- 関
- external ophthalmoplegia、oculomotor nerve paralysis、ophthalmoparesis、ophthalmoplegia
WordNet
- paralysis of the motor nerves of the eye
- loss of the ability to move a body part (同)palsy
- supplies extrinsic muscles of the eye (同)oculomotor_nerve, nervus_oculomotorius, third_cranial_nerve
PrepTutorEJDIC
- (体の)麻痺(まひ),中風 / (…の)停滞《+『of』+『名』》
UpToDate Contents
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English Journal
- Congenital myasthenic syndrome due to choline acetyltransferase mutations in infants: clinical suspicion and comprehensive electrophysiological assessment are important for early diagnosis.
- Dilena R1, Abicht A, Sergi P, Comi GP, Fonzo AD, Chidini G, Natacci F, Barbieri S, Lochmüller H.Author information 11Unit of Clinical Neurophysiology, Department of Neurological Sciences, Foundation IRCCS Ca' Granda Ospedale Maggiore Policlinico, Milan, Italy.AbstractCongenital myasthenic syndromes are inherited disorders caused by various defects in neuromuscular transmission. Although the typical presentation is fatigable weakness with prominent cranial involvement, neonates can lack these hallmark manifestations, and in those with choline acetyltransferase gene mutations, basal electrophysiological testing can yield negative findings. The authors report the case of a male infant presenting at birth with oculomotor and bulbofacial weakness, hypotonia, clubfoot, and severe respiratory insufficiency. Electromyography showed myogenic signs, and basal repetitive nerve stimulation yielded negative findings. Since age 6 months, the infant had progressively improved, acquiring autonomous respiration. Prolonged subtetanic repetitive nerve stimulation disclosed a marked decremental response compatible with suspected congenital myasthenic syndrome with episodic apnea. Genetic testing identified 2 novel choline acetyltransferase mutations (R470X, F580C). Keeping a high clinical suspicion of this rare condition and undertaking early comprehensive electrophysiological assessments including prolonged repetitive nerve stimulation (10 Hz for 5 minutes) can expedite the diagnosis.
- Journal of child neurology.J Child Neurol.2014 Mar;29(3):389-93. doi: 10.1177/0883073812470000. Epub 2013 Jan 4.
- Congenital myasthenic syndromes are inherited disorders caused by various defects in neuromuscular transmission. Although the typical presentation is fatigable weakness with prominent cranial involvement, neonates can lack these hallmark manifestations, and in those with choline acetyltransferase ge
- PMID 23292760
- Pharyngeal-cervical-brachial variant of Guillain-Barre syndrome.
- Wakerley BR1, Yuki N.Author information 1Department of Medicine, National University Hospital, Singapore.AbstractThe pharyngeal-cervical-brachial (PCB) variant of Guillain-Barré syndrome is defined by rapidly progressive oropharyngeal and cervicobrachial weakness associated with areflexia in the upper limbs. Serial nerve conduction studies suggest that PCB represents a localised subtype of Guillain-Barré syndrome characterised by axonal rather than demyelinating neuropathy. Many neurologists are unfamiliar with PCB, which is often misdiagnosed as brainstem stroke, myasthenia gravis or botulism. The presence of additional ophthalmoplegia and ataxia indicates overlap with Fisher syndrome. Half of patients with PCB carry IgG anti-GT1a antibodies which often cross-react with GQ1b, whereas most patients with Fisher syndrome carry IgG anti-GQ1b antibodies which always cross-react with GT1a. Significant overlap between the clinical and serological profiles of these patients supports the view that PCB and Fisher syndrome form a continuous spectrum. In this review, we highlight the clinical features of PCB and outline new diagnostic criteria.
- Journal of neurology, neurosurgery, and psychiatry.J Neurol Neurosurg Psychiatry.2014 Mar;85(3):339-44. doi: 10.1136/jnnp-2013-305397. Epub 2013 Jun 26.
- The pharyngeal-cervical-brachial (PCB) variant of Guillain-Barré syndrome is defined by rapidly progressive oropharyngeal and cervicobrachial weakness associated with areflexia in the upper limbs. Serial nerve conduction studies suggest that PCB represents a localised subtype of Guillain-Barré syn
- PMID 23804237
- Recovery of ocular motor cranial nerve palsy after herpes zoster ophthalmicus.
- Chhabra MS1, Golnik KC.Author information 1Department of Ophthalmology (MSC, KCG), University of Cincinnati, Cincinnati Eye Institute, Cincinnati, Ohio; and the Virdi Eye Clinic (MSC), Rock Island, Illinois.AbstractOBJECTIVE: To report the course of ocular motor cranial nerve palsy due to herpes zoster.
- Journal of neuro-ophthalmology : the official journal of the North American Neuro-Ophthalmology Society.J Neuroophthalmol.2014 Mar;34(1):20-2. doi: 10.1097/WNO.0b013e3182a59c69.
- OBJECTIVE: To report the course of ocular motor cranial nerve palsy due to herpes zoster.METHODS: A retrospective chart review identified patients with ocular motor cranial nerve palsy occurring at the time of herpes zoster ophthalmicus. Patients were seen by a single neuro-ophthalmologist from 1994
- PMID 24051426
Japanese Journal
- 右動眼神経麻痺で初発し,後に対側の眼症状で診断に至った右海綿静脈洞部硬膜動静脈瘻の1例
- 右動眼神経麻痺で初発し,後に対側の眼症状で診断に至った右海綿静脈洞部硬膜動静脈瘻の1例
- 侵襲型アスペルギルス症による眼窩先端症候群を発症し頭蓋内へ病巣の拡大がみられた2型糖尿病の1例
Related Links
- oculomotor nerve paralysis causes pupillary dilatation, absence of pupillary light reflex, ventrolateral deviation of the eye, defective eye movement and palpebral ptosis. oculomotor Pertaining to movement of the eyes, or to the oc·u ...
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★リンクテーブル★
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- 英
- oculomotor nerve paralysis, oculomotor paralysis, oculomotor palsy
- ラ
- paralysis oculomotoria
- 関
- 動眼神経
概念
病因
瘤
症状
- 滑車神経が支配する上斜筋、外転神経の支配する外直筋のみが眼球運動を支配するので、外転以外は困難となる。よって複視を生じる。
国試
[show details]
[★]
- 関
- external ophthalmoplegia、oculomotor paralysis、ophthalmoplegia
[★]
- 関
- eye movement、ocular movement