WordNet

free of extraneous elements of any kind; "pure air and water"; "pure gold"; "pure primary colors"; "the violins pure and lovely song"; "pure tones"; "pure oxygen"
in a state of sexual virginity; "pure and vestal modesty"; "a spinster or virgin lady"; "men have decreed that their women must be pure and virginal" (同)vestal, virgin, virginal, virtuous
(used of persons or behaviors) having no faults; sinless; "I felt pure and sweet as a new baby"- Sylvia Plath; "pure as the driven snow"
concerned with theory and data rather than practice; opposed to applied; "pure science"
free from discordant qualities
a word is a string of bits stored in computer memory; "large computers use words up to 64 bits long"
a brief statement; "he didnt say a word about it"
a unit of language that native speakers can identify; "words are the blocks from which sentences are made"; "he hardly said ten words all morning"
a verbal command for action; "when I give the word, charge!"
partial or complete loss of hearing (同)hearing_loss
the manner in which something is expressed in words; "use concise military verbiage"- G.S.Patton (同)diction, phrasing, phraseology, choice of words, verbiage
language that is spoken or written; "he has a gift for words"; "she put her thoughts into words"
the words that are spoken; "I listened to his words very closely"

PrepTutorEJDIC

(金など)『混じりけのない』,純粋の / (水など)『汚れていない』,きれいな / (道徳的に)汚れていない,清らかな / (血統が)純粋の,純血の,きっすいの / 《名詞の前にのみ用いて》《話》全くの / 《名詞の前にのみ用いて》(応用的に対して)理論的な,純粋の
〈C〉『語』,単語 / 《しばしば複数形で》(表現された)『言葉』;(自分の考えに基く)言葉 / 〈C〉《しばしば複数形で》『短い会話』,ひと言 / 《単数形で;one's word》『約束』,保証 / 〈U〉《冠詞をつけずに》『知らせ』,伝言 / 《the word》合い言葉 / 〈C〉《the word, one's》命令,指図 / 《複数形で》『口論』,論争 / 《the Word》聖書,(聖書に書かれた)神の言葉 / …‘を'言葉に表す
言い回し,言葉づかい

Wikipedia preview

出典(authority):フリー百科事典『ウィキペディア（Wikipedia）』「2013/04/03 21:25:40」(JST)

wiki en

Main article: Agnosia

Auditory verbal agnosia, also known as Pure Word Deafness, is caused by bilateral damage to the posterior superior temporal lobes or disruption of connections between these areas. It exhibits itself as inability to comprehend the meaning of speech, but (in most cases) still being able to hear, speak, read, and write. Individuals that exhibit pure word deafness are usually also able to comprehend non-verbal sounds.^[1] Sometimes this agnosia is preceded by complete cortical deafness of varying duration, however this is not always the case. Researchers have documented that in most patients exhibiting auditory verbal agnosia the differentiation of consonants suffers more than that of vowels, but as with most neurological disorders there is variation among patients.^[2]

Presentation

Auditory verbal agnosia is a rarely diagnosed disorder in its pure form of being incapable of phonemic discrimination.^[1] Often individuals diagnosed with auditory verbal agnosia are also incapable of discriminating between non-verbal sounds as well as speech. The underlying problem seems to be temporal in that understanding speech requires the discrimination between specific sounds which are closely spaced in time.^[3] Note that this is not unique to speech; studies using non-speech sounds closely spaced in time (dog bark, phone ring, lightning, etc.) have shown that those with auditory verbal agnosia are unable to discriminate between those sounds in the majority of cases, though a few putative examples of speech-specific impairment have been documented in the literature.^[4]^[5] Historically, those with pure word deafness are not deaf - they can (in the absence of other impairments) hear sounds, including speech (so it has nothing to do with words). As such, "pure word deafness" is something of a misnomer. "Pure word" is intended to mean that only words are affected (not accurate for many cases); "deafness" is intended to specify that these patients have an inability to hear (not accurate).

