スタージ・ウェーバー症候群
WordNet
- the main sensory nerve of the face and motor nerve for the muscles of mastication (同)trigeminal_nerve, trigeminus, nervus_trigeminus, fifth_cranial_nerve
UpToDate Contents
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English Journal
- Sturge Weber Syndrome--unusual presentation. .
- Neki NS.
- Journal of Ayub Medical College, Abbottabad : JAMC.J Ayub Med Coll Abbottabad.2014 Jan-Mar;26(1):106-7.
- Sturge Weber Syndrome or encephalo-trigeminal angiomatosis is non-hereditary, congenital and rare disorder of unknown aetiology. It is characterised by vascular malformation with capillary venous angiomas involving face, eye and leptomeninges resulting in neurological and orbital manifestations. A c
- PMID 25358234
- Anesthesia for encephalo-trigeminal angiomatosis (Sturge-Weber syndrome).
- Delvi MB1, Takrouri MS.
- Middle East journal of anaesthesiology.Middle East J Anaesthesiol.2006 Feb;18(4):785-90.
- A case report of rare congenital disease of encephalo-trigeminal angiomatosis (Sturge-Weber Syndrome) (SWS), is presented to alert the anesthesiologist of its potential risk. The case was anesthetized for emergency orthopedic surgery. Anesthesia management is directed towards observing the clinical
- PMID 16749573
- Dorothy A1, Kamboj M, Reddy BS, Mahajan S, Boaz K.
- Indian journal of dental research : official publication of Indian Society for Dental Research.Indian J Dent Res.2004 Oct-Dec;15(4):152-4.
- A variant of hemangioma and an uncommon congenital condition, the Sturge Weber syndrome (SWS), also called encephalo trigeminal angiomatosis, is a neurocutaneous disorder with angiomas involving the skin of the face (cutaneous angioma) and pia arachnoid (leptomeningeal angioma). It occurs typically
- PMID 16035646
Related Links
- Author: Dr. Shamimul Hasan, Dr. Sameer Ahmed Abstract: Sturge –weber syndrome, also known as encephalo trigeminal hemangiomatosis, is an uncommon congenital condition. It is characterized by hemangiomatous lesions of ...
- [Encephalo-trigeminal angiomatosis]. on ResearchGate, the professional network for scientists. ... [Show abstract] [Hide abstract] ABSTRACT: Die Vernderungen an Auge und Hirn bei Phakomatosen lassen nicht nur im ...
★リンクテーブル★
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- 英
- Sturge-Weber syndrome
- 同
- (国試)Sturge-Weber症候群、パルケス・ウェーバー・ディミトリ病 Parkes-Weber-Dimitri disease、nevoid amentia、三叉神経脳血管腫症 trigeminal encephaloangiomatosis encephalo-trigeminal angiomatosis
- 関
- (使われない傾向にある)母斑症 phacomatosis、神経皮膚症候群
概念
- 母斑症の一つ
- 顔面の血管腫、神経症状、眼症状
- 顔面片側性の単純血管腫(三叉神経第1枝に沿う(CN V1))、眼の脈絡膜血管腫、脳軟膜の血管腫(NDE.349)
遺伝形式
症状
- 皮膚症状:顔面片側性の単純血管腫(三叉神経第1枝に沿う(CN V1))
- 中枢神経症状:顔面血管腫が存在する側の特に後頭葉に脳軟膜の血管腫が発生 (NDE.349)。乳幼児期からの血管発作。大脳半球萎縮、石灰化、知能障害
- 眼症状:緑内障(牛眼)
治療
- 皮膚症状:レーザー療法
- 中枢神経症状:(痙攣発作)薬物療法、脳切除
- 眼症状:眼圧の調整
参考
http://www.nature.com/eye/journal/v19/n3/fig_tab/6701474f1.html
[★]
- 英
- regional phacomatosis
[★]
- 関
- brain, cerebral, cerebro, encephalic, encephalon
[★]
- 関
- nervi trigemini、trigeminal nerve
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血管腫症
- 同
- epithelioid