double outlet right ventricle

両大血管右室起始症, DORV

WordNet

1. toward or on the right; also used figuratively; "he looked right and left"; "the party has moved right"
2. (frequently plural) the interest possessed by law or custom in some intangible thing; "mineral rights"; "film rights"
3. anything in accord with principles of justice; "he feels he is in the right"; "the rightfulness of his claim" (同)rightfulness
4. a turn toward the side of the body that is on the south when the person is facing east; "take a right at the corner"
5. the hand that is on the right side of the body; "he writes with his right hand but pitches with his left"; "hit him with quick rights to the body" (同)right_hand
6. those who support political or social or economic conservatism; those who believe that things are better left unchanged (同)right wing
7. an abstract idea of that which is due to a person or governmental body by law or tradition or nature; "they are endowed by their Creator with certain unalienable Rights"; "Certain rights can never be granted to the government but must be kept in the hands
8. location near or direction toward the right side; i.e. the side to the south when a person or object faces east; "he stood on the right"
9. make reparations or amends for; "right a wrongs done to the victims of the Holocaust" (同)compensate, redress, correct
10. correct in opinion or judgment; "time proved him right" (同)correct
11. exactly; "he fell flop on his face" (同)flop
12. an interjection expressing agreement (同)right on
13. intended for the right hand; "a right-hand glove" (同)right-hand
14. (of the side of cloth or clothing) facing or intended to face outward; "the right side of the cloth showed the pattern"; "be sure your shirt is right side out"
15. being or located on or directed toward the side of the body to the east when facing north; "my right hand"; "right center field"; "a right-hand turn"; "the right bank of a river is the bank on your right side when you are facing downstream"
16. completely; "she felt right at home"; "he fell right into the trap"
17. having the axis perpendicular to the base; "a right angle"
18. immediately; "she called right after dinner"
19. in conformance with justice or law or morality; "do the right thing and confess"
20. in or into a satisfactory condition; "things are right again now"; "put things right"
21. of or belonging to the political or intellectual right
22. precisely, exactly; "stand right here!"
23. put in or restore to an upright position; "They righted the sailboat that had capsized"
24. regain an upright or proper position; "The capsized boat righted again"
25. used of flowers having more than the usual number of petals in crowded or overlapping arrangements; "double chrysanthemums have many rows of petals and are usually spherical or hemispherical"
26. increase twofold; "The population doubled within 50 years" (同)duplicate
27. a base hit on which the batter stops safely at second base; "he hit a double to deep centerfield" (同)two-base hit, two-bagger, two-baser
28. someone who closely resembles a famous person (especially an actor); "he could be Gingrichs double"; "shes the very image of her mother" (同)image, look-alike
29. a stand-in for movie stars to perform dangerous stunts; "his first job in Hollywood was as a double for Clark Gable" (同)stunt man, stunt woman
30. a quantity that is twice as great as another; "36 is the double of 18"
31. twice as great or many; "ate a double portion"; "the dose is doubled"; "a twofold increase" (同)doubled, twofold, two-fold
32. consisting of or involving two parts or components usually in pairs; "an egg with a double yolk"; "a double (binary) star"; "double doors"; "dual controls for pilot and copilot"; "duple (or double) time consists of two (or a multiple of two) beats to a measure" (同)dual, duple
33. having more than one decidedly dissimilar aspects or qualities; "a double (or dual) role for an actor"; "the office of a clergyman is twofold; public preaching and private influence"- R.W.Emerson; "every episode has its double and treble meaning"-Frederick Harrison (同)dual, twofold, two-fold, treble, threefold, three-fold
34. having two meanings with intent to deceive; "a sly double meaning"; "spoke with forked tongue" (同)forked
35. bridge: make a demand for (a card or suit)
36. do double duty; serve two purposes or have two functions; "She doubles as his wife and secretary"
37. downward and forward; "he was bent double with pain"
38. hit a two-base hit
39. large enough for two; "a double bed"; "a double room"
40. two together; "some people sleep better double"
41. connect or secure to; "They rigged the bomb to the ignition"
42. formation of masts, spars, sails, etc., on a vessel (同)rigging
43. gear (including necessary machinery) for a particular enterprise
44. manipulate in a fraudulent manner; "rig prices" (同)manipulate
45. arrange the outcome of by means of deceit; "rig an election" (同)set_up
46. equip with sails or masts; "rig a ship" (同)set, set_up
47. a chamber of the heart that receives blood from an atrium and pumps it to the arteries (同)heart_ventricle
48. one of four connected cavities in the brain; is continuous with the central canal of the spinal cord and contains cerebrospinal fluid

