Banti syndrome

バンチ症候群

WordNet

1. a pattern of symptoms indicative of some disease
2. a complex of concurrent things; "every word has a syndrome of meanings"
3. Canadian physiologist who discovered insulin with C. H. Best and who used it to treat diabetes(1891-1941) (同)F. G. Banting, Sir Frederick Grant Banting

PrepTutorEJDIC

1. (疾患の徴候となる一群の)症徴候,症候群 / (事件・社会的状態などのパターンを示す)徴候形態

Wikipedia preview

出典(authority):フリー百科事典『ウィキペディア（Wikipedia）』「2016/07/04 22:12:20」(JST)

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[Wiki en表示]

Banti's syndrome (also known as Banti's disease) is a chronic congestive enlargement of the spleen resulting in premature destruction of the red blood cells by the spleen. It is named for Guido Banti.

Pathogenesis

Banti's disease in a child aged seven years

The basic pathology is some kind of obstructive pathology in the portal, hepatic or splenic vein that causes obstruction of venous blood flow from the spleen towards the heart. The cause of such obstruction may be abnormalities present at birth (congenital) of certain veins, blood clots, or various underlying disorders causing inflammation and obstruction of veins (vascular obstruction) of the liver.

Clinical presentation

Enlargement of spleen, ascites, jaundice, and the result of destruction of various blood cells by spleen – anemia, leukopenia, thrombocytopenia, gastrointestinal bleeding – may constitute the presenting symptoms.

External links

• WebMD article
• Free Dictionary article
• 1937 article in The Journal of Clinical Investigation

Organization

Organizations related to Banti's syndrome are:

• American Liver Foundation
• NIH/National Digestive Diseases Information Clearinghouse

Notes

English Journal

• Complex chromosomal aberrations in a fetus originating from oocytes with smooth endoplasmic reticulum (SER) aggregates.

• Sfontouris IA, Lainas GT, Lainas TG, Faros E, Banti M, Kardara K, Anagnostopoulou K, Kontos H, Petsas GK, Kolibianakis EM.
• Systems biology in reproductive medicine. 2018 Aug;64(4)283-290.
• The presence of smooth endoplasmic reticulum aggregates (SERa) in the ooplasm is considered as the most severe oocyte dysmorphism due to its serious and potentially lethal outcomes in offspring. In the present case report, a couple underwent their first intracytoplasmic sperm injection (ICSI) cycle
• PMID 29718716

• [Role of splenectomy in the treatment of non-cirrhotic portal hypertension: about 3 cases].

• Belhamidi MS, Hammi SE, Bouzroud M, Benmoussa M, Ali AA, Bounaim A.
• The Pan African medical journal. 2017 ;28()84.
• Non-cirrhotic portal hypertension was first described by Guido BANTI in 1898 as a condition characterized by the association of portal hypertension with splenomegaly, anemia and healthy liver. The diagnosis was based on abdominal ultrasound, splenoportography and liver biopsy. Our study aimed to eva
• PMID 29255554

• Women's Issues in Antiphospholipid Syndrome.

• Papadakis E, Banti A, Kioumi A.
• The Israel Medical Association journal : IMAJ. 2016 Sep;18(9)524-529.
• Antiphospholipid syndrome (APS) is an autoimmune systemic disease characterized by vascular thrombosis (arterial or venous) and/or pregnancy complications associated with the occurrence of autoantibodies, specifically lupus anticoagulant, anticardiolipin antibodies, and/or anti-β2 glycoprotein-I an
• PMID 28471597

Japanese Journal

• Abnormally Shaped-Polyclonal Hypergammaglobulinemia in Pulmonary Fibrosis, Splenomegaly, Sjogren Syndrome and Reactive Lymphadenopathy

• Isobe Takashi,Shiozawa Shunichi,Yamada Hazime,Maeda Sakan,Chihara Kazuo
• Bulletin of health sciences Kobe 14, 123-131, 1998-12-26
• … Clinical diagnosis varied along the course such as Banti syndrome, pulmonary fibrosis, Sjogren syndrome and malignant lymphoma. …
• NAID 110004599665

• The efficacy of indomethacin in the treatment of uremic pericarditis

• MORIMOTO Satoshi,KATOH Shuji,INOUE Keiji,TERASHIMA Satoshi,TATSUKAWA Hirotaka,IDA Kazunori
• The Japanese journal of nephrology = / 日本腎臓学会 [編集] 37(2), 140-144, 1995-02-25
• NAID 10004915477

Related Links

• バンチ症候群 - 自治医科大学

バンチ症候群 (Banti syndrome) グリッソン鞘には3つ組と呼ばれる動脈、静脈（門脈）、胆管がある。バンチでは異所性に拡張した静脈が認められる。 （83回）

• Banti syndrome | definition of Banti syndrome by Medical ...

Looking for online definition of Banti syndrome in the Medical Dictionary? Banti syndrome explanation free. What is Banti syndrome? Meaning of Banti syndrome medical term. What does Banti syndrome mean? Banti syndrome ...

Related Pictures

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★リンクテーブル★

リンク元	「特発性門脈圧亢進症」
関連記事	「syndrome」

「特発性門脈圧亢進症」

　　[★]

英

idiopathic portal hypertension, IPH

同

バンチ症候群 Banti's syndrome Banti syndrome

関

門脈圧亢進症

まとめ

• 原因不明の肝内末梢門脈枝の閉塞をきたす肝疾患であり、肝内性、前類洞性の門脈圧亢進症を呈する。中年女性に多い。腹腔鏡では肝臓の外観は表面平滑、もしくは波打ち状である。肝静脈造影では肝静脈枝相互間吻合し、しだれ柳状所見がみとめられる。門脈圧は亢進しているが、閉塞感静脈圧は正常化軽度上昇にとどまる。門脈造影あるいはMRAで門脈末梢枝の走行異常・分岐異常が認められ、病理所見では、軽度から中等度の線維化が見られるが、実質はほぼ正常であり、特に肝内門脈末梢枝のつぶれ像が特徴的である。肝機能は正常であり、肝硬変、慢性肝炎の所見は認められない。予後は比較的良好で、10年生存率は70-80%程度である。

(YN.B-59 SSUR.644)

疫学

• 中年女性に多い(男女=1:3で40歳代に最も多い) (YN.B-59)

病理

• 肝内門脈末梢枝のつぶれ像

病態

• 門脈圧の亢進：30cmH₂Oを越えない(YN.B-59)
• 閉塞肝静脈圧は正常

検査

確定診断のために門脈造影、肝静脈カテーテル法、腹腔鏡、肝生検を行う(YN .B-59)　←　肝硬変などを除外診断するのため？

腹腔鏡

• 正常、もしくは波打ち状

肝静脈造影

• しだれ柳状所見(肝静脈枝の相互間吻合)

閉塞性肝静脈圧

肝内性、前類洞性の門脈圧亢進症の所見

• 正常～中等度上昇 (検査の本)
• 正常～軽度上昇 (SSUR.645)

治療

• 脾機能亢進、門脈圧亢進、食道静脈瘤に対する治療を行う。

予後

• 10年生存率：70-80% (SSUR.645)
• 年死亡率約1%(YN.B-60)

「syndrome」

　　[★]

• n.

• 症候群