大動脈弓離断症
WordNet
- a passageway under a curved masonry construction; "they built a triumphal arch to memorialize their victory" (同)archway
- (architecture) a masonry construction (usually curved) for spanning an opening and supporting the weight above it
- a curved shape in the vertical plane that spans an opening
- expert in skulduggery; "an arch criminal"
- a curved bony structure supporting or enclosing organs (especially the inner sides of the feet)
- (used of behavior or attitude) characteristic of those who treat others with condescension (同)condescending, patronizing, patronising
- form an arch or curve; "her back arches"; "her hips curve nicely" (同)curve, arc
- naughtily or annoyingly playful; "teasing and worrying with impish laughter"; "a wicked prank" (同)impish, implike, mischievous, pixilated, prankish, puckish, wicked
- destroy the peace or tranquility of; "Dont interrupt me when Im reading" (同)disturb
- terminate; "She interrupted her pregnancy"; "break a lucky streak"; "break the cycle of poverty" (同)break
- a signal that temporarily stops the execution of a program so that another procedure can be carried out
- interfere in someone elses activity; "Please dont interrupt me while Im on the phone" (同)disrupt
- make a break in; "We interrupt the program for the following messages" (同)disrupt, break_up, cut_off
- a continuous portion of a circle
- constructed with or in the form of an arch or arches; "an arched passageway"
- discontinued temporarily; "we resumed the interrupted discussion"
PrepTutorEJDIC
- (建物の)『アーチ』,迫持(せりもち) / アーチ型の記念碑,弓形門 / 『弓形のもの』 / (足の)土踏まず / …'を'弓形にする / …‘に'アーチをかける / 弓形になる,弓状に伸びる
- 《名詞の前にのみ用いて》おもな,主要な(chief) / (おもに女・子供が)ずるそうな,いたずらそうな(mischievous)
- (行動や話の途中で)〈人〉‘を'『さえぎる』,妨げる / 〈行為・話など〉‘を'『中断する』 / 〈物事〉‘を'さえぎる / 『じゃまする』,話の腰を折る
- 『弧』,円弧 / 電弧(2点間を弧状に流れる電流) / 弧を描く / 電弧を生じる
- アーチ形の,弓形の / アーチのある
Wikipedia preview
出典(authority):フリー百科事典『ウィキペディア(Wikipedia)』「2015/09/30 08:58:15」(JST)
[Wiki en表示]
Interrupted aortic arch |
Classification and external resources |
Specialty |
medical genetics |
ICD-10 |
Q25.2 (EUROCAT) |
ICD-9-CM |
747.11 |
eMedicine |
ped/2515 |
Interrupted aortic arch is a very rare heart defect (affecting 3 per million live births)[1] in which the aorta is not completely developed. There is a gap between the ascending and descending thoracic aorta. In a sense it is the complete form of a coarctation of the aorta. Almost all patients also have other cardiac anomalies, including a ventricular septal defect (VSD), aorto-pulmonary window, and truncus arteriosus. Interrupted aortic arch is often associated with DiGeorge syndrome.[2]
Contents
- 1 Diagnosis
- 2 Treatment
- 3 References
- 4 External links
Diagnosis
It can be diagnosed with an echocardiogram. Patients will have a loss of appetite, turn pale, may feel cold in the lower half of the body due to not enough blood flow.
Treatment
Treatment consists of open heart surgery soon after birth. Awaiting surgery, prostaglandin can be administered to keep the ductus arteriosus open, thereby allowing blood flow to the lower body. Failure to treat the condition yields a mortality rate of 90% at a median age of 4 days.[1]
References
- ^ a b Messner, Greg; Reul, George J.; Flamm, Scott D.; Gregoric, Igor D.; Opfermann, Ulrich Tim (2002). "Interrupted aortic arch in an adult single-stage extra-anatomic repair". Texas Heart Institute journal / from the Texas Heart Institute of St. Luke's Episcopal Hospital, Texas Children's Hospital 29 (2): 118–21. PMC 116738. PMID 12075868.
- ^ Chin, Alvin J (Oct 2, 2007). "Interrupted Aortic Arch". eMedicine. Retrieved May 27, 2009.
External links
- C.S. Mott Children's Hospital, Congenital Heart Center: Interrupted Aortic Arch at umich.edu
- Heart center encyclopedia at cincinnatichildrens.orgcincinnatichildrens.org
- Collins-Nakai, RL; Dick, M; Parisi-Buckley, L; Fyler, DC; Castaneda, AR (1976). "Interrupted aortic arch in infancy". The Journal of pediatrics 88 (6): 959–62. doi:10.1016/S0022-3476(76)81049-9. PMID 1271195.
