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1. 表皮水疱症の診断 diagnosis of epidermolysis bullosa
2. 表皮水疱症のマネージメントの概要 overview of the management of epidermolysis bullosa
3. 表皮水疱症の疫学、病因および臨床的特徴 epidemiology pathogenesis and clinical features of epidermolysis bullosa
4. 後天性表皮水疱症 epidermolysis bullosa acquisita
5. 皮膚の水疱を有する患者に対するアプローチ approach to the patient with cutaneous blisters

English Journal

Chemical shift assignments of the fibronectin III like domains 7-8 of type VII collagen.

Hermsdorf U1, Seeger K2.
Biomolecular NMR assignments.Biomol NMR Assign.2016 Apr;10(1):53-5. doi: 10.1007/s12104-015-9636-9. Epub 2015 Sep 12.
Type VII collagen (Col7) is important for skin stability. This is underlined by the severe skin blistering phenotype in the Col7 related diseases dystrophic epidermolysis bullosa and epidermolysis bullosa acquisita (EBA). Col7 has a large N-terminal non-collagenous domain (NC1) that is followed by t
PMID 26364055

Skin microbiota-associated inflammation precedes autoantibody induced tissue damage in experimental epidermolysis bullosa acquisita.

Ellebrecht CT1, Srinivas G2, Bieber K3, Banczyk D4, Kalies K4, Künzel S2, Hammers CM3, Baines JF2, Zillikens D3, Ludwig RJ3, Westermann J4.
Journal of autoimmunity.J Autoimmun.2016 Apr;68:14-22. doi: 10.1016/j.jaut.2015.08.007. Epub 2015 Sep 1.
Epidermolysis bullosa acquisita (EBA) is a chronic autoimmune blistering skin disease characterized by autoantibodies against type VII collagen (COL7). Immunization of SJL/J mice with recombinant murine COL7 results in break of tolerance and skin blisters. Strikingly, despite circulating autoantibod
PMID 26341384

Feasibility, efficacy, and safety of ultrasound-guided axillary plexus blockade in pediatric patients with epidermolysis bullosa dystrophica.

van den Heuvel I1, Gottschalk A2, Langer M3, Hahnenkamp K4, Ellger B2.
Paediatric anaesthesia.Paediatr Anaesth.2016 Apr;26(4):405-8. doi: 10.1111/pan.12860. Epub 2016 Feb 9.
BACKGROUND: In patients suffering from epidermolysis bullosa dystrophica (DEB), the most severe form of epidermolysis bullosa, trauma or friction cause separation of the skin from underlying tissue with consecutive painful blisters, scarifications, contractures, and pseudosyndactyly. To retain funct
PMID 26857539

武藤正彦
山口医学 62(4), 199-204, 2013-11-01
… The seven diseases consisted of pemphigus, epidermolysis bullosa, congenital ichthyosiform erythroderma, generalized pustular psoriasis, neurofibromatosis(I･II),xeroderma pigmentosum, and tuberous sclerosis（Bourneville-Pringle diseases）．We are trying to develop bio bank for a continuous medical research for the intractable skin diseases. …
NAID 120005399164

Measurement of protease activity of exfoliative toxin A using synthetic peptidyl substrates and correlation between in vivo and in vitro activities

Tachi Mizuki T.,Ohara-Nemoto Yuko,Baba Tomomi T.,Kobayakawa Takeshi,Fujita Shuichi,Ikeda Tohru,Ayuse Takao,Oi Kumiko,Nemoto Takayuki K.
Acta medica Nagasakiensia 58(2), 41-48, 2013-08
… In accord with these results, intraepidermal blister formation and epidermolysis were induced more exclusively by Glu39-ETA than Phe24-ETA. …
NAID 110009614178

関: dominant epidermolysis bullosa dystrophica、dystrophic epidermolysis bullosa、recessive epidermolysis bullosa dystrophica

リンク元	「表皮溶解」「表皮融解」
拡張検索	「epidermolysis bullosa dystrophica」「epidermolysis bullosa hereditaria」「dystrophic epidermolysis bullosa」