PBG synthase

アミノレブリン酸脱水酵素、ポルフォビリノゲンシンターゼ

WordNet

1. the 16th letter of the Roman alphabet (同)p

PrepTutorEJDIC

1. parking
2. phosphorusの化学記号

UpToDate Contents

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• 1. ALA脱水酵素欠損性ポルフィリン症 ala dehydratase porphyria
• 2. ポルフィリン症：概要 porphyrias an overview
• 3. 遺伝性疾患に伴う神経障害 neuropathies associated with hereditary disorders
• 4. 急性間欠性ポルフィリン症：発症機序、臨床的特徴、診断 acute intermittent porphyria pathogenesis clinical features and diagnosis
• 5. 遺伝コプロポルフィリン症 hereditary coproporphyria

English Journal

• Computational insights into the mechanism of porphobilinogen synthase.

• Erdtman E, Bushnell EA, Gauld JW, Eriksson LA.SourceSchool of Science and Technology, Örebro Life Science Center, Örebro University, Örebro, Sweden.
• The journal of physical chemistry. B.J Phys Chem B.2010 Dec 23;114(50):16860-70. Epub 2010 Nov 23.
• Porphobilinogen synthase (PBGS) is a key enzyme in heme biosynthesis that catalyzes the formation of porphobilinogen (PBG) from two 5-aminolevulinic acid (5-ALA) molecules via formation of intersubstrate C-N and C-C bonds. The active site consists of several invariant residues, including two lysyl r
• PMID 21090799

• Marked geographic aggregation of acute intermittent porphyria families carrying mutation Q180X in Venezuelan populations, with description of further mutations.

• Paradisi I, Arias S.SourceLaboratorio de Genética Humana, Centro de Medicina Experimental, Instituto Venezolano de Investigaciones Científicas, IVIC, Apartado 20632, Caracas, 1020-A, Venezuela, iparadis@ivic.gob.ve.
• Journal of inherited metabolic disease.J Inherit Metab Dis.2010 Oct 27. [Epub ahead of print]
• Acute intermittent porphyria (AIP) caused by mutations in the hydroxymethylbilane synthase gene (HMBS), has been reported in almost all human populations, with varying frequencies. A founder effect for a few specific mutations in geographic regions where prevalence is high (Sweden, The Netherlands,
• PMID 20978940

Japanese Journal

• Effect of Culture Conditions on Production of 5-Aminolevulinic Acid by Recombinant Escherichia coli

• Bioscience, biotechnology, and biochemistry 69(3), 470-476, 2005-03-23
• NAID 130000030383

• Enzymatic Activities for the Synthesis of Chlorophyll in Pigment-Deficient Variegated Leaves of Euonymus japonicus :

• Plant and cell physiology 37(4), 481-487, 1996
• NAID 110003720845

• 緑青 (塩基性炭酸銅) による造血系諸酵素活性の変動:緑青 (塩基性炭酸銅) の毒性に関する研究 (第3報)

• 食品衛生学雑誌 26(6), 624-629_1, 1985
• NAID 130003692624

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★リンクテーブル★

関連記事	「synthase」「P」「PBG」「PB」

「synthase」

　　[★]

• n.

• (脱離酵素リアーゼの逆反応である合成方向の反応を指す) シンターゼ, 合成酵素, 付加酵素

関

lyase、synthetase、transferase

「P」

　　[★]

• プロリン proline
• P波 P wave
• リン phosphorus

　 　 　

「PBG」

　　[★] ポルフォビリノゲン porphobilinogen

「PB」

　　[★] フェノバルビタール phenobarbital