Congenital vascular defects / Vascular malformation (Q25–Q28, 747)
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Great arteries/
other arteries |
Aorta |
- Patent ductus arteriosus
- Coarctation of the aorta
- Interrupted aortic arch
- Double aortic arch
- Right-sided aortic arch
- Overriding aorta
- Aneurysm of sinus of Valsalva
- Vascular ring
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Pulmonary artery |
- Pulmonary atresia
- Stenosis of pulmonary artery
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Subclavian artery |
- Aberrant subclavian artery
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Umbilical artery |
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Great veins |
Superior/inferior vena cava |
- Congenital stenosis of vena cava
- Persistent left superior vena cava
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Pulmonary vein |
- Anomalous pulmonary venous connection (Total, Partial)
- Scimitar syndrome
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Arteriovenous malformation |
- Cerebral arteriovenous malformation
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Index of the circulatory system
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Description |
- Anatomy
- Arteries
- head and neck
- arms
- chest
- abdomen
- legs
- Veins
- head and neck
- arms
- chest
- abdomen and pelvis
- legs
- Development
- Cells
- Physiology
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Disease |
- Congenital
- Neoplasms and cancer
- Lymphatic vessels
- Injury
- Vasculitis
- Other
- Symptoms and signs
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Treatment |
- Procedures
- Drugs
- beta blockers
- channel blockers
- diuretics
- nonsympatholytic vasodilatory antihypertensives
- peripheral vasodilators
- renin–angiotensin system
- sympatholytic antihypertensives
- vasoprotectives
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UpToDate Contents
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English Journal
- Type B Aortic Arch Interruption in an Adult.
- Abdoli S1, Tatum JM1, Fratello AL1, Bowdish ME1, Baker CJ2.
- The Annals of thoracic surgery.Ann Thorac Surg.2016 Nov;102(5):e431-e432. doi: 10.1016/j.athoracsur.2016.04.040.
- The presentation and treatment of a patient with a type B interrupted aortic arch with an isolated left subclavian artery is described.Copyright © 2016 The Society of Thoracic Surgeons. Published by Elsevier Inc. All rights reserved.
- PMID 27772600
- Prevalence of Noncardiac and Genetic Abnormalities in Neonates Undergoing Cardiac Operations: Analysis of The Society of Thoracic Surgeons Congenital Heart Surgery Database.
- Patel A1, Costello JM2, Backer CL3, Pasquali SK4, Hill KD5, Wallace AS5, Jacobs JP6, Jacobs ML7.
- The Annals of thoracic surgery.Ann Thorac Surg.2016 Nov;102(5):1607-1614. doi: 10.1016/j.athoracsur.2016.04.008. Epub 2016 Jun 17.
- BACKGROUND: Among patients with congenital heart disease (CHD), the coexistence of noncardiac congenital anatomic abnormalities (NC), genetic abnormalities (GA), and syndromes (S) may influence therapeutic strategies and outcomes. The appreciated prevalence of these abnormalities has risen because i
- PMID 27319986
- Unusual late discovery of interrupted aortic arch by ultrasonography and three-dimensional MDCT.
- Pasteur-Rousseau A1, Dridi L2, Fitoussi A3, Peric AS4, Dautry R4, Dohan A4, Bonnin P5, Soyer P6.
- Diagnostic and interventional imaging.Diagn Interv Imaging.2016 Oct 3. pii: S2211-5684(16)00072-3. doi: 10.1016/j.diii.2016.02.003. [Epub ahead of print]
- PMID 26947723
Japanese Journal
- 手術の工夫 大動脈弓離断術後上行大動脈狭窄に対する自家肺動脈パッチによる拡大形成術
- 胸部外科 = The Japanese journal of thoracic surgery 67(9), 800-804, 2014-08
- NAID 40020162123
- 両側肺動脈絞扼術後に根治手術(大動脈弓再建+動脈スイッチ手術+心室内血流路作成)を施行した両大血管右室起始・大動脈弓離断症の1例
- A Case Report of Persistent Fifth Aortic Arch Presenting With Severe Left Ventricular Dysfunction
Related Links
- In patients with interrupted aortic arch, oxygen-rich blood from the left side of the heart is not able to reach all areas of the body because of the defect in the aortic arch. An infant with interrupted aortic arch must depend on an ...
- (rollover to compare with normal) What Is It? This rare genetic disorder involves two defects. First, the Aortic Arch does not form a complete tube and is divided, or "interrupted" (see upper arrow in diagram). The aortic arch is the part of ...
★リンクテーブル★
[★]
- ファロー四徴症
- DiGeoge症候群(ほとんどの患者で見られる):本疾患は流出路に関する心奇形と関連している
[★]
- 英
- aortic arch interruption, interrupted aortic arch IAA
- 同
- 大動脈弓欠損症 absence of aortic arch
- 関
- coarctation of the aorta
[★]
- 関
- abort、break、discontinuance、discontinuation、discontinue、discontinuity、disturb、disturbance、hamper、hindrance、impede、impediment、intercept、interception、interfere、interruption、obstruct、occlude、occlusion、preclude、preclusion、prevent
[★]
- 関
- AIDS-related complex、lymphadenopathy syndrome
[★]
- 関
- arcuate
[★]
- 関
- aorta、aortae、aortal
[★]
- 関
- intermittent