (TAPVR), is a rare cyanotic congenital heart defect ( CHD) in which ...
- Total anomalous pulmonary venous return is a heart disease that is present at birth (congenital heart disease) in which none of the four veins that take blood from the lungs to the heart is attached to the left atrium (left upper chamber of the ...
★リンクテーブル★
[★]
- 英
- total anomalous pulmonary venous connection TAPVC、total anomalous pulmonary venous return TAPVR
- 同
- 総肺静脈還流異常
- 関
- 肺静脈還流異常、部分的肺静脈還流異常、先天性肺静脈還流異常、三日月刀症候群
- チアノーゼ性心疾患
[show details]
- NSU.387
まとめ
- 先天的な心奇形であって、左心房に還流すべき肺静脈血が右心系に流入する病態である。生存に心房中隔欠損か卵円孔開存が必要であり、病態によっては肺静脈閉塞による肺うっ血を来す。右心系の容量負荷により右室肥大、不完全右室ブロックをきたす。チアノーゼ性心疾患であり、多くの場合、生後一ヶ月以内にチアノーゼ、右心不全、肺うっ血による呼吸困難を来す。治療は緊急的に、バルーン心房中隔裂開術(BAS)やBlalock-Hanlon手術を行う。(SSUR.370 YN.C-115)
疫学
- 先天性心疾患の約1%
- 全体の80%以上は新生児期から肺うっ血、肺高血圧、心不全となり早急な手術が必要(SSUR.370)
病型
- I型:上心臓型:垂直動脈から無名静脈、あるいは下大静脈に灌流還流
- II型:心臓型:右房、冠静脈洞
- III型:下心臓型:横隔膜を貫いて下降し、下大静脈、門脈に灌流
病態
検査
胸部単純X線写真
I型:上心臓型
- 次の構造によって8の字(雪だるま)が描かれる
- 上大静脈 腕頭静脈(無名静脈、垂直静脈)
- 右心室 左心
治療
- 心房中隔欠損、卵円孔開存が存在しなければ、緊急にバルーン心房中隔裂開術(BAS)、Blalock-Hanlon手術を施行
- I型:共通肺静脈管を左心房に吻合。垂直動脈結紮切除。心房中隔欠損の閉鎖。
- II型:右心房にパッチを当て、肺静脈血を左心房に流出させる。
- III型:共通肺静脈管を左心房に吻合する。
禁忌
- 酸素投与 → 肺血管抵抗を下げて肺血流を増加させてしまう。
予後
- 手術死亡率:15% (SSUR.372)
- 手術生存者の5-15%に肺静脈の狭窄 (SSUR.372)
- 約60%が生後1ヶ月で心不全となり、約80%が1歳以内に脂肪。
参考
[★]
総肺静脈還流異常症 total anomalous pulmonary venous return
[★]
- 関
- ameliorate、amelioration、feedback、recover、recovery、recuperate、regain、resolution、resolve、restitution、restoration、restore、reversal、revert
[★]
- 関
- aberrant、aberrantly、aberration、abnormal、abnormality、abnormally、anomalously、anomaly、defect、deviant、exceeding、extraordinarily、extraordinary、unusual、unusually
[★]
- 関
- all、altogether、common、entire、entirety、gross、overall、total amount、whole
[★]
- 関
- vein、vena
[★]
- 関
- lung、pneumo