Auditory verbal agnosia can present as the result of acute damage or chronic, progressive degeneration over time. Cases have been documented that result from severe acute head trauma resulting in bilateral temporal lobe damage.^[6] In contrast, auditory verbal agnosia has also been documented to present progressively over several years. In one such case, the patient exhibited progressive word deafness over a 9 year period but did not exhibit any other cognitive of mental deterioration. This patient was found, using MRIs, to have cortical atrophy in the left superior temporal lobe region.^[7]

Auditory verbal agnosia is unique among other language perception disorders in that it has a high degree of specificity. This specificity suggests that there is a separation between speech perception, nonspeech auditory processing, and central language processing.^[8]

In a study examining a female patient presenting with bilateral temporoparietal destruction was diagnosed with auditory verbal agnosia. It was found that she was unable to comprehend auditory sounds even when the rate of speech was reduced, however temporal resolution was improved when the length of a nonverbal sound was increased. This same patient was also unable to perceive and reproduce rhythm on a rate-dependent scale.^[9]

In extremely rare cases, auditory verbal agnosia has been known to present as a symptom of neurodegenerative disease, such as Alzheimer’s disease.^[10] In such cases auditory verbal agnosia is a symptom that is typically followed by more severe neurological symptoms typical of Alzheimer’s disease.

Causes

Auditory verbal agnosia is often associated with lesions to the left posterior superior temporal lobe, but no such unilateral case has yet been documented without damage to the white matter tract connecting superior temporal lobes bilaterally or bilateral damage to the superior temporal lobe. In cases where unilateral damage to the left superior temporal lobe has been documented, patients exhibited problems processing both speech and non-speech sounds (in other words, not typical of auditory verbal agnosia).^[3] These facts, in combination with the existence of cases of damage to these white matter tracts without detectable cortical damage, in combination with cases of pure word deafness resulting enlargement of the III ventricle alone^[4] suggest that the disorder results from damage to the left-right superior temporal circuit rather than the superior temporal area on one hemisphere or another.

References

^ ^a ^b Wolberg SC, Temlett JA, Fritz VU (December 1990). "Pure word deafness". S. Afr. Med. J. 78 (11): 668–70. PMID 2251612.
^ Ackermann H, Mathiak K (November 1999). "[Symptomatology, Neuroanatomlcal Correlates and Pathomechanisms of Central Hearing Disorders (Pure Word Deafness, Verbal/Nonverbal Auditory Agnosia, Cortical Deafness) A Review]". Fortschr Neurol Psychiatr 67 (11): 509–23. doi:10.1055/s-2007-995228. PMID 10598334.
^ ^a ^b Stefanatos GA, Gershkoff A, Madigan S (2005). "On pure word deafness, temporal processing, and the left hemisphere". Journal of the International Neuropsychological Society : JINS 11 (4): 456–70; discussion 455. PMID 16209426.
^ ^a ^b Riley, J. and Cogan, G. (2007) A Two Mechanism Model of Pure Word Deafness. Maryland Working Papers in Linguistics: '16. http://www.ling.umd.edu/publications/volume16/riley.pdf
^ Saffran EM, Marin OS, Yeni-Komshian GH (April 1976). "An analysis of speech perception in word deafness". Brain Lang 3 (2): 209–28. doi:10.1016/0093-934X(76)90018-3. PMID 938928.
^ Wirkowski E, Echausse N, Overby C, Ortiz O, Radler L (January 2006). "I can hear you yet cannot comprehend: a case of pure word deafness". J Emerg Med 30 (1): 53–5. doi:10.1016/j.jemermed.2005.03.016. PMID 16434336.
^ Otsuki M, Soma Y, Sato M, Homma A, Tsuji S (1998). "Slowly progressive pure word deafness". Eur. Neurol. 39 (3): 135–40. doi:10.1159/000007923. PMID 9605389.
^ Poeppel, David (2001). "Pure word deafness and the bilateral processing of the speech code". Cognitive Science 25 (5): 679–693. doi:10.1207/s15516709cog2505_3. ISSN 03640213.
^ Tanaka Y, Yamadori A, Mori E (April 1987). "Pure word deafness following bilateral lesions. A psychophysical analysis". Brain. 110 ( Pt 2): 381–403. doi:10.1093/brain/110.2.381. PMID 3567528.
^ Kim SH, Suh MK, Seo SW, Chin J, Han SH, Na DL (December 2011). "Pure word deafness in a patient with early-onset Alzheimer's disease: an unusual presentation". J Clin Neurol 7 (4): 227–30. doi:10.3988/jcn.2011.7.4.227. PMC 3259498. PMID 22259620.

