UpToDate Contents

全文を閲覧するには購読必要です。 To read the full text you will need to subscribe.

1. 表皮水疱症のマネージメントの概要 overview of the management of epidermolysis bullosa
2. 表皮水疱症の診断 diagnosis of epidermolysis bullosa
3. 表皮水疱症の疫学、病因、分類、および臨床的特徴 epidemiology pathogenesis classification and clinical features of epidermolysis bullosa
4. 後天性表皮水疱症 epidermolysis bullosa acquisita
5. 遺伝性皮膚症 the genodermatoses

English Journal

Miquel J, Chevrant-Breton J, Dupuy A, Le Gall F, Bourdon-Lannoy E, Adamski H, Bodemer C.SourceService de dermatologie, hôpital Pontchaillou, CHU, 2, rue Henri-le-Guilloux, 35033 Rennes, France. Juliette.miquel@chu-rennes.fr
Annales de dermatologie et de vénéréologie.Ann Dermatol Venereol.2012 Jun;139(6-7):435-43. Epub 2012 May 21.
BACKGROUND: EB naevus (EBN) are little-known, atypical, eruptive, pigmented melanocytic lesions that may occur in former sites of bullae occurring in epidermolysis bullosa hereditaria (EBH). We sought to describe the characteristics of such lesions and assess their course.PATIENTS AND METHODS: This
PMID 22721475

Le Roux-Villet C, Prost-Squarcioni C.SourceService de dermatologie, Centre de référence maladies rares national, pour les dermatoses bulleuses toxiques et auto-immunes, sites Avicenne et Saint-Louis, hôpital Avicenne, 125 rue de Stalingrad, Bobigny, France.
Annales de dermatologie et de vénéréologie.Ann Dermatol Venereol.2011 Mar;138(3):228-46. Epub 2011 Feb 24.
INTRODUCTION: Epidermolysis bullosa acquisita (EBA) is the rarest of the autoimmune bullous diseases (AIBD). It is defined as an AIBD secondary to production of antibodies directed against type VII collagen and then binding to anchoring fibrils in the basal membrane zone (BMZ) of the skin and the Ma
PMID 21397153

川本真一郎
日本補綴歯科学会誌 5(1), 100-103, 2013
症例の概要：患者は先天性表皮水疱症の既往がある上下無歯顎の男性．口腔粘膜に水疱や糜爛を生じやすく，義歯の装着に支障をきたすため，インプラント治療を希望して来院した．考察：下顎はインプラント支持の可撤性ブリッジ，上顎は通常の全部床義歯により咬合回復とそれに伴う口腔機能向上を図ることができた．バーアタッチメントの適用によりブリッジの強固な支持と維持が可能になったことと先天性表皮水疱症の影響下にあると考 …
NAID 130004544604