PrepTutorEJDIC

1. 《名試の前にのみ用いて》『右の』,右側の / 《しばしば『R-』》(政治上)『右派の』,保守的な / 〈U〉《the~》『右』,右側,右方 / 〈C〉『右手』(right hand) / 〈U〉《集合的に》《しばしばthe R-》(政治上の)右派,保守派 / 〈C〉(野球の)右翼(right field) / 『右に』,右側に,右方に
2. 《補語にのみ用いて》(道徳的に)『正しい』,正当な,正義の(just) / (人,人の判断・意見などが)『間偉いのない』,正しい(correct) / (事実に合って)『正しい』,正確な / 適切な,ぴったりの / (精神が)健全な,まともな;(心身が)健康な / 表の,正面の / 〈U〉(道徳的な)『正しさ』,正義;正しい行い / 〈C〉〈U〉(法律上・道徳上の)権利 / 〈U〉〈C〉《複数形で》(政治的・社会的な)人権,権利 / 《話》『まっすぐに』;まともに(directly) / 《話》『きっかり』,ちょうど(exactly) / 正確に,間違いなく(correctly) / (道徳的に)正しく,公正に / すっかり,完全に(completely);ずっと(all the way) / 適切に,ふさわしく;都合よく,うまく / 《おもに米話》すぐに,ただちに / 《特定の称号に付けて》非常に(very) / …‘を'正しい位置(状態)に戻す,立ち直らせる,整とんする / 〈誤りなど〉‘を'正す
3. (数量・強さ・重さ・価値などが)『2倍の』,倍の / 『二重の』,二様の;複の,対の,2人用の / 表裏のある,二心ある / (意味が)二様にとれる,あいまいな / (花が)八重の,重弁の / 『2倍に』,2倍だけ(twice) / 二重に,二様に / 対をなして,二人いっしょに / 〈U〉『2倍』[の数量・価額など] / 〈C〉2倍のもの / 〈C〉よく似た人(物),生き写し / 〈C〉(映画の)代役 / 《複数形》《単数扱い》(テニスなどの)ダブルス / 〈C〉(獲物が追っ手を逃れるときなどの)逆走,急転回 / 〈C〉2塁打 / 〈C〉(ブリッジの点の)倍加 / 〈C〉(競馬・ドッグレースの)重勝式のかけ,複式 / …‘を'『2倍にする』 / …‘を'『二つ折りにする』 / …‘の'2倍の数(量)がある / 〈二役〉‘を'ひとりで演ずる / 〈船が〉〈岬〉‘を'回る / 『2倍になる』 / (…の役を)兼ねる《+『as』+『名』》 / (急に)取って返す,逆戻りする《+『back』》 / 二つ折りになる / (ブリッジで)相手のせり高を倍加する / 2塁打を打つ
4. 〈船〉‘を'艤装(ぎそう)する / (マストなどを)〈船〉‘に'つける《+『名』+『with』+『名』》;(マストに)〈帆〉‘を'つける《+『名』+『to』+『名』》 / …‘に'装備をつける;…‘を'装備する《+『up』+『名,』+『名』+『up』》 / 船の装備(帆装),艤装(ぎそう) / (特定の目的のための)道具,用具 / 《英話》衣服,服装(clothing)
5. 〈他〉〈相場など〉を不正な手段であやつる
6. (脳髄・喉頭などの)室,空洞,(心臓の)心室
7. (水・煙などの)『出口』,はけ口《+『for』+『名』》 / (感情・精力などの)『はけ口』《+『for』+『名』》 / 《米》(電気コードの)差し込口 / (特定の商品の)販売口,販路《+『for』+『名』》

Wikipedia preview

出典(authority):フリー百科事典『ウィキペディア（Wikipedia）』「2016/01/11 09:14:20」(JST)

wiki en

[Wiki en表示]

Double outlet right ventricle
Classification and external resources
Specialty	medical genetics
ICD-10	Q20.1
ICD-9-CM	745.11
OMIM	217095
DiseasesDB	32215
MedlinePlus	007328
eMedicine	ped/2509 ped/2508
MeSH	D004310

Double outlet right ventricle (DORV) is a form of congenital heart disease where both of the great arteries connect (in whole or in part) to the right ventricle (RV). In some cases it is found that this occurs on the left side of the heart rather than the right side.

