WordNet

the absence of fibrinogen in the plasma leading to prolonged bleeding
a protein present in blood plasma; converts to fibrin when blood clots (同)factor_I

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1. フィブリノゲンの異常 disorders of fibrinogen
2. 稀な（劣性遺伝性）凝固異常 rare recessively inherited coagulation disorders
3. 成人における播種性血管内凝固の臨床的特徴、診断、および治療 clinical features diagnosis and treatment of disseminated intravascular coagulation in adults
4. 出血性素因を有する成人患者へのアプローチ approach to the adult patient with a bleeding diathesis
5. 幼児および小児における播種性血管内凝固 disseminated intravascular coagulation in infants and children

Escobar MA.SourceDepartment of Pediatrics and Internal Medicine, Division of Hematology, University of Texas Medical School at Houston, Houston, Texas.
Haemophilia : the official journal of the World Federation of Hemophilia.Haemophilia.2013 Apr 22. doi: 10.1111/hae.12137. [Epub ahead of print]
Inherited coagulation disorders constitute a broad spectrum of coagulation factor deficiencies that include X-linked factor (F)VIII or FIX deficiency that causes haemophilia, and autosomal recessive disorders producing heterogeneous deficiencies in fibrinogen (FI), prothrombin (FII), FV, FVII, FX, F
PMID 23600951

Djoudi R.SourceEFS Alsace, BP 36, 10, rue Spielmann, 67065 Strasbourg cedex, France. Electronic address: rachid.djoudi@efs-alsace.fr.
Transfusion clinique et biologique : journal de la Societe francaise de transfusion sanguine.Transfus Clin Biol.2013 Apr 12. pii: S1246-7820(13)00011-6. doi: 10.1016/j.tracli.2013.02.005. [Epub ahead of print]
The use of therapeutic plasma has increased in France by more than 40% since 2002. This growth may be explained by the improvement in transfusion safety, the diminution of the risk of transmission of pathogens and the regained confidence of the physicians in blood products. Therapeutic plasma also b
PMID 23587624

Sumitha E, Jayandharan GR, Arora N, Abraham A, David S, Sankari Devi G, Shenbagapriya P, Nair SC, George B, Mathews V, Chandy M, Viswabandya A, Srivastava A.SourceDepartments of Hematology, Christian Medical College, Vellore, India.
Haemophilia : the official journal of the World Federation of Hemophilia.Haemophilia.2013 Apr 8. doi: 10.1111/hae.12143. [Epub ahead of print]
Congenital fibrinogen deficiency is an extremely rare (1:1 000 000) hereditary bleeding disorder caused by defects in genes coding for fibrinogen Aα-, Bβ- and γ-chains, respectively. We report here the molecular basis of fibrinogen deficiency in a large series of patients from India. Twenty-sev
PMID 23560673

内藤祐,林宜亨,秋野光明,若本志乃舞,藤原満博,本間稚広,池田久實,髙本滋
日本輸血細胞治療学会誌 60(6), 577-584, 2014
日本において，新鮮凍結血漿-LR（FFP-LR）は融解後3時間以内に使用することとされている．欧米のように，融解後の使用期限が延長できれば，新生児医療や緊急性の高い救命救急での使用可能範囲は広くなると考える．我々は各血液凝固因子の活性に加えて，凝固反応の全体像が評価可能なトロンビン生成能の経時変化を検討し，FFP-LR融解後の品質について，保存温度を含めた評価を改めて試みた．その結果，血液凝固因子 …
NAID 130004948933