complete transposition of great arteries

完全大血管転位症 TGA

WordNet

1. having every necessary or normal part or component or step; "a complete meal"; "a complete wardrobe"; "a complete set of the Britannica"; "a complete set of china"; "a complete defeat"; "a complete accounting"
2. having come or been brought to a conclusion; "the harvesting was complete"; "the affair is over, ended, finished"; "the abruptly terminated interview" (同)concluded, ended, over, all_over, terminated
3. perfect and complete in every respect; having all necessary qualities; "a complete gentleman"; "consummate happiness"; "a consummate performance" (同)consummate
4. write all the required information onto a form; "fill out this questionnaire, please!"; "make out a form" (同)fill out, fill_in, make_out
5. come or bring to a finish or an end; "He finished the dishes"; "She completed the requirements for her Masters Degree"; "The fastest runner finished the race in just over 2 hours; others finished in over 4 hours" (同)finish
6. complete a pass (同)nail
7. bring to a whole, with all the necessary parts or elements; "A child would complete the family"
8. remarkable or out of the ordinary in degree or magnitude or effect; "a great crisis"; "had a great stake in the outcome"
9. a person who has achieved distinction and honor in some field; "he is one of the greats of American music"
10. of major significance or importance; "a great work of art"; "Einstein was one of the outstanding figures of the 20th centurey" (同)outstanding
11. relatively large in size or number or extent; larger than others of its kind; "a great juicy steak"; "a great multitude"; "the great auk"; "a great old oak"; "a great ocean liner"; "a great delay"
12. any abnormal position of the organs of the body (同)heterotaxy
13. the act of reversing the order or place of (同)reversal
14. (electricity) a rearrangement of the relative positions of power lines in order to minimize the effects of mutual capacitance and inductance; "he wrote a textbook on the electrical effects of transposition"
15. (mathematics) the transfer of a quantity from one side of an equation to the other along with a change of sign
16. (music) playing in a different key from the key intended; moving the pitch of a piece of music upwards or downwards
17. (genetics) a kind of mutation in which a chromosomal segment is transfered to a new position on the same or another chromosome
18. caught; "a completed forward pass"
19. (of a marriage) completed by the first act of sexual intercourse after the ceremony

PrepTutorEJDIC

1. (比較変化なし)『全部の』,完備した / 《名詞の前にのみ用いて》『完全な』,全くの / (比較変化なし)『完成した』,完結した / …'を'『仕上げる』,終える / …'を'完全なものにする,完成する
2. (規模・範囲などが)『大きい』,巨大な / 『多数の』;『多量の』 / 『偉大な』,すぐれた;《the Great》《称号・肩書に用いて》 / (身分・地位などの)高い / 気高い,崇高な / 《名詞の前にのみ用いて》重要な,重大な / 《人を表す名詞の前にのみ用いて》大の,たいへんな / 《話》すてきな,すばらしい / 《名詞的に》《the great》偉大な人たち,重要人物 / とても,すごく / とてもよく(very well) / 大物,花形
3. 置き換え,転位 / (数学で)移項 / (音楽で)移調
4. 《所有・所属》…『の』,…のものである,…に属する・《材料・要素》…『でできた』,から成る・《部分》…『の』[『中の』] ・《数量・単位・種類を表す名詞に付いて》…の・《原因・動機》…『で』,のために(because of) ・《主格関係》…『の』,による,によって・《目的格関係》…『を』,の・《同格関係》…『という』・《関係・関連》…『についての』[『の』],の点で・《抽象名詞などと共に》…の[性質をもつ] ・《『It is』+『形』+『of』+『名』+『to』 doの形で,ofの後の名詞を意味上の主語として》・《分離》…『から』・《起原・出所》…『から』[『の』](out of) ・《『名』+『of』+『a』(『an』)+『名』の形で》…のような・《『名』+『of』+『mine』(『yours, his』など独立所有格)の形で》…の…・《時》(1)《副詞句を作って》…に《形容詞句を作って》…の・《時刻》《米》…前(to,《米》before)

UpToDate Contents

全文を閲覧するには購読必要です。 To read the full text you will need to subscribe.

