大動脈弓離断症
WordNet
- a passageway under a curved masonry construction; "they built a triumphal arch to memorialize their victory" (同)archway
- (architecture) a masonry construction (usually curved) for spanning an opening and supporting the weight above it
- a curved shape in the vertical plane that spans an opening
- expert in skulduggery; "an arch criminal"
- a curved bony structure supporting or enclosing organs (especially the inner sides of the feet)
- (used of behavior or attitude) characteristic of those who treat others with condescension (同)condescending, patronizing, patronising
- form an arch or curve; "her back arches"; "her hips curve nicely" (同)curve, arc
- naughtily or annoyingly playful; "teasing and worrying with impish laughter"; "a wicked prank" (同)impish, implike, mischievous, pixilated, prankish, puckish, wicked
- some abrupt occurrence that interrupts an ongoing activity; "the telephone is an annoying interruption"; "there was a break in the action when a player was hurt" (同)break
- a continuous portion of a circle
- constructed with or in the form of an arch or arches; "an arched passageway"
PrepTutorEJDIC
- (建物の)『アーチ』,迫持(せりもち) / アーチ型の記念碑,弓形門 / 『弓形のもの』 / (足の)土踏まず / …'を'弓形にする / …‘に'アーチをかける / 弓形になる,弓状に伸びる
- 《名詞の前にのみ用いて》おもな,主要な(chief) / (おもに女・子供が)ずるそうな,いたずらそうな(mischievous)
- 〈U〉〈C〉(…の)じゃま,妨害,中断《+『of』+『名』》 / 〈C〉妨害する物;さえぎる物
- 『弧』,円弧 / 電弧(2点間を弧状に流れる電流) / 弧を描く / 電弧を生じる
- アーチ形の,弓形の / アーチのある
- are (面積の単位)の変形
Wikipedia preview
出典(authority):フリー百科事典『ウィキペディア(Wikipedia)』「2014/04/03 11:05:41」(JST)
[Wiki en表示]
Interrupted aortic arch |
Classification and external resources |
ICD-10 |
Q25.2 (EUROCAT) |
ICD-9 |
747.11 |
eMedicine |
ped/2515 |
Interrupted aortic arch is a very rare heart defect (affecting 3 per million live births)[1] in which the aorta is not completely developed. There is a gap between the ascending and descending thoracic aorta. In a sense it is the complete form of a coarctation of the aorta. Almost all patients also have other cardiac anomalies. Interrupted aortic arch is often associated with DiGeorge syndrome.[2]
Contents
- 1 Diagnosis
- 2 Treatment
- 3 References
- 4 External links
Diagnosis[edit]
It can be diagnosed with an echocardiogram. Patients will have a loss of appetite, turn pale, may feel cold in the lower half of the body due to not enough blood flow.
Treatment[edit]
Treatment consists of open heart surgery soon after birth. Awaiting surgery, prostaglandin can be administered to keep the ductus arteriosus open, thereby allowing blood flow to the lower body. Failure to treat the condition yields a mortality rate of 90% at a median age of 4 days.[1]
References[edit]
- ^ a b Messner, Greg; Reul, George J.; Flamm, Scott D.; Gregoric, Igor D.; Opfermann, Ulrich Tim (2002). "Interrupted aortic arch in an adult single-stage extra-anatomic repair". Texas Heart Institute journal / from the Texas Heart Institute of St. Luke's Episcopal Hospital, Texas Children's Hospital 29 (2): 118–21. PMC 116738. PMID 12075868.
- ^ Chin, Alvin J (Oct 2, 2007). "Interrupted Aortic Arch". eMedicine. Retrieved May 27, 2009.
External links[edit]
- C.S. Mott Children's Hospital, Congenital Heart Center: Interrupted Aortic Arch at umich.edu
- Heart center encyclopedia at cincinnatichildrens.orgcincinnatichildrens.org
- Collins-Nakai, RL; Dick, M; Parisi-Buckley, L; Fyler, DC; Castaneda, AR (1976). "Interrupted aortic arch in infancy". The Journal of pediatrics 88 (6): 959–62. doi:10.1016/S0022-3476(76)81049-9. PMID 1271195.
Congenital vascular defects / Vascular malformation (Q25–Q28, 747)
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Great arteries/
other arteries |
Aorta
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- Patent ductus arteriosus
- Coarctation of the aorta
- Interrupted aortic arch
- Double aortic arch
- Right-sided aortic arch
- Overriding aorta
- Aneurysm of sinus of Valsalva
- Vascular ring
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Pulmonary artery
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- Pulmonary atresia
- Stenosis of pulmonary artery
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Subclavian artery
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- Aberrant subclavian artery
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Umbilical artery
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Great veins |
Superior/inferior vena cava
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- Congenital stenosis of vena cava
- Persistent left superior vena cava
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Pulmonary vein
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- Anomalous pulmonary venous connection (Total, Partial)
- Scimitar syndrome
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Arteriovenous malformation |
- Cerebral arteriovenous malformation
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anat (a:h/u/t/a/l,v:h/u/t/a/l)/phys/devp/cell/prot
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noco/syva/cong/lyvd/tumr, sysi/epon, injr
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proc, drug (C2s+n/3/4/5/7/8/9)
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UpToDate Contents
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English Journal
- Aortic Arch Reconstruction in Neonates with Biventricular Morphology: Increased Risk for Development of Recoarctation by Use of Autologous Pericardium.
