成人スティル病
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- 1. 成人スティル病の臨床症状および診断clinical manifestations and diagnosis of adult stills disease [show details]
…have been few reports of cases in twins . Adult Still disease is very uncommon. A retrospective French study estimated the annual incidence of adult Still disease (ASD) to be 0.16 cases per 100,000 people …
- 2. 成人スティル病の治療treatment of adult stills disease [show details]
… but who had features similar to the children with systemic JIA ; this term and sometimes "adult-onset Still disease" are now widely used for this condition. The treatment and prognosis of ASD will be reviewed …
- 3. 学会が公開する診療ガイドラインのリンク：成人のスチル病society guideline links adult stills disease [show details]
…Japanese Ministry of Health, Labour, and Welfare: Evidence-based clinical practice guideline for adult Still disease (2018)…
- 4. 成人における不明熱の病因etiologies of fever of unknown origin in adults [show details]
…FUO in older adults . Adult Still disease is an inflammatory disorder characterized by quotidian (daily) fevers, arthritis, and an evanescent rash. Patients with adult Still disease have features similar …
- 5. 全身型若年性特発性関節炎：臨床症状および診断systemic juvenile idiopathic arthritis clinical manifestations and diagnosis [show details]
… prognosis, with a mortality rate of 40 to 60 percent . Pharyngitis, a common feature of adult-onset Still disease, is not commonly seen in children but is occasionally a prominent complaint in older children…
English Journal
Japanese Journal
- Interleukin-18 and fibroblast growth factor 2 in combination is a useful diagnostic biomarker to distinguish adult-onset Still's disease from sepsis
- Koga Tomohiro,Sumiyoshi Remi,Furukawa Kaori,Sato Shuntaro,Migita Kiyoshi,Shimizu Toshimasa,Umeda Masataka,Endo Yushiro,Fukui Shoichi,Kawashiri Shin-ya,Iwamoto Naoki,Ichinose Kunihiro,Tamai Mami,Nakamura Hideki,Origuchi Tomoki,Nonaka Fumiaki,Yachie Akihiro,Kondo Hideaki,Maeda Takahiro,Kawakami Atsushi
- Arthritis Research & Therapy 22(1), 108, 2020-05-07
- … Objective: To identify potential biomarkers to distinguish adult-onset Still's disease (AOSD) from sepsis. …
- NAID 120006847158
- 症例報告 メトトレキサート併用が奏効した成人Still病の1例
- 渡部 茉耶,森田 知世,栁瀬 哲至
- 臨床皮膚科 = Japanese journal of clinical dermatology 74(2), 151-156, 2020-02
- NAID 40022176090
- Adult-onset Still's disease with macrophage activation syndrome diagnosed and treated based on cytokine profiling: a case-based review
- Goda Ken,Kenzaka Tsuneaki,Hoshijima Masahiko,Yachie Akihiro,Akita Hozuka
- Rheumatology International 40(1), 145-152, 2020-01
- … Adult-onset Still's disease (AOSD) is a relatively rare systemic inflammatory disorder and is diagnosed using various sets of classification criteria, with the Yamaguchi criteria as the most widely used criteria. …
- NAID 120006786955
Related Links
- Adult-onset Still’s disease (AOSD) is a rare condition that is estimated to cause up to 0.4 cases in every 100,000 adults.There’s also a version that affects children called systemic onset ...
- Adult-onset Still's disease is an inflammatory disease that may affect many joints, internal organs, and other parts of the body. Adult Still's develops most often in people before age 45, but can ...
- Abbreviations: AE = adverse event, AOSD = adult-onset Still disease, BM = bone marrow, CI = confidence interval, CRP = C-reactive protein, CSs = corticosteroids, CT = computed tomography, DMARDs = disease-modifying antirheumatic drugs, ESR = erythrocyte sedimentation rate, 18 FDG-PET = 18 F-fluorodeoxyglucose positron emission tomography, GF = glycosylated ferritin, IL = interleukin, IVIg ...
★リンクテーブル★
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- 英
- adult-onset Still's disease AOSD, adult-onset Still disease, adult Still's disease
- 同
- 成人発症スチル病、成人発症Still病、成人スチル病、成人Still病
- 関
- アレルギー性亜敗血症、スティル病、若年性関節リウマチ
[show details]
概念
診断基準
- 参考4 YN.F-47
大項目
- 1. 発熱(39℃以上、1週間以上持続)
- 2. 関節痛(2週間以上持続)
- 3. 定型的皮疹(体幹・四肢近位部にサーモンピンク様皮疹、ケブネル現象陽性)
- 4. 白血球増加(10000/μl以上、好中球80%以上)
小項目
- 1. 咽頭痛
- 2. リンパ節腫脹または脾腫
- 3. 肝機能異常
- 4. リウマトイド因子および抗核抗体陰性
除外項目
- 感染症(特に敗血症・伝染性単核症)、悪性腫瘍(特にリンパ腫)、膠原病(特に多発性動脈炎、悪性関節リウマチ)
診断
- 大症状2項目以上を含み、合計5項目以上で成人Still病と診断する。血清フェリチンの異常高値は診断の参考とする。
検査
参考
- http://www.collagen-disease.com/_src/sc2405/83X83e83B838B95a8ECA905E.jpg
- http://img2.blogs.yahoo.co.jp/ybi/1/1a/52/fukusama1019/folder/1092861/img_1092861_57599288_0?1262257060
- http://www.hospital.japanpost.jp/fukuoka/health/pdf/ProfileNo.43.pdf
- http://www8.ocn.ne.jp/~halfboil/criteria/tab-f11.html
- http://www.nanbyou.or.jp/entry/282
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- 疾患：illnessより厳密な概念。「ある臓器に明確な障害が確認され、それによって症状が出ているとはっきり説明できる場合」 (PSY.9)
- 特定の原因、病態生理、症状、経過、予後、病理組織所見が全てそろった場合 (PSY.9)
- something that is very wrong with people's attitudes, way of life or with society.
- 関
- ail、ailment、disease entity、disorder、ill、illness、malady、sick、sickness
- disease ≠ illness ≠ disorder
[★]
- 襲撃、攻撃。(病気などの)始まり、開始、襲来。着手、手始め
- 関
- affect、commence、commencement、develop、development、developmental、emergence、engender、episode、event、generate、generation、initiate、initiation、institute、mount、occur、occurrence、pathogenesis、start、symptom onset、transpire
[★]
- 動きのない、制止した
- 静かな。しんとした、音のしない、黙った。(声が)やさしい(soft)。静穏な、平和な
- 静める、落ち着かせる。(泣く子を)なだめる。(食欲・両親などを)満足させる。(音などを)止める、黙らせる。動かなくする、制止させる
[★]
- 関
- adult human、adult type
