polycystic liver disease

多嚢胞肝、多発性肝嚢胞症

WordNet

1. pursue a positive and satisfying existence; "You must accept yourself and others if you really want to live"
2. actually being performed at the time of hearing or viewing; "a live television program"; "brought to you live from Lincoln Center"; "live entertainment involves performers actually in the physical presence of a live audience" (同)unrecorded
3. abounding with life and energy; "the club members are a really live bunch"
4. charged with an explosive; "live ammunition"; "a live bomb"
5. exerting force or containing energy; "live coals"; "tossed a live cigarette out the window"; "got a shock from a live wire"; "live ore is unmined ore"; "a live bomb"; "a live ball is one in play"
6. highly reverberant; "a live concert hall"
7. in current use or ready for use; "live copy is ready to be set in type or already set but not yet proofread"
8. lead a certain kind of life; live in a certain style; "we had to live frugally after the war"
9. not recorded; "the opera was broadcast live"
10. of current relevance; "a live issue"; "still a live option"
11. an impairment of health or a condition of abnormal functioning
12. a person who has a special life style; "a high liver"
13. large and complicated reddish-brown glandular organ located in the upper right portion of the abdominal cavity; secretes bile and functions in metabolism of protein and carbohydrate and fat; synthesizes substances involved in the clotting of the blood; sy
14. liver of an animal used as meat
15. someone who lives in a place; "a liver in cities"
16. caused by or altered by or manifesting disease or pathology; "diseased tonsils"; "a morbid growth"; "pathologic tissue"; "pathological bodily processes" (同)morbid, pathologic, pathological

PrepTutorEJDIC

1. 『生きている』,生命がある / 《副詞[句]を伴って》〈人などが〉『生き続ける』 / 〈物事が〉長く続く,存続する / 《場所を表す副詞[句]を伴って》〈人などが〉『住む』,居住する / 《副詞[句]を伴って》『生活する』,暮らす / 生人を楽しむ,おもしろく桟らす / 《a+形容詞癌lifeを目的語にして》〈…を生活〉‘を'する / 〈思想など〉‘を'実銭する
2. 《名詞の前にのみ用いて》『生きている』 / 『活気のある』 / (問題などが)当面の / 燃えている / (弾丸などが)まだ爆発してない,未発の / まだ動いている(働いている),有効な / 電流が通じている / (放走が)生の,実況の
3. (体の)『病気』,疾患 / (精神・道徳などの)病気,病弊
4. 女性の話術芸人 =diseur
5. (ある態度で)生活する人;居住者
6. 〈C〉『肝臓』 / 〈U〉(食用にする)動物の肝臓,レバー
7. 病気にかかった / 病的な,不健全な(morbid)

Wikipedia preview

出典(authority):フリー百科事典『ウィキペディア（Wikipedia）』「2014/05/21 17:50:17」(JST)

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Polycystic liver disease
Classification and external resources
Micrograph showing a von Meyenburg complex, a bile duct hamartoma associated with polycystic liver disease. Trichrome stain.
ICD-10	Q44.6
OMIM	174050
DiseasesDB	33340

Polycystic liver disease (PLD) usually describes the presence of multiple cysts scattered throughout normal liver tissue, in association with polycystic kidney disease.

Pathophysiology

Associations with PRKCSH and SEC63 have been described. Polycystic Liver Disease comes in two forms as ADPKD (with kidney cysts) and ADPLD (liver cysts alone without any kidney cysts).

See also

• Hepatic cyst (liver cyst)

References

External links

• http://www.pkdcure.org/site/PageServer?pagename=pkdabt_patientsartic6
• http://www.hdcn.com/symp/01pkd/per/per1.htm (requires free account, register at http://www.hdcn.com/reg.htm)
• http://www.pkdiet.com/pld.php
• http://www.polycysticliverdisease.com/html/about_pld.html
• http://polycysticliverdisease.weebly.com/

Template:Individuals with PLD

UpToDate Contents

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• 1. 肝嚢胞性病変の診断およびマネージメント diagnosis and management of cystic lesions of the liver
• 2. 常染色体優性多発性嚢胞腎の腎外症状 extrarenal manifestations of autosomal dominant polycystic kidney disease
• 3. 常染色体優性多発性嚢胞腎の経過および治療 course and treatment of autosomal dominant polycystic kidney disease
• 4. 肝肥大：鑑別診断および評価 hepatomegaly differential diagnosis and evaluation
• 5. 常染色体優性多発性嚢胞腎の診断およびスクリーニング diagnosis of and screening for autosomal dominant polycystic kidney disease

English Journal

• Somatostatin analog therapy for severe polycystic liver disease: results after 2 years.

