オリーブ・橋・小脳萎縮症
WordNet
- a decrease in size of an organ caused by disease or disuse (同)wasting, wasting away
- undergo atrophy; "Muscles that are not used will atrophy"
- any weakening or degeneration (especially through lack of use) (同)withering
- relating to or associated with the cerebellum; "cerebellar artery"
PrepTutorEJDIC
- (栄養不良などによる)萎縮(いしゅく) / (一般的に)衰退,退化 / 萎縮する,衰退する / …'を'萎縮させる,衰退させる
UpToDate Contents
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English Journal
- Characteristic diffusion tensor tractography in multiple system atrophy with predominant cerebellar ataxia and cortical cerebellar atrophy.
- Fukui Y, Hishikawa N, Sato K, Nakano Y, Morihara R, Ohta Y, Yamashita T, Abe K.
- Journal of neurology.J Neurol.2016 Jan;263(1):61-7.
- The objective of this study is to determine whether diffusion tensor imaging (DTI) tractography analysis is a potential method for differentiating cerebellar ataxia patients with multiple system atrophy with predominant cerebellar ataxia (MSA-C) and cortical cerebellar atrophy (CCA). Forty-one MSA-C
- PMID 26477028
- A combination of chorea, myoclonus, and dystonia in a patient with pontocerebellar hypoplasia type 2: a video case presentation.
- Gupta HV1, Ramakrishnaiah RH2, Sharp GB3, Lee RW4, Walters WD5.
- Acta neurologica Belgica.Acta Neurol Belg.2015 Dec;115(4):783-5. doi: 10.1007/s13760-015-0461-9. Epub 2015 Apr 3.
- PMID 25837317
- Psychosis in a patient with probable multiple system atrophy of cerebellar type.
- Khan S1, Moore J1, Ealing J2, Kobylecki C3.
- Journal of the neurological sciences.J Neurol Sci.2015 Nov 15;358(1-2):501-2. doi: 10.1016/j.jns.2015.09.354. Epub 2015 Sep 18.
- PMID 26409569
Japanese Journal
- 四茂野 はるみ,栗崎 博司,蛇沢 晶 [他],崎山 快夫,齊藤 祐子,村山 繁雄
- 臨床神経学 50(3), 156-162, 2010-03-01
- パーキンソニズムを主症状としたSCA2の最初の剖検例である．12q23-24に38と40のモザイクCAGリピート延長がありSCA2と判明，母と息子も同病であった．自律神経障害，認知症を合併し，小脳症状は軽度であった．頭部画像では橋・延髄萎縮が著明でMSA-Cに似ていた．髄液HVA，5HIAAは減少，MIBG心筋シンチでH/M比低下をみとめた．剖検で橋核，下オリーブ核，小脳，黒質等に1C2陽性封入体 …
- NAID 10026291592
- 東京女子医大病院神経内科入院患者における発汗障害例の検討(神経内科学教室竹宮敏子教授退任記念特別号)
- 松村 美由起,竹宮 敏子,岩田 誠
- 東京女子医科大学雑誌 70(臨時増刊号2), E340-E353, 2000-12-30
- … Causative diseases of dyshidrosis are primary autonomic failure including pure progressive autonomic failure (pure PAF) PAF with multiple system atrophy (MSA), or Shy-Drager syndrome (SDS). …
- NAID 110007526909
- 古川 朋靖,渡辺 道隆,正木 義男,都丸 香緒,山口 洋子,市川 銀一郎
- 耳鼻咽喉科臨床 92(4), 347-354, 1999-04-01
- … The main clinical findings of OPCA include cerebellar symptoms, extrapyramidal symptoms, autonomic nerve symptoms, in addition to various oculo-motor disturbances. … The oculo-motor disturbances of OPCA start with impairment of cerebellar and smooth pursuit eye movement, and eventually result in brainstem disorders such as saccadic eye movement and visual suppression. …
- NAID 10006828875
Related Links
- Listen. Olivopontocerebellar atrophy (OPCA) is a term used for a progressive condition characterized by the degeneration of nerve cells (neurons) in specific areas of the brain. [1] OPCA can be viewed as a finding of several diseases, and indicates a form of progressive ataxia (abnormal or uncontrolled movements) distinguished by characteristic ...
- オリーブ橋小脳萎縮症は、小脳失調症状や自律神経症状を呈する神経変性疾患です。予後も良好とはいえない本症の最新 ...
- The term olivopontocerebellar atrophy (OPCA) has historically been used to describe a group of disorders that affect the central nervous system and are termed neurodegenerative diseases because they result in a progressive deterioration of nerve cells in certain parts of the brain.
★リンクテーブル★
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- 英
- olivopontocerebellar atrophy, OPCA, olivopontocerebellar atrophies
- 同
- デジュリーヌ・トーマ病 Dejerine-Thomas disease、オリーブ・橋・小脳萎縮症 olivo-ponto-cerebellar atrophy、オリーブ橋小脳変性症 olivopontocerebellar degeneration
- 関
- spinocerebellar ataxia, SCA1、多系統萎縮症、脊髄小脳変性症
概念
脊髄小脳変性症との関係
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多系統萎縮症
症状
- YN.J-124
- 歩行障害→運動失調→平衡障害→構音障害
- 1. 小脳症状
- 2. 錐体路症状
- 3. 錐体外路症状
- 4. 自立心液晶状
- 5. 知能低下
治療
予後(YN.J-124)
国試
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遺伝性オリーブ橋小脳萎縮症
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- 関
- cerebelli、cerebellum
[★]
小脳萎縮、小脳萎縮症
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