Anatomy and pathophysiology

DORV occurs in multiple forms, with variability of great artery position and size, as well as of ventricular septal defect (VSD) location. It can occur with or without transposition of the great arteries. The clinical manifestations are similarly variable, depending on how the anatomical defects affect the physiology of the heart, in terms of altering the normal flow of blood from the RV and left ventricle (LV) to the aorta and pulmonary artery. For example:

• in DORV with a subaortic VSD, blood from the LV flows through the VSD to the aorta and blood from the RV flows mainly to the pulmonary artery, yielding physiology similar to ventricular septal defect
• in DORV with a subpulmonic VSD (called Taussig-Bing syndrome), blood from the LV flows through the VSD to the pulmonary artery and blood from the RV flows mainly to the aorta, yielding physiology similar to Transposition of the Great Arteries
  • but if there is pulmonic stenosis in addition, physiology resembles Tetralogy of Fallot
• in other forms of DORV, blood from both ventricles is substantially mixed in the RV, yielding physiology that resembles a large VSD
  • but again, if there is pulmonic stenosis, physiology resembles Tetralogy of Fallot

Treatment

DORV is treated with surgery.

Epidemiology

DORV affects between 1% and 3% of people born with congenital heart defects.

Chromosomal abnormalities were reported in about 40% of reported cases in the medical literature.

References

External links

• Pediatric Heart Surgery
• The Congenital Heart Surgery Video Project
• Ashley: Repair of DORV
• synd/2285 at Who Named It?
• Illustrations at rch.org.au

UpToDate Contents

全文を閲覧するには購読必要です。 To read the full text you will need to subscribe.

• 1. 新生児におけるチアノーゼの心臓の原因 cardiac causes of cyanosis in the newborn
• 2. 房室（AV）管欠損の臨床症状、病態生理、および診断 clinical manifestations pathophysiology and diagnosis of atrioventricular av canal defects
• 3. ファロー四徴症の病態生理、臨床的特徴、および診断 pathophysiology clinical features and diagnosis of tetralogy of fallot
• 4. 先天性および小児冠動脈異常 congenital and pediatric coronary artery abnormalities
• 5. 肺閉鎖症および主要大動脈肺動脈側副動脈（TOF/ PA/ MAPCA）を伴うファロー四徴症 tetralogy of fallot with pulmonary atresia and major aortopulmonary collateral arteries tof pa mapcas

English Journal

• First report of a de novo 18q11.2 microdeletion including GATA6 associated with complex congenital heart disease and renal abnormalities.

• Bui PH, Dorrani N, Wong D, Perens G, Dipple KM, Quintero-Rivera F.SourceDepartment of Pathology, Laboratory Medicine, David Geffen School of Medicine, University of California at Los Angeles, Los Angeles, California.
• American journal of medical genetics. Part A.Am J Med Genet A.2013 Jul;161(7):1773-8. doi: 10.1002/ajmg.a.35974. Epub 2013 May 21.
• Deletions of the long arm of chromosome 18 have been previously reported in many patients. Most cases involve the more distal regions of the long arm (18q21.1->qter). However, proximal interstitial deletions involving 18q11.2 are extremely rare. Here we report on a 14-month-old female with a 4.7�
• PMID 23696469

• How best can we define double outlet right ventricle when describing congenitally malformed hearts?

• Anderson RH.SourceInstitute of Genetic Medicine, Newcastle University, UK.
• Anatomical record (Hoboken, N.J. : 2007).Anat Rec (Hoboken).2013 Jul;296(7):993-4. doi: 10.1002/ar.22716. Epub 2013 May 15.
• PMID 23674328

• Individual risk factors and complexity associated with congenital heart disease in a pediatric medicaid cohort.

