systemic amyloidosis

全身性アミロイドーシス

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• 1. アミロイドーシスの概要overview of amyloidosis [show details]
  … include dialysis-related amyloidosis, heritable amyloidoses, age-related systemic amyloidosis and organ-specific amyloid. Clinical manifestations vary depending upon the type of amyloid and the distribution …
• 2. 免疫グロブリン軽鎖（AL）アミロイドーシスの臨床症状、検査所見、診断clinical presentation laboratory manifestations and diagnosis of immunoglobulin light chain al amyloidosis [show details]
  …Affected patients may have amyloidosis alone or in association with other plasma cell dyscrasias (multiple myeloma, Waldenstrom macroglobulinemia). All forms of systemic amyloidosis in which the fibrils are …
• 3. 免疫グロブリン軽鎖（AL）アミロイドーシスおよび軽鎖重鎖沈着症の治療と予後treatment and prognosis of immunoglobulin light chain al amyloidosis and light and heavy chain deposition diseases [show details]
  …deposits are not due to an underlying systemic clonal plasma cell disorder and do not progress to systemic disease . Patients with amyloid cardiomyopathy due to AL amyloidosis need careful management of cardiac …
• 4. AA（続発性）アミロイドーシスの治療treatment of aa secondary amyloidosis [show details]
  …an early phase trial in patients with systemic amyloidosis, including a patient with AA amyloidosis, as well as patients with AL and hereditary forms of amyloidosis . This approach may provide a new and …
• 5. AAアミロイドーシスの原因と診断およびリウマチ性疾患との関連性causes and diagnosis of aa amyloidosis and relation to rheumatic diseases [show details]
  … age-related systemic amyloidosis, and organ-specific amyloidosis. …

English Journal

• Ptosis and macroglossia in a woman with systemic light-chain amyloidosis.

• Hsiao PJ, Chang YC, Tsao YH, Wu KL, Kao YH, Chan JS, Wang CH, Lin YY, Chuu CP, Lin YS.
• Clinica chimica acta; international journal of clinical chemistry. 2019 Jul;494()112-115.
• Amyloidosis is a rare and variable disease, characterized by extracellular deposits of amyloid protein in different tissues and organs. Patients may present with a range of symptoms, depending on the extent of involvement. Rapid, accurate diagnosis is still challenging in clinical practice. A 72-y-o
• PMID 30905590

• Pinch purpura unmasking systemic amyloidosis.

• Apalla Z, Kirtsios TN, Katodritou E, Lallas A, Konstantinou D, Karamitsos T.
• International journal of dermatology. 2019 Jun;().
• PMID 31175659

• Schnitzler syndrome.

• Gellrich FF, Günther C.
• Der Hautarzt; Zeitschrift fur Dermatologie, Venerologie, und verwandte Gebiete. 2019 Jun;().
• Schnitzler syndrome is a very rare acquired systemic disease with many similarities to hereditary autoinflammatory syndromes. The main characteristics are generalized exanthema and IgM monoclonal gammopathy. Other clinical features include fever, muscle, bone, and/or joint pain, and lymphadenopathy
• PMID 31165908

Japanese Journal

• ALアミロイドーシスに対する造血幹細胞移植

• 塚田 信弘
• 血液内科 = Hematology 78(3), 430-436, 2019-03
• NAID 40021851208

• 全身性アミロイドーシスの伝播 (特集 認知症におけるタンパク質伝播について議論する)

• 樋口 京一
• Dementia Japan : 日本認知症学会誌 33(1), 23-30, 2019-01
• NAID 40021797261

• 下顎骨に発生した限局性アミロイドーシスの1例

• 幸地 真人,銘苅 泰明,上田 剛生,伊禮 充孝,比嘉 努,新垣 敬一
• 日本口腔外科学会雑誌 65(3), 205-210, 2019
• … <p>The authors report a case of localized amyloidosis arising in the mandible. … A diagnosis of amyloidosis was made based on the biopsy results. … Further testing done in our Hematology Department did not reveal systemic amyloidosis or multiple myeloma. … Excision was done with the patient under general anesthesia, and the histopathologic diagnosis was amyloidosis. …
• NAID 130007651429

Related Links

• Amyloidosis: Causes, Types, Symptoms, Diagnosis ...

Amyloidosis is when an abnormal protein called amyloid builds up in your tissues and organs. When it does, it affects their shape and how they work. Amyloidosis is a serious health problem that can lead to life-threatening organ ...

• Secondary systemic amyloidosis: MedlinePlus Medical ...

Secondary systemic amyloidosis is a disorder in which abnormal proteins build up in tissues and organs. Clumps of the abnormal proteins are called amyloid deposits. Secondary means it occurs because of another ...

• Systemic Amyloidoses - PubMed Central (PMC)

Differences between systemic and localized amyloidosis Amyloidoses are clinically heterogeneous because one or more organs (such as heart, kidneys, liver, pancreas, peripheral, autonomic, and central nervous ...

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★リンクテーブル★

リンク元	「全身性アミロイドーシス」
拡張検索	「senile systemic amyloidosis」
関連記事	「systemic」「system」「amyloidosis」

「全身性アミロイドーシス」

　　[★]

英

systemic amyloidosis

関

アミロイドーシス

アミロイドーシスの病型	アミロイド 蛋白	前駆体蛋白
１．免疫細胞性アミロイドーシス
1）AL型アミロイドーシス	AL	L鎖（ κ,λ ）
2）AH型アミロイドーシス	AH	Igγ
２．反応性AA型アミロイドーシス	AA	アポSAA
３．家族性アミロイドーシス
1）FAP I	ATTR	トランスサイレチン
2）FAP II	ATTR	トランスサイレチン
3）FAP III	AApoA1	アポA1
4）FAP IV	AGel1	ゲルソリン
5）家族性地中海熱	AA	アポSAA
6）Muckle-Wells症候群	AA	アポSAA
４．透析性アミロイドーシス	Aβ2M	β2マイクログロブリン
５．老人性TTR型アミロイドーシス	ATTR	トランスサイレチン

「senile systemic amyloidosis」

　　[★] 老人性全身性アミロイドーシス

「systemic」

　　[★]

• adj.

• 全身性の、全身的な、全身の、(植物)浸透移行性の

関

general、generalized、systemically、total body、whole body、whole-body

　 　

「system」

　　[★]

• n.

• 系、システム、体系、体制、方式

関

method、series、strain

　 　 　 　 　 　 　 　

「amyloidosis」

　　[★] アミロイドーシス アミロイド症