UpToDate Contents

全文を閲覧するには購読必要です。 To read the full text you will need to subscribe.

1. 失語症患者へのアプローチ approach to the patient with aphasia

English Journal

Health-related quality of life and mental distress in patients with partial deafness: preliminary findings.

Cieśla K1, Lewandowska M2,3, Skarżyński H2.
European archives of oto-rhino-laryngology : official journal of the European Federation of Oto-Rhino-Laryngological Societies (EUFOS) : affiliated with the German Society for Oto-Rhino-Laryngology - Head and Neck Surgery.Eur Arch Otorhinolaryngol.2016 Mar;273(3):767-76. doi: 10.1007/s00405-015-3713-7. Epub 2015 Aug 5.
The aim of the study was to evaluate mental distress and health-related quality of life in patients with bilateral partial deafness (high-frequency sensorineural hearing loss) before cochlear implantation, with respect to their audiological performance and time of onset of the hearing impairment. Th
PMID 26242252

Delayed restoration of maximum speech discrimination scores in patients with idiopathic sudden sensorineural hearing loss.

Noguchi Y1, Takahashi M2, Ito T2, Fujikawa T2, Kawashima Y2, Kitamura K2.
Auris, nasus, larynx.Auris Nasus Larynx.2015 Dec 28. pii: S0385-8146(15)30003-1. doi: 10.1016/j.anl.2015.12.003. [Epub ahead of print]
OBJECTIVE: To assess possible delayed recovery of the maximum speech discrimination score (SDS) when the audiometric threshold ceases to change.METHODS: We retrospectively examined 20 patients with idiopathic sudden sensorineural hearing loss (ISSNHL) (gender: 9 males and 11 females, age: 24-71 year
PMID 26739945

Reversible pure word deafness due to inferior colliculi compression by a pineal germinoma in a young adult.

Joswig H1, Schönenberger U2, Brügge D3, Richter H4, Surbeck W5.
Clinical neurology and neurosurgery.Clin Neurol Neurosurg.2015 Dec;139:62-5. doi: 10.1016/j.clineuro.2015.08.034. Epub 2015 Sep 9.
We report a clinical case of a 19-year-old male patient who developed pure word deafness due to the local compressive effect of a pineal germinoma on the inferior colliculi of the quadrigeminal plate. After percutaneous radiation therapy the size of the tumor decreased significantly, while audiometr
PMID 26372938

Japanese Journal

てんかん発作中による純粋語聾の1例

四條友望,菅野重範,澁谷聡,及川祟紀,大沼歩,望月廣
臨床神経学 55(7), 506-506, 2015
NAID 130005089316

てんかん発作による純粋語聾

前田憲吾
臨床神経学 55(7), 505-505, 2015
NAID 130005089310

てんかん発作中による純粋語聾の1例

四條友望,菅野重範,澁谷聡,及川祟紀,大沼歩,望月廣
臨床神経学 advpub(0), 2015
NAID 130005069853

Related Pictures

PPT - Speech perception PowerPoint Presentation - ID:73903 PPT - שפה ומוח: שפה דבורה והפרעותיה PowerPoint Presentation PPT - PSY 335 Memory and Amnesia PowerPoint Presentation - ID:3619876 PPT - Aphasia PowerPoint Presentation, free download - ID:421013 PPT - Chapter 19: Higher mental functions PowerPoint Presentation - ID:389271 (PDF) Pure Word Deafness in a Patient with Early-Onset Alzheimer's Disease: An Unusual Coping With Pure Word Deafness

