もやもや病
WordNet
- an impairment of health or a condition of abnormal functioning
- caused by or altered by or manifesting disease or pathology; "diseased tonsils"; "a morbid growth"; "pathologic tissue"; "pathological bodily processes" (同)morbid, pathologic, pathological
PrepTutorEJDIC
- (体の)『病気』,疾患 / (精神・道徳などの)病気,病弊
- 女性の話術芸人 =diseur
- 病気にかかった / 病的な,不健全な(morbid)
UpToDate Contents
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English Journal
- Collateralization and ischemia in hemodynamic cerebrovascular insufficiency.
- Czabanka M1, Acker G, Jussen D, Finger T, Pena-Tapia P, Schubert GA, Scharf J, Martus P, Schmiedek P, Vajkoczy P.
- Acta neurochirurgica.Acta Neurochir (Wien).2014 Nov;156(11):2051-8. doi: 10.1007/s00701-014-2227-1. Epub 2014 Sep 25.
- BACKGROUND: Moyamoya disease and atherosclerotic cerebrovascular occlusive disease lead to hemodynamic impairment of cerebral blood flow. One major differentiation between both disease entities lies in the collateralization pathways. The clinical implications of the collateralization pathways for th
- PMID 25253629
- RNF213 Rare Variants in an Ethnically Diverse Population With Moyamoya Disease.
- Cecchi AC1, Guo D1, Ren Z1, Flynn K1, Santos-Cortez RL1, Leal SM1, Wang GT1, Regalado ES1, Steinberg GK1, Shendure J1, Bamshad MJ1; University of Washington Center for Mendelian Genomics, Grotta JC1, Nickerson DA1, Pannu H1, Milewicz DM2.
- Stroke; a journal of cerebral circulation.Stroke.2014 Nov;45(11):3200-7. doi: 10.1161/STROKEAHA.114.006244. Epub 2014 Oct 2.
- BACKGROUND AND PURPOSE: Moyamoya disease (MMD) is a rare, genetically heterogeneous cerebrovascular disease resulting from occlusion of the distal internal carotid arteries. A variant in the Ring Finger 213 gene (RNF213), altering arginine at position 4810 (p.R4810K), is associated with MMD in Asian
- PMID 25278557
- Vaginal delivery in pregnancy with Moyamoya disease: Experience at a single institute.
- Tanaka H1, Katsuragi S, Tanaka K, Miyoshi T, Kamiya C, Iwanaga N, Neki R, Takahashi JC, Ikeda T, Yoshimatsu J.
- The journal of obstetrics and gynaecology research.J Obstet Gynaecol Res.2014 Oct 27. doi: 10.1111/jog.12557. [Epub ahead of print]
- AIM: Cesarean section is commonly selected in pregnancy with Moyamoya disease. We consider vaginal delivery with epidural anesthesia a viable alternative in such cases.METHODS: Mode of delivery and outcomes were examined in 27 pregnancies in 19 women with Moyamoya disease treated at the Department o
- PMID 25345600
Japanese Journal
- 関根 基樹,飯田 政弘,浜野 巨秀 [他],大上 研二,小田 真理
- 耳鼻咽喉科臨床 99(12), 1005-1010, 2006-12-01
- … Selective catheter embolization was performed with NBCA (N-butyl-2-cyanoacrylate), which was introduced into the distal branch of the sphenopalatine artery.Radical surgery was planned for a few days after embolization, but it was postponed because Moya-Moya disease was found during angiographic study. …
- NAID 10020336715
- 発症後10年以上経過した慢性期患者への認知リハビリテーションの効果 : 症例報告
- 岡村 陽子,原 行弘
- 高次脳機能研究 : 日本高次脳機能障害学会誌 = Higher brain function research 25(1), 17-25, 2005-03-31
- 慢性期の患者では認知機能の新たな改善が期待されないためか, 認知リハは行われない傾向にある。本症例では発症後10年以上が経過しているが, 注意訓練を主体とした認知リハの結果, 認知機能の改善が認められた。症例は1991年12月もやもや病, 脳出血の発症から高次脳機能障害を呈した33歳の女性。認知リハ開始前の初期評価において全般的な知的低下, 記憶力の低下, 注意力低下が認められたため, 段階的に注 …
- NAID 10015687238
- 頭蓋内出血をくり返したモヤモヤ病の経時的 angiography の変化 : 症例報告から
- 本田 英一郎,大島 勇紀,倉本 進賢,安陪 等思,宇都宮 英綱
- 脳卒中の外科 = Surgery for cerebral stroke 27, 328, 1998-06-24
- NAID 10016505372
Related Links
- Pictures of my MoyaMoya Disease STA-MCA surgery for MoyaMoya sufferers and their families ... "Maui Maui? What the hell is that!!??" Those were my exact words when I first heard of MoyaMoya in June 2001. I spent ...
- This disease affects only 1 in 2,000,000 people. The only option to help stop the progression of moyamoya and alleviate the symptoms is surgery. Justin bravely endured 8 hours of brain surgery in April of 2007. Justin will always ...
★リンクテーブル★
[★]
- 英
- moyamoya disease, moya-moya disease
- 同
- モヤモヤ病、ウイリス動脈輪閉塞症 大脳動脈輪閉塞症 occlusive disease in circle of Willis, Willis circle occlusion syndrome、脳底部異常血管網症 abnormal vascularnet at the brain base, vascularnet of cerebral basal area、西本-竹内-工藤病 Nishimoto-Takeuchi-Kudo disease、脳血管もやもや病
- 関
- 難病
概念
徴候
- 過換気により血中PaCO2が低下し脳血流が低下することが発作の誘因となりうる。
- 小児:片麻痺、知覚障害、不随意運動、頭痛、痙攣発作。
- 成人:頭蓋内出血(脳出血・クモ膜下出血)
検査
- 認定基準上はMRIとMRAで十分であり、血管造影は施行しなくとも良い
- MRI
failpicload@./t_image/101/101G028.JPG
- 血管造影
failpicload@./t_image/099/099G026.JPG
除外診断
治療
- 間接的血行再建術:組織・血管を移植(側頭筋、浅側頭動脈、大網など)
- 直接的血行再建術:浅側頭動脈-中大脳動脈吻合術
参考
- http://www.nanbyou.or.jp/entry/47
- http://www.nanbyou.or.jp/upload_files/115z_s.pdf
国試
[★]
- 疾患:illnessより厳密な概念。「ある臓器に明確な障害が確認され、それによって症状が出ているとはっきり説明できる場合」 (PSY.9)
- 特定の原因、病態生理、症状、経過、予後、病理組織所見が全てそろった場合 (PSY.9)
- something that is very wrong with people's attitudes, way of life or with society.
- 関
- ail、ailment、disease entity、disorder、ill、illness、malady、sick、sickness
- disease ≠ illness ≠ disorder