• 1. L型大血管転位 l transposition of the great arteries
• 2. D型大血管転位のマネージメントおよび転帰 management and outcome of d transposition of the great arteries
• 3. D型大血管転位の病態生理、臨床症状、および診断 pathophysiology clinical manifestations and diagnosis of d transposition of the great arteries
• 4. 先天性心疾患女性における妊娠：特定病変 pregnancy in women with congenital heart disease specific lesions
• 5. 小児における徐脈 bradycardia in children

English Journal

• Anatomic repair of complex transposition with en bloc rotation of the truncus arteriosus: 10-year experience†.

• Mair R1, Sames-Dolzer E2, Innerhuber M2, Tulzer A2, Grohmann E2, Tulzer G2.
• European journal of cardio-thoracic surgery : official journal of the European Association for Cardio-thoracic Surgery.Eur J Cardiothorac Surg.2016 Jan;49(1):176-82. doi: 10.1093/ejcts/ezv056. Epub 2015 Feb 19.
• OBJECTIVES: Transposition of the great arteries, ventricular septal defect and left ventricular outflow tract obstruction are commonly called complex transposition. The traditional method of repair is the Rastelli procedure. Aortic translocation (Nikaidoh 1984) provides a more anatomic repair of thi
• PMID 25700698

• Dynamic left ventricular outflow obstruction in situs inversus with levocardia.

• Hirata K1, Tengan T2, Mototake H2, Wake M1.
• BMJ case reports.BMJ Case Rep.2015 Dec 1;2015. pii: bcr2015213030. doi: 10.1136/bcr-2015-213030.
• A 69-year-old man with situs inversus, levocardia and inverted great arteries developed severe dynamic left ventricular outflow tract (LVOT) obstruction with systolic anterior motion of the anterior mitral leaflet. There was no asymmetric septal hypertrophy. A possible mechanism of the LOVT obstruct
• PMID 26628311

• Simplified Bernoulli's method significantly underestimates pulmonary transvalvular pressure drop.

• Falahatpisheh A1, Rickers C2, Gabbert D2, Heng EL3, Stalder A4, Kramer HH2, Kilner PJ3, Kheradvar A1.
• Journal of magnetic resonance imaging : JMRI.J Magn Reson Imaging.2015 Nov 19. doi: 10.1002/jmri.25097. [Epub ahead of print]
• PURPOSE: To determine whether neglecting the flow unsteadiness in simplified Bernoulli's equation significantly affects the pulmonary transvalvular pressure drop estimation.MATERIALS AND METHODS: 3.0T magnetic resonance imaging (MRI) 4D velocity mapping was performed on four healthy volunteers, seve
• PMID 26584006

Japanese Journal

• Transaortic Approach to Residual Ventricular Septal Shunt after Repairing Corrected Transposition of the Great Arteries

• Takahashi Hiroaki,Oshima Yoshihiro,Shimazu Chikashi
• Annals of
• … Many surgical approaches have been taken when closing ventricular septal defects after correcting transposition of the great arteries in order to avoid postoperative complete heart block. … The defect was closed transaortically without a complete heart block. …
• NAID 130002148281

• Commotio Cordis Presenting as Temporary Complete Atrioventricular Block in a 2-Year Old Girl with Congenitally Corrected Transposition of Great Arteries

• Fujita Shuhei,Nakamura Taichi,Igarashi Noboru,Hatasaki Kiyoshi
• Journal of
• … We report a 2-year old girl with the congenitally corrected transposition of the great arteries (ccTGA) that presented the transient complete atrioventricular (AV) block after slight chest blow. … After that, she was cyanotic, pale and transient loss of consciousness. … On the electrocardiogram (ECG), it demonstrated a complete AV block with her heart rate was 78 beat per minuets (bpm). …
• NAID 130002130556

• Successful initiation and maintenance of hemodialysis in an adult patient with complete transposition of the great arteries

• YAMADA Shunsuke,YOTSUEDA Hideki,TANIGUCHI Masatomo,TSURUYA Kazuhiko,HIRAKATA Hideki,IIDA Mitsuo
• Clinical and experimental nephrology 14(5), 511-515, 2010-10-01
• NAID 10027707446

Related Links

• Complete Transposition of the Great Arteries

Abstract Background Transposition of the great arteries (TGA) is considered to be associated only rarely with genetic syndromes and to have a low risk of precurrence among relatives of affected patients. Because ...

• Transposition of the great vessels: MedlinePlus Medical ...

