Angiomatosis is a non-neoplastic condition[1] characterised by nests of proliferating capillaries arranged in a lobular pattern, displacing adjacent muscle and fat.[2] It consists of many angiomas.[3]
These tend to be cavernous hemangiomas, which are sharply defined, sponge-like tumors composed of large, dilated, cavernous vascular spaces.
Contents
1Presentation
1.1Associated
2Histology
3Diagnosis
4Prognosis
5See also
6References
7External links
Presentation
Associated
They often appear in:
Von Hippel-Lindau disease: It can be associated with Von Hippel-Lindau Disease and is a rare genetic multi system disorder characterized by the abnormal growth of tumours in the body. Symptoms may include headaches, problems with balance and walking, dizziness, weakness of the limbs, vision problems and high blood pressure.[4]
Bacillary angiomatosis
Klippel-Trenaunay-Weber syndrome
Sturge-Weber syndrome
Histology
It is a vascular malformation wherein blood vessels proliferate along with accompanying mature fat and fibrous tissue, lymphatics and sometimes nerves.[2] They may involve skin, subcutaneous tissue, skeletal muscle and occasionally bone.[2]
Diagnosis
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Prognosis
Prognosis depends on the size and location of the tumour, untreated angiomatosis may lead to blindness and/ or permanent brain damage. Death may occur, with complications in the kidney or brain.[4]
See also
Angioma
Hemangioma
List of cutaneous conditions
References
^Angiomatosis at the US National Library of Medicine Medical Subject Headings (MeSH)
^ abcHowat, AJ; Campbell, PE (October 1987). "Angiomatosis: a vascular malformation of infancy and childhood. Report of 17 cases". Pathology. 19 (4): 377–82. doi:10.3109/00313028709103887. PMID 3444663.
^"angiomatosis" at Dorland's Medical Dictionary
^ ab"Von Hippel-Lindau Disease (VHL) Information Page". www.ninds.nih.gov. National Institute of Neurological Disorders and Stroke.
Clinical features of Sturge-Weber syndrome without facial nevus: Five novel cases.
Siri L, Giordano L, Accorsi P, Cossu M, Pinelli L, Tassi L, Striano P.SourceNeuropsichiatria Infantile Pediatria Ospedale San Paolo, Savona, Italy.
European journal of paediatric neurology : EJPN : official journal of the European Paediatric Neurology Society.Eur J Paediatr Neurol.2012 Jul 17. [Epub ahead of print]
Classic Sturge-Weber syndrome (SWS) is characterized by presence of flammeus nevus involving the first sensory branch of trigeminal nerve, ipsilateral leptomeningeal angiomatosis, and choroidal angioma. Sporadic cases of SWS without facial nevus (SWS type III) have been rarely reported. Here we repo
Ramdial PK, Sing Y, Ramburan A, Dlova NC, Bagratee JS, Calonje E.SourceDepartments of Anatomical Pathology (P.K.R., Y.S., A.R.) Dermatology (N.C.D.) Obstetrics and Gynaecology (J.S.B.), Nelson R Mandela School of Medicine, University of KwaZulu-Natal National Health Laboratory Service (P.K.R., Y.S., A.R.), Durban, KwaZulu-Natal, South Africa Department of Dermatopathology (E.C.), St John's Institute of Dermatology, St Thomas's Hospital, London, UK.
International journal of gynecological pathology : official journal of the International Society of Gynecological Pathologists.Int J Gynecol Pathol.2012 Jul;31(4):390-4.
Bacillary angiomatosis (BA) is an increasingly reported infection, mainly in patients with acquired immunodeficiency syndrome. Different epidemiological risk factors are associated with the transmission of the causative agents, Bartonella henselae and B. quintana. Vulval BA is described rarely. Two
Angiomatosis is a non-neoplastic condition presenting with little knots of capillaries in various organs. It consists of many angiomas. It is also known as Von Hippel-Lindau Disease and is a rare genetic multi system disorder characterized by ...