★リンクテーブル★

リンク元	「純粋語聾」
関連記事	「deafness」「pure」「word」

「純粋語聾」

　　[★]

英: pure word deafness
同: 純粋感覚性失語 pure sensory aphasia、皮質下性感覚性失語 subcortical sensory aphasia
関: 感覚性失語、語聾、皮質下性失語、失語症

「deafness」

　　[★]

n.

聴覚消失
難聴。(人の話を故意に)聞こうとしないこと。耳が聞こえないこと、ろう、聾
1. the quality of being unable to hear, either completely or partly. 2.an unwillingness to listen, or a lack of understanding about something(https://dictionary.cambridge.org/dictionary/english/deafness)

「pure」

　　[★]

adj.

純粋な

関: genuinely、purely、sincere

「word」

　　[★]

n.

語

[Wolberg-1] Wolberg SC, Temlett JA, Fritz VU (December 1990). "Pure word deafness". S. Afr. Med. J. 78 (11): 668–70. PMID 2251612.

[2] Ackermann H, Mathiak K (November 1999). "[Symptomatology, Neuroanatomlcal Correlates and Pathomechanisms of Central Hearing Disorders (Pure Word Deafness, Verbal/Nonverbal Auditory Agnosia, Cortical Deafness) A Review]". Fortschr Neurol Psychiatr 67 (11): 509–23. doi:10.1055/s-2007-995228. PMID 10598334.

[Stefanatos-3] Stefanatos GA, Gershkoff A, Madigan S (2005). "On pure word deafness, temporal processing, and the left hemisphere". Journal of the International Neuropsychological Society : JINS 11 (4): 456–70; discussion 455. PMID 16209426.

[RileyCogan-4] Riley, J. and Cogan, G. (2007) A Two Mechanism Model of Pure Word Deafness. Maryland Working Papers in Linguistics: '16. http://www.ling.umd.edu/publications/volume16/riley.pdf

[5] Saffran EM, Marin OS, Yeni-Komshian GH (April 1976). "An analysis of speech perception in word deafness". Brain Lang 3 (2): 209–28. doi:10.1016/0093-934X(76)90018-3. PMID 938928.

[6] Wirkowski E, Echausse N, Overby C, Ortiz O, Radler L (January 2006). "I can hear you yet cannot comprehend: a case of pure word deafness". J Emerg Med 30 (1): 53–5. doi:10.1016/j.jemermed.2005.03.016. PMID 16434336.

[7] Otsuki M, Soma Y, Sato M, Homma A, Tsuji S (1998). "Slowly progressive pure word deafness". Eur. Neurol. 39 (3): 135–40. doi:10.1159/000007923. PMID 9605389.

[Poeppel2001-8] Poeppel, David (2001). "Pure word deafness and the bilateral processing of the speech code". Cognitive Science 25 (5): 679–693. doi:10.1207/s15516709cog2505_3. ISSN 03640213.

[9] Tanaka Y, Yamadori A, Mori E (April 1987). "Pure word deafness following bilateral lesions. A psychophysical analysis". Brain. 110 ( Pt 2): 381–403. doi:10.1093/brain/110.2.381. PMID 3567528.

[10] Kim SH, Suh MK, Seo SW, Chin J, Han SH, Na DL (December 2011). "Pure word deafness in a patient with early-onset Alzheimer's disease: an unusual presentation". J Clin Neurol 7 (4): 227–30. doi:10.3988/jcn.2011.7.4.227. PMC 3259498. PMID 22259620.

匿名

検索

案内

案内

pure word deafness