Transposition of the great vessels is a heart defect that occurs from birth (congenital). The two major vessels that carry blood away from the heart -- the aorta and the pulmonary artery -- are switched (transposed).

---

★リンクテーブル★

リンク元	「完全大血管転位症」「大血管転位症」
関連記事	「great」「complete」「transposition」

「完全大血管転位症」

　　[★]

英

complete transposition of great arteries, complete-TGA

同

完全大血管転位　←　googleでこちらが多く、ガイドラインではこちらが使われている。一方、教科書には「完全大血管転位症」として載っていることが多い

関

大血管転位症 TGA、修正大血管転位症

[show details]

完全大血管転位 : 約 17,400 件
完全大血管転位症 : 約 15,200 件

概念

• 大動脈が右室から、肺動脈が左室から起始している先天性心疾患。

疫学

• 男児に多い(64$)
• 早産や低体重児であることは少ない

病型

• 1型：60%：VSD(-)、PS(-)、ASD、PDA　→　心房中隔欠損か動脈開存症が生存に必須。
• 2型：30%：VSD(+)、PS(-)
• 3型：10%：VSD(+)、PS(+)

治療

手術療法

• I型：生後14日までにarterial switch

• そうでないと肺動脈・左室圧が低下し左室の心筋重量が低下してしまうため、術後に左室芽体血圧を支えることができなくなるため

まとめ PED.922

	VSD	PS	チアノーゼ	頻呼吸	陥没呼吸	心雑音	肺血管陰影	手術
I型	－	－	生後	○	なし	なし	増強	生後14日までにarterial switch
II型	＋	－	軽度		生後1-2週	生後数日	－	新生児期・乳児期早期にarterial switch手術+VSD閉鎖術
III型	＋	＋				生直後	－	Blalock-Taussig手術→Rastelli手術。乳児期から幼児期前半。

SPE.456-457, 医学大事典, YN.C-115

割合

VSD

PS

ASD

PDA

肺高血圧

チアノーゼ

うっ血性心不全

肺血管陰影 (PHを反映)

心室肥大 pressure loadを反映?

予後

姑息手術・内科的治療

根治手術

I型

60(%)

－

－

あり

あり

＋

生後より強い

＋

増強

右室

うっ血心不全で70%死亡

BAS/Blalock-Hanlon手術、PGE1

生後14日までにJatene手術施行

II型

30(%)

＋

－

＋＋

軽度

増強

右室＋左室

肺高血圧で6ヶ月以内に大部分死亡

PA binding(肺血流↓)、(新生児期にBAS)

新生児期～3ヶ月以内にJatene手術施行

III型

10(%)

＋

＋

－

I型より重症

－

右室

比較的良好

Blalock-Taussig手術(肺血流↑)

1,2歳で二期的にRastelli手術施行

参考

• 先天性心疾患の診断、病態把握、治療選択のための検査法の選択ガイドライン

• http://www.j-circ.or.jp/guideline/pdf/JCS2010_hamaoka_h.pdf

-complete transposition of the great arteries

同

TGA

「大血管転位症」

　　[★]

英

transposition of great vessels transposition of great arteries transposition of the great arteries TGA

同

大血管転換症

関

修正大血管転位症、完全大血管転位症 complete transposition of great arteries

「great」

　　[★]

• adj.

• [限定]偉大な、卓越した。有名な、著明な
• [限定](規模・形の)大きな、巨大な
• (比較)(同種の中で)大きい方の、大形種の
• [限定](数量の)多い、多数[大量]の。(時間・距離の)長い
• (程度の)大きな、非常な
• [程度表示の可能な、人を表す名詞を限定して]大の、真にその名にふさわしい
• [限定]重要な。(比較)[the ～]主要な
• [限定]身分/地位の高い
• (考え・行為などが)高潔な
• [限定]好んで使われる

• adv.
• n.

関

a large number of、a lot of、large、large number、manifold、many、massive、multitude、numerous、sizable

　 　 　 　 　

「complete」

　　[★]

• adj.

• 完全な、徹底的な、完了する、完成する、終了する

関

completely、completion、drastic、drastically、end、entirely、execution、exhaustive、exhaustively、finish、fulfillment、full、fully、in depth、integral、perfect、perfectly、radically、terminate、termination、thorough、thoroughly

　 　 　 　 　 　 　 　

「transposition」

　　[★]

日

関