抗C1q血管炎
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- 1. 蕁麻疹性血管炎urticarial vasculitis [show details]
… pain; HUVS can occur independently or can be associated with other conditions . Diagnostic criteria for HUVS have been proposed . However, these criteria lack specificity, and a diagnosis of HUVS should …
- 2. 成人における血管炎の概要およびアプローチoverview of and approach to the vasculitides in adults [show details]
…IgAV, in place of Henoch-Schonlein purpura (HSP); anti-C1q vasculitis as an alternative name for hypocomplementemic urticarial vasculitis, abbreviated HUV; and use of the term "cryoglobulinemic vasculitis" …
- 3. 後天性C1インヒビター欠損症:臨床症状、疫学、病因、および診断acquired c1 inhibitor deficiency clinical manifestations epidemiology pathogenesis and diagnosis [show details]
…seen in hypocomplementemic urticarial vasculitis syndrome (HUVS) and systemic lupus erythematosus (SLE). Levels of C1q less than 30 percent of normal are typical of both conditions. However, HUVS usually …
- 4. 皮膚小血管性血管炎の概要overview of cutaneous small vessel vasculitis [show details]
…vessel vasculitis include antiglomerular basement membrane disease, IgAV (HSP), and hypocomplementemic urticarial vasculitis. Many medications can cause cutaneous small vessel vasculitis (CSVV), but penicillins…
- 5. 血清病および血清病様反応serum sickness and serum sickness like reactions [show details]
…hypocomplementemia and autoantibodies to the complement component C1q as part of the hypocomplementemic urticarial vasculitis syndrome. Children with immunoglobulin A vasculitis (IgA vasculitis; formerly called…
English Journal
Japanese Journal
- 症例報告 全身性エリテマトーデスの初発症状として低補体血症性蕁麻疹様血管炎(抗C1q血管炎)を認めた1例
- 望月 珠江,石黒 直子,阪 久美子,星 大介,川島 眞
- 臨床皮膚科 = Japanese journal of clinical dermatology 73(1), 19-22, 2019-01
- NAID 40021795728
- 血管性浮腫を伴った低補体血症性蕁麻疹様血管炎症候群の1例
- 東 典子,小豆澤 宏明,吉岡 華子,山岡 俊文,片山 一朗,榎本 圭佑
- 皮膚の科学 14(3), 123-129, 2015
- … 蕁麻疹様紅斑は,消退時の色素沈着は明らかではなかったが,皮膚生検にて核破砕性血管炎を認め,抗 C1q 抗体が 53.4U/ml(<15U/ml)と陽性であり,低補体血症性蕁麻疹様血管炎症候群と診断した。 …
- NAID 130005103409
- Immune Complex Vasculitis (2) Hypocomplementemic Urticarial Vasculitis (Anti-C1q Vasculitis) (特集 血管炎症候群 : 新しい分類と名称) -- (Small vessel vasculitis)
Related Links
- Anti-C1q or urticarial vasculitis is a form of cutaneous vasculitis characterised by inflammation of the small blood vessels. Urticarial Vasculitis can be classified into three subtypes. All are defined by a measure of the "complement" levels in the blood. The complement system is a set of proteins that contribute to and amplify immune responses.
- Other important autoantibodies in primary small vessel vasculitis are anti-glomerular basement membrane antibodies, anti-C1q, anti-galactose deficient IgA and cryoglobulins. A wide variety of systemic inflammatory diseases and infections can be complicated by small vessel vasculitis and detected by serological testing.
- Testing for C1q, anti-C1q, C3 and C4 complement components is essential to determine the type of Urticarial Vasculitis. Tests may also be done for Anti-Nuclear Antibody (ANA) levels (which are positive in 30 to 50 per cent of patients), and Anti ds-DNA levels may also be positive.
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- 英
- hypocomplementemic urticarial vasculitis HUV
- 同
- 抗C1q血管炎 anti-C1q vasculitis
- 関
- 小型血管炎、血管炎
定義
- CHCC 2012
uptodate
- https://www.uptodate.com/contents/urticarial-vasculitis
- 以下の疾患概念があるとしている。全身症状を伴うのが前者、全身症状に乏しいのが後者としている。
- hypocomplementemic urticarial vasculitis syndrome(HUVS)
- hypocomplementemic urticarial vasculitis(HUV)
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- 同
- ants, stinging
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