- 英
- endovascular papillary angioendothelioma
- 同
- ダブスカ腫瘍 Dabska tumor
- 血管内乳頭状血管内皮腫は、1969年Dabskaによって最初に定義されたまれな血管腫。
- 小児ないし若年成人の皮膚または皮下に生じる
- 顕微鏡的には血管の吻合から構成され、それらのうちのいくらかは、時に乳頭状突起あるいは腎糸球体に似た房のような構造からなる。
- 領域リンパ節への転移例で報告されている例があるが、長期予後は一般によい。
参考
- [原著]Malignant endovascular papillary angioendothelioma of the skin in childhood. Clinicopathologic study of 6 cases.
- Dabska M.
- Cancer.Cancer.1969 Sep;24(3):503-10.
- PMID 5343389
- http://emedicine.medscape.com/article/1112873-overview
UpToDate Contents
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- 1. Tufted angioma, kaposiform hemangioendothelioma (KHE), and Kasabach-Merritt phenomenon (KMP)tufted angioma kaposiform hemangioendothelioma khe and kasabach merritt phenomenon kmp [show details]
… different from other forms of disseminated intravascular coagulation or localized intravascular coagulopathy,… Tufted angioma and kaposiform hemangioendothelioma (KHE) are rare, vascular tumors that typically occur during infancy or early childhood. Tufted angioma, previously known as "angioblastoma of Nakagawa … the subcutis in a so-called "cannonball" pattern . These capillary tufts are surrounded by cleft-like, semilunar, empty, vascular spaces. Thin-walled, lymphatic spaces may be seen throughout the dermis …
- 2. 成人の播種性血管内凝固 (DIC)に対する評価およびマネージメントevaluation and management of disseminated intravascular coagulation dic in adults [show details]
… Disseminated intravascular coagulation (DIC; also called consumption coagulopathy and defibrination syndrome) is a systemic process with the potential for causing thrombosis and hemorrhage.… NETs are web-like structures composed of decondensed chromatin coated with… including aortic aneurysm and Kaposiform hemangioendothelioma; Rattlesnake or other viper bite (considered by…
- 3. 悪性肝腫瘍の病理pathology of malignant liver tumors [show details]
… and multifocal papillary epithelial lesions with or without mucin production This rare type of tumor resembles its counterpart: the intraductal papillary mucinous neoplasm… or cellular "ovarian-like" stroma is characteristic of these lesions, often requiring extensive sampling to demonstrate its presence. The cellular "ovarian-like" stroma is seen… (cholangiocarcinoma and biliary cystadenocarcinoma), endothelial cells (angiosarcoma, epithelioid hemangioendothelioma), or combinations of these cells with various mesenchymal cells (eg, hepatoblastoma) . Some …
- 4. 甲状腺結節および非髄様甲状腺癌におけるオンコジーンおよび腫瘍抑制遺伝子oncogenes and tumor suppressor genes in thyroid nodules and nonmedullary thyroid cancer [show details]
… cell-derived neoplasm has been identified, termed noninvasive follicular thyroid neoplasm with papillary-like nuclear features (NIFTP) . Preliminary studies suggest that the most frequent gene mutations …
- 5. 冠循環の血管内超音波、光干渉断層撮影、および血管内視鏡intravascular ultrasound optical coherence tomography and angioscopy of coronary circulation [show details]
… The intravascular imaging techniques of optical coherence tomography (OCT), intravascular ultrasound (IVUS),… three types of neointimal layer were observed: a white layer with a cotton-like surface,…
Related Links
- 血管内乳頭状内皮腫 Endovascular papillary angioendothelioma (Dabska) 2) 類上皮血管内皮腫 Epithelioid hemagioendothelioma 良悪性中間群の病変で、肺で最初に報告され、軟部、骨、肝、脳 などで報告。組織学的に腫瘍 ...
- 紡錘細胞血管内皮腫(spindle-cell hemangioendothelioma) p.404 血管外皮細胞腫(hemangiopericytoma) p.404 化膿性肉芽腫(pyogenic granuloma) p.402 血管内乳頭状内皮細胞増殖症 (intravascular papillary endothelial ...
- 血管腫とは、血管が拡張したり増殖したりすることによってできる良性腫瘍のことを指します。医学的に血管内皮細胞の増殖を伴うものは血管腫、増殖を伴わず脈管の形成異常によるものは血管奇形と分類されています。
Related Pictures
★リンクテーブル★
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血管内乳頭状血管内皮腫。ダブスカ腫瘍
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血管内乳頭状血管内皮腫
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血管内乳頭状血管内皮腫
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- 英
- blood vessel, blood vessels
構造
- 内皮細胞(単層扁平上皮細胞)
- 基底板
- 内皮下結合組織(内皮下層 subendothelial layer):疎性結合組織、縦走平滑筋
- 内弾性板
分類
[★]
- 英
- endothelium (Z)
- 関
- 血管
Table 10-1. Endothelial Cell Properties and Functions
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Maintenance of Permeability Barrier
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Elaboration of Anticoagulant, Antithrombotic, Fibrinolytic Regulators
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prostacyclin
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thrombomodulin
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heparin-like molecules
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plasminogen activator
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Elaboration of Prothrombotic Molecules
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Von Willebrand factor
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Tissue factor
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Plasminogen activator inhibitor
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Extracellular Matrix Production (Collagen, Proteoglycans)
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Modulation of Blood Flow and Vascular Reactivity
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Vasconstrictors: endothelin, ACE
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Vasodilators: NO, prostacyclin
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Regulation of Inflammation and Immunity
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IL-1, IL-6, chemokines
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Adhesion molecules: VCAM-1, ICAM, E-selectin P-selectin
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Histocompatibility antigens
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Regulation of Cell Growth
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Growth stimulators: PDGF, CSF, FGF
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Growth inhibitors: heparin, TGF-β
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Oxidation of LDL
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[★]
- 英
- nipple, papilla
- ラ
- papilla mammae
- 関
- 乳房
位置
- 鎖骨中線のあたりであって、T4-T5肋骨の間、すなわち第4肋間隙にある(♂)、と思われる。
- 上記の位置は、性差・個体差あり(KL.265)
臨床関連
- 胸骨圧迫(心臓マッサージ):圧迫部位は両乳頭のを結ぶ線と胸骨が交わる部位である。胸骨のやや下部となる。
[★]
- 英
- intravascular、endovascular、intravascularly、endovascularly
- 関
- 静脈内
[★]
- 関
- がん、腫瘍、腫瘤、良性新生物