• Shuler CO, Tripathi A, Black GB, Park YM, Jerrell JM.SourceFrom the University of South Carolina School of Medicine and the Arnold School of Public Health, Columbia, and the University of Mississippi School of Medicine, Jackson.
• Southern medical journal.South Med J.2013 Jul;106(7):385-90. doi: 10.1097/SMJ.0b013e31829bd0bc.
• OBJECTIVES: To determine the sex and race differences associated with specific congenital heart diseases (CHDs) and the patterns of concomitant conditions associated with eight severe, complex lesions.METHODS: A 15-year Medicaid dataset (1996-2010) from one state was analyzed for 14,496 patients age
• PMID 23820317

Japanese Journal

• 褐色細胞腫を合併したEisenmenger症候群の剖検例

• 三浦 文武,伊藤 悦朗,山本 洋平,嶋田 淳,北川 陽介,敦賀 和志,大谷 勝記,高橋 徹,米坂 勧,加藤 哲子
• 日本小児循環器学会雑誌 35(1), 46-51, 2019
• … <p>Eisenmenger症候群（ES）に褐色細胞腫（pheochromocytoma: PCC）を合併した稀な症例を経験した．症例は女性で，新生児期に両大血管右室起始（double outlet right ventricle: DORV）と診断したが，乳児期よりESの病態を呈した．30歳時にPCCの合併を診断した．外科的切除は周術期のリスクから適応外とされた．32歳時に心不全，腎不全のため死亡した．病理解剖でDORV，高 …
• NAID 130007625124

• 症例 大動脈縮窄とEbstein奇形を合併した両大血管右室起始症に対する二期的修復術の1例

• 西岡 雅彦,渕上 泰,赤繁 徹,長田 信洋
• 胸部外科 = The Japanese journal of thoracic surgery 71(8), 615-621, 2018-08
• NAID 40021648611

• Application of a Fresh Decellularized Pulmonary Allograft for Pulmonary Valve Replacement in Japan

• Ozawa Hideto,Ueno Takayoshi,Taira Masaki,Toda Koichi,Kuratani Toru,Sawa Yoshiki
• 日本循環器學誌, 2018
• … Valves were implanted in 5 adults with pulmonary valve insufficiency after tetralogy of Fallot repair and in 1 infant with a double-outlet right ventricle with pulmonary stenosis. …
• NAID 130006887089

Related Links

• Double outlet right ventricle : MedlinePlus Medical Encyclopedia

Double outlet right ventricle (DORV) is a heart disease that is present from birth (congenital). The aorta connects to the right ventricle (RV, the chamber of the heart that pumps oxygen-poor blood to

• Double Outlet Right Ventricle | Children's Hospital of Philadelphia

Double outlet right ventricle symptoms vary depending on how much oxygenated blood is reaching the body. In most cases, children will have symptoms in the first days or weeks of life, including: Blue or purple tint to lips, skin and ...

• Double Outlet Right Ventricle (DORV) | Boston Children's Hospital

What is double outlet right ventricle? Double outlet right ventricle (DORV) is a rare congenital heart defect, meaning it’s a condition a baby is born with. In DORV, the pulmonary artery and the aorta — the heart’s two major arteries ...

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★リンクテーブル★

リンク元	「両大血管右室起始症」「DORV」
拡張検索	「double-outlet right ventricle」
関連記事	「right」「ventricle」「double」「doubling」「rig」

「両大血管右室起始症」

　　[★]

英

double outlet right ventricle, double-outlet right ventricle, DORV

同

両大血管右室起始

関

タウシク・ビング症候群

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両大血管右室起始 : 約 25,100 件
両大血管右室起始症 : 約 20,000 件

• 大動脈と肺動脈が右心室から出ている先天性心疾患

「DORV」

　　[★] 両大血管右室起始症 double outlet right ventricle

「double-outlet right ventricle」

　　[★] 両大血管右室起始症 DORV

「right」

　　[★]

• n.

• 右、権利

• adj.

• 正しい、右位の、直角の

関

correct、dexter、dextroposition、fair、human right、rectangular、right angle

　 　 　 　 　 　 　 　 　 　 　 　 　 　 　 　 　 　 　 　 　 　 　 　 　 　

「ventricle」

　　[★]

• n.

• 室、心室、脳室

関

cardiac ventricle、cerebral ventricle、cerebroventricle、cerebroventricular、heart ventricle、ventricular、ventriculi、ventriculus

　 　 　

「double」

　　[★]

• adj.

同

outlet right ventricle

　 　 　 　 　 　 　 　 　 　 　 　 　 　 　 　 　

「doubling」

　　[★]

• n.

• 倍加

関

double

　 　

「rig」

　　[★]