- Bechtold C1, Purbojo A1, Schwitulla J2, Glöckler M3, Toka O3, Dittrich S3, Cesnjevar RA1, Rüffer A1.
- The Thoracic and cardiovascular surgeon.Thorac Cardiovasc Surg.2015 Aug;63(5):373-9. doi: 10.1055/s-0034-1396532. Epub 2015 Jan 8.
- Background The aim of this study was to analyze risk factors promoting development of recoarctation (Re-CoA) in neonates who survived aortic arch repair from an anterior approach. Methods Fifty consecutive neonates with biventricular morphology and ductal-dependent lower body perfusion who were
- PMID 25569698
- 3D MDCT angiography for the preoperative assessment of truncus arteriosus.
- Hong SH1, Kim YM2, Lee CK1, Lee CH3, Kim SH4, Lee SY4.
- Clinical imaging.Clin Imaging.2015 Jul 19. pii: S0899-7071(15)00184-9. doi: 10.1016/j.clinimag.2015.07.019. [Epub ahead of print]
- Truncus arteriosus is an uncommon conotruncal anomaly, which is amenable to surgical correction. The systemic, pulmonary, and coronary circulations originate from a single arterial vessel that arises from the ventricular part of the heart and overrides the ventricular septum. The value of multidetec
- PMID 26253771
- An inoperable aortic arch interruption in a patient with differential cyanosis.
- Fan C1, Yang J2.
- European heart journal.Eur Heart J.2015 Jul 3. pii: ehv287. [Epub ahead of print]
- PMID 26141395
Japanese Journal
- 大動脈縮窄,大動脈弓離断合併の複雑心奇形に対する段階的修復の成績
- 木戸 高志,西垣 恭一,川平 洋一,前畠 慶人,村上 洋介,江原 英治,鈴木 嗣敏,小澤 有希,平野 恭悠
- Pediatric Cardiology and Cardiac Surgery 29(4), 171-175, 2013
- 背景:当センターでは,複雑心奇形を合併する大動脈縮窄,大動脈弓離断(CoA/IAA)に対し,新生児期の人工心肺を回避する目的で,初回手術で側開胸下に拡大大動脈弓吻合法による大動脈弓再建(EEDA)と肺動脈絞扼術(PAB)を行う段階的修復を基本方針とし,低体重,大動脈弓低形成を認める症例に対しては両側肺動脈絞扼術(BPAB)を先行させた段階的修復を施行してきた.対象・方法:対象は,1996~2009 …
- NAID 130003380034
- 大動脈離断または縮窄を伴う機能的単心室に対する外科治療
- 大動脈縮窄・離断を伴う機能的単心室に対する外科治療
- 盤井 成光,川田 博昭,小澤 秀登,山内 早苗,金谷 知潤,萱谷 太,稲村 昇,岸本 英文
- Pediatric Cardiology and Cardiac Surgery 29(2), 92-97, 2013
- … <B>目的</B>:大動脈縮窄・離断(CoA・IAA)を伴う機能的単心室(f-SV)に対する外科治療成績を検討した.<BR><B>方法</B>:CoA・IAAを伴うf-SVに対し, 初回手術として両側肺動脈絞扼術(bil.PAB)を施行した13例と, 大動脈弓修復+肺動脈絞扼(Arch repair+PAB)を施行した11例を対象とし, 手術成績と心機能につき比較検討した. …
- NAID 130003380020
Related Links
- Clinical description Patients with AAI present, like other ductal dependent left-sided, heart obstructive lesions, with acute cardiovascular collapse or heart failure after spontaneous closure of the ductus arteriosus in the first days of life.
- CELORIA GC, PATTON RB. Congenital absence of the aortic arch. Am Heart J. 1959 Sep; 58:407–413. [PubMed] DAVES ML, TREGER A. VERTEBRAL GRAND LARCENY. Circulation. 1964 Jun; 29:911–913. [PubMed] Everts ...
★リンクテーブル★
[★]
- 英
- aortic arch interruption, interrupted aortic arch IAA
- 同
- 大動脈弓欠損症 absence of aortic arch
- 関
- coarctation of the aorta
[★]
- 関
- abort、break、discontinuance、discontinuation、discontinue、discontinuity、disturb、disturbance、hamper、hindrance、impede、impediment、intercept、interception、interfere、interrupt、obstruct、occlusion、preclusion
[★]
- 関
- AIDS-related complex、lymphadenopathy syndrome
[★]
- 関
- arcuate
[★]
- 関
- aorta、aortae、aortal