フィブリノーゲン欠乏症、フィブリノゲン欠乏症
- 関
- afibrinogenemia
WordNet
- the absence of fibrinogen in the plasma leading to prolonged bleeding
- a protein present in blood plasma; converts to fibrin when blood clots (同)factor_I
PrepTutorEJDIC
- 〈U〉〈C〉(…の)(量・額などの)不足,欠乏《+『of』(『in』)+『名』》 / 〈C〉不足分,不足量,不足額 / 〈C〉(精神・肉体などの)欠陥
UpToDate Contents
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English Journal
- Advances in the treatment of inherited coagulation disorders.
- Escobar MA.SourceDepartment of Pediatrics and Internal Medicine, Division of Hematology, University of Texas Medical School at Houston, Houston, Texas.
- Haemophilia : the official journal of the World Federation of Hemophilia.Haemophilia.2013 Apr 22. doi: 10.1111/hae.12137. [Epub ahead of print]
- Inherited coagulation disorders constitute a broad spectrum of coagulation factor deficiencies that include X-linked factor (F)VIII or FIX deficiency that causes haemophilia, and autosomal recessive disorders producing heterogeneous deficiencies in fibrinogen (FI), prothrombin (FII), FV, FVII, FX, F
- PMID 23600951
- [Transfusion of plasma: Products - Indications.]
- Djoudi R.SourceEFS Alsace, BP 36, 10, rue Spielmann, 67065 Strasbourg cedex, France. Electronic address: rachid.djoudi@efs-alsace.fr.
- Transfusion clinique et biologique : journal de la Societe francaise de transfusion sanguine.Transfus Clin Biol.2013 Apr 12. pii: S1246-7820(13)00011-6. doi: 10.1016/j.tracli.2013.02.005. [Epub ahead of print]
- The use of therapeutic plasma has increased in France by more than 40% since 2002. This growth may be explained by the improvement in transfusion safety, the diminution of the risk of transmission of pathogens and the regained confidence of the physicians in blood products. Therapeutic plasma also b
- PMID 23587624
- Molecular basis of quantitative fibrinogen disorders in 27 patients from India.
- Sumitha E, Jayandharan GR, Arora N, Abraham A, David S, Sankari Devi G, Shenbagapriya P, Nair SC, George B, Mathews V, Chandy M, Viswabandya A, Srivastava A.SourceDepartments of Hematology, Christian Medical College, Vellore, India.
- Haemophilia : the official journal of the World Federation of Hemophilia.Haemophilia.2013 Apr 8. doi: 10.1111/hae.12143. [Epub ahead of print]
- Congenital fibrinogen deficiency is an extremely rare (1:1 000 000) hereditary bleeding disorder caused by defects in genes coding for fibrinogen Aα-, Bβ- and γ-chains, respectively. We report here the molecular basis of fibrinogen deficiency in a large series of patients from India. Twenty-sev
- PMID 23560673
Japanese Journal
- 症例報告 第169回日本血液学会例会:臼杵憲祐例会長 推薦演題 慢性骨髄性白血病の発症で偶発的に発見された先天性フィブリノゲン異常症
- 内藤 祐,林 宜亨,秋野 光明,若本 志乃舞,藤原 満博,本間 稚広,池田 久實,髙本 滋
- 日本輸血細胞治療学会誌 60(6), 577-584, 2014
- 日本において,新鮮凍結血漿-LR(FFP-LR)は融解後3時間以内に使用することとされている.欧米のように,融解後の使用期限が延長できれば,新生児医療や緊急性の高い救命救急での使用可能範囲は広くなると考える.我々は各血液凝固因子の活性に加えて,凝固反応の全体像が評価可能なトロンビン生成能の経時変化を検討し,FFP-LR融解後の品質について,保存温度を含めた評価を改めて試みた.その結果,血液凝固因子 …
- NAID 130004948933
- 慢性骨髄性白血病の発症で偶発的に発見された先天性フィブリノゲン異常症
- 桐原 健彦,藤川 祐子,武田 航,栗原 太郎,佐藤 慶二郎,植木 俊充,廣島 由紀,住 昌彦,上野 真由美,市川 直明,新井 慎平,征矢 佳輔,奥村 伸生,小林 光
- 臨床血液 55(5), 541-545, 2014
- … 当科紹介受診し,末梢血・骨髄で各成熟段階の白血球増多およびフィブリノゲン(fibrinogen, Fbg)低値を認めた。 …
- NAID 130004501848
Related Pictures
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![Disease Overview | Rare Coagulation](https://1mg.info/0/f/9/2135.jpg)
![Fibrinogen Deficiency:](https://1mg.info/0/f/9/2136.jpg)
![Figure 6 : Transglutaminases: crosslinking](https://1mg.info/0/f/9/2137.jpg)
![About RiaSTAP: Treatment for CFD](https://1mg.info/0/f/9/2138.jpg)
★リンクテーブル★
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- 英
- fibrinogen deficiency
- 関
- 無フィブリノーゲン血症、フィブリノゲン欠乏症
[★]
- 英
- fibrinogen deficiency
- 関
- フィブリノーゲン欠乏症
[★]
- 不足、欠乏、欠失、欠如、欠損、不十分。栄養不足、栄養素欠乏、欠乏症。(遺伝子)(染色体内の)遺伝子欠失
- 欠けているもの、不足している物。不足分。不完全なもの、欠点のあるもの
- 関
- absence, agenesis, dearth, defect, defective, deficient, deficit, delete, deletion, deletional, depletion, deprivation, deprive, lack, miss, missing, morphological defect, paucity, scarce, scarcity, starve