• Hogan MC, Masyuk TV, Page L, Holmes DR 3rd, Li X, Bergstralh EJ, Irazabal MV, Kim B, King BF, Glockner JF, Larusso NF, Torres VE.Source1Department of Internal Medicine, Division of Nephrology and Hypertension, Mayo Clinic, Rochester, MN, USA.
• Nephrology, dialysis, transplantation : official publication of the European Dialysis and Transplant Association - European Renal Association.Nephrol Dial Transplant.2012 Jul 6. [Epub ahead of print]
• BackgroundWe showed in a randomized double-blinded placebo-controlled clinical trial that octreotide long-acting repeatable depot.® (OctLAR(®)) for 12 months reduces kidney and liver growth in autosomal dominant polycystic kidney patients with severe polycystic liver disease (PLD) and liver growth
• PMID 22773240

• Boy with autosomal recessive polycystic kidney and autosomal dominant polycystic liver disease.

• Zingg-Schenk A, Caduff J, Azzarello-Burri S, Bergmann C, Drenth JP, Neuhaus TJ.SourceChildren's Hospital Lucerne, 6000, Lucerne, Switzerland.
• Pediatric nephrology (Berlin, Germany).Pediatr Nephrol.2012 Jul;27(7):1197-200. Epub 2012 Mar 14.
• BACKGROUND: Autosomal recessive polycystic kidney disease (ARPKD) shows a great phenotypic variability between patients, ranging from perinatal demise to mildly affected adults. Autosomal dominant polycystic liver disease (PCLD) does not manifest in childhood. CASE-DIAGNOSIS/TREATMENT: A boy was rep
• PMID 22415584

Japanese Journal

• Cholangiopathy: Genetics, Mechanism, and Pathology

• Nakanuma Yasuni,Demetris Anthony J.,Ueno Yoshiyuki,Quaglia Alberto
• International Journal of Hepatology 2012, 950713, 2012
• … Several animal models have been developed for autoimmune and genetic cholangiopathy such as primary biliary cirrhosis and polycystic disease of the liver and biliary tract. …
• NAID 120004186275

• 本邦における多発肝嚢胞症のアンケート調査

• 小川 光一,福永 潔,竹内 朋代,川岸 直樹,工藤 正俊,大河内 信弘
• 肝臓 52(11), 709-715, 2011
• 多発肝嚢胞症は肝内に多数の嚢胞を形成し，嚢胞数の増加，嚢胞の巨大化により肝腫大をきたす遺伝性疾患である．比較的まれな疾患であり治療法のコンセンサスは得られていない．今回我々は本邦における多発肝嚢胞症患者の実態を把握するため全国490施設に対しアンケート調査を行った．症例数は422例であり，223例（53％）に治療が行われていた．治療適応となった症状は腹部膨満が73％と最も多かった．実施された治療法 …
• NAID 130001413814

Related Links

• Polycystic Liver Disease: Symptoms, Causes, Treatments

Polycystic liver disease (PLD or PCLD) is a rare condition that causes cysts -- fluid-filled sacs -- to grow throughout the liver. A normal liver has a smooth, uniform appearance. A polycystic liver can look like a cluster of very large ...

• Polycystic Liver Disease (PLD) - Liver Doctor

Polycystic liver disease (PLD) is rare and is considered to be an inherited condition with an autosomal dominant genetic trait. ... Liver disease is serious and requires treatment and regular monitoring by a liver specialist. A liver ...

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★リンクテーブル★

リンク元	「多嚢胞肝」「多発性肝嚢胞症」
関連記事	「disease」「live」「liver disease」「polycystic」「liver」

「多嚢胞肝」

　　[★]

英

polycystic liver disease

関

多発性肝嚢胞症

「多発性肝嚢胞症」

　　[★]

英

polycystic liver disease

関

多嚢胞肝

「disease」

　　[★]

• n.

疾患：illnessより厳密な概念。「ある臓器に明確な障害が確認され、それによって症状が出ているとはっきり説明できる場合」 (PSY.9)

特定の原因、病態生理、症状、経過、予後、病理組織所見が全てそろった場合 (PSY.9)

• something that is very wrong with people's attitudes, way of life or with society.

関

ail、ailment、disease entity、disorder、ill、illness、malady、sick、sickness

• 注意

disease ≠ illness ≠ disorder

　 　 　

「live」

　　[★]

[liv]

• vt.
• vi.

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[laiv]

• adj.

同

LAIV

　 　 　 　 　 　 　 　 　 　 　 　

「liver disease」

　　[★] 肝疾患、肝臓病、肝臓疾患

「polycystic」

　　[★]

• 多嚢胞性の、多嚢胞の

「liver」

　　[★] 肝臓