WordNet

Wikipedia preview

出典(authority):フリー百科事典『ウィキペディア（Wikipedia）』「2016/05/18 09:27:08」(JST)

全文を閲覧するには購読必要です。 To read the full text you will need to subscribe.

Electrochemical characterization of gelatinized starch dispersions: Voltammetry and electrochemical impedance spectroscopy on platinum surface.

Hernandez-Jaimes C1, Lobato-Calleros C2, Sosa E3, Bello-Pérez LA4, Vernon-Carter EJ2, Alvarez-Ramirez J5.
Carbohydrate polymers.Carbohydr Polym.2015 Jun 25;124:8-16. doi: 10.1016/j.carbpol.2015.02.002. Epub 2015 Feb 12.
The electrochemical properties of gelatinized starch dispersions (GSD; 5% w/w) from different botanical sources were studied using cyclic voltammetry (CV) and electrochemical impedance spectroscopy (EIS) tests over a platinum surface. The phenomenological modelling of EIS data using equivalent circu
PMID 25839788

Application of whole exome sequencing to a rare inherited metabolic disease with neurological and gastrointestinal manifestations: A congenital disorder of glycosylation mimicking glycogen storage disease.

Choi R1, Woo HI2, Choe BH3, Park S4, Yoon Y4, Ki CS1, Lee SY1, Kim JW1, Song J5, Kim DS6, Kwon S6, Park HD7.
Clinica chimica acta; international journal of clinical chemistry.Clin Chim Acta.2015 Apr 15;444:50-3. doi: 10.1016/j.cca.2015.02.008. Epub 2015 Feb 11.
BACKGROUND: Rare inherited metabolic diseases with neurological and gastrointestinal manifestations can be misdiagnosed as other diseases or remain as disorders with indeterminate etiologies. This study aims to provide evidence to recommend the utility of whole exome sequencing in clinical diagnosis
PMID 25681648

Protection factor for n95 filtering facepiece respirators exposed to laboratory aerosols containing different concentrations of nanoparticles.

Rengasamy S1, Walbert G2, Newcomb W2, Coffey C2, Wassell JT2, Szalajda J2.
The Annals of occupational hygiene.Ann Occup Hyg.2015 Apr;59(3):373-81. doi: 10.1093/annhyg/meu095. Epub 2014 Nov 25.
A previous study used a PortaCount Plus to measure the ratio of particle concentrations outside (C out) to inside (C in) of filtering facepiece respirators (FFRs) worn by test subjects and calculated the total inward leakage (TIL) (C in/C out) to evaluate the reproducibility of the TIL test method b
PMID 25429023

ランドスケープ・アーバニズムをめぐる4つの方向性 : ハーバード大学大学院デザインスクールチャールズ・ウォルドハイム教授に聞く (特集ランドスケープ・アーバニズムのもたらしたもの)

ランドスケープ研究 : 日本造園学会誌 : journal of the Japanese Institute of Landscape Architecture 78(4), 329-332, 2015-01
NAID 40020350194

Assessing real-time performances of N95 respirators for health care workers by simulated workplace protection factors

型	欠損酵素	組織	グリコーゲン構造	病名	発症時期	症状
I	グルコース-6-ホスファターゼ	肝臓	正常	フォン・ギールケ病	childhood	growth retardation, enlarged liver and kidney, hypoglycemia, elevated blood lactate, cholesterol, triglycerides, and uric acid
II	α-1,4-グルコシダーゼ	リソソーム	正常	ポンペ病	childhood
III	アミロ-1,6-グルコシダーゼ debrancher enzyme deficiency	全器官	最外層分子がないか非常に短い	コリ病	childhood	hypoglycemia, hepatomegaly, short-stature, and myopathty
IV	アミロ-(1,4→1,6)-トランスグリコシラーゼ brancher enzyme deficiency	肝臓、全器官?	非常に長い枝無し鎖	アンダーセン病		infantile failure to thrive, cirrhosis, liver failure, and extreme hypotonia.
V	グリコーゲンホスホリラーゼ muscle phosphorylase deficiency	筋肉	正常	マッカードル病	adult	exercise intolerance, muscle cramps, myoglobinuria on strenuous exercise, increased CK
VI	グリコーゲンホスホリラーゼ hepatic phosphorylase deficiency	肝臓	正常	エルス病		hematomegaly and variable hypoglycemia
VII	6-ホスホフルクト-1-キナーゼ	筋肉	正常	垂井病
VIII	ホスホリラーゼキナーゼ	肝臓	正常	X染色体ホスホリラーゼキナーゼ欠損症
IX	ホスホリラーゼキナーゼ	全器官	正常		childhoog
0	グリコーゲンシンターゼ	肝臓	正常だが少量