多脾症
Wikipedia preview
出典(authority):フリー百科事典『ウィキペディア（Wikipedia）』「2012/04/19 22:45:22」(JST)
[Wiki en表示]
| Polysplenia |
| Classification and external resources |
| ICD-10 |
Q89.0 |
| ICD-9 |
759.0 |
| DiseasesDB |
32864 |
| eMedicine |
ped/2514 |
Polysplenia is a congenital disease manifested by multiple small accessory spleens.[1]
Associated conditions
There are frequent associated congenital anomalies all related to deviations in the development of anatomical asymmetries in early embryonic stages. These conditions considered together are called "polysplenia syndrome".[2]
Associated conditions include heterotaxy syndrome, intestinal malrotation, situs inversus, biliary atresia, and the range of congenital cardiac malformations.
Although present, the multiple small spleens are ineffective; this is termed functional asplenia.
References
- ^ "polysplenia" at Dorland's Medical Dictionary
- ^ "polysplenia syndrome" at Dorland's Medical Dictionary
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Lymphatic disease: Congenital lymphatic organ disorders (Q89.0/Q89.2, 759.0/759.2)
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| Thymus |
Thymic hypoplasia (DiGeorge syndrome) · Ectopic thymus
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| Spleen |
Congenital asplenia/hyposplenism (Asplenia with cardiovascular anomalies) · Accessory spleen · Polysplenia
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anat(h, u, t, a, l)/phys/devp
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UpToDate Contents
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English Journal
- Antenatally diagnosed right-sided stomach (dextrogastria): A rare rotational anomaly.
- Versteegh HP1, Adams SD1, Boxall S2, Burge DM1, Stanton MP3.
- Journal of pediatric surgery.J Pediatr Surg.2016 Feb;51(2):236-9. doi: 10.1016/j.jpedsurg.2015.10.060. Epub 2015 Nov 4.
- AIM: Antenatal detection of right-sided stomach (dextrogastria) is rare, and its significance in regards to intestinal rotation is unclear. We aimed to review all cases of antenatally-diagnosed dextrogastria in our regional fetal medicine unit over 10years.METHODS: A retrospective case-note review o
- PMID 26655213
- Polysplenia or Left Isomerism?
- Loomba RS1, Anderson RH.
- Internal medicine (Tokyo, Japan).Intern Med.2016;55(5):555. doi: 10.2169/internalmedicine.55.5840. Epub 2016 Mar 1.
- PMID 26935387
- Polysplenia Syndrome With Splenic and Skeletal Muscle Metastases From Thyroid Carcinoma Evaluated by FDG PET/CT: Case Report and Literature Review: A Care-Compliant Article.
- Li ZG1, Lin ZC, Mu HY.
- Medicine.Medicine (Baltimore).2016 Jan;95(4):e2532. doi: 10.1097/MD.0000000000002532.
- Polysplenia syndrome (PSS) is a rare congenital abnormality. Metastases to spleen and skeletal muscle from differentiated thyroid cancer (DTC) are also extremely rare. Our case report aims to present an interesting case of PSS associated with splenic metastasis (SM) and skeletal muscle metastasis (S
- PMID 26825891
Japanese Journal
- Successful Pancreatic Duct Stent Placement for Recurrent Pancreatitis in a Patient with Polysplenia with Agenesis of the Dorsal Pancreas and Peutz-Jeghers Syndrome
- 開心術後，静脈還流異常を伴った上大静脈狭窄に対し，ステント拡張術が著効した1例
- Polysplenia or Left Isomerism?
Related Links
- Polysplenia syndrome, also known as left isomerism, is a type of heterotaxy syndrome where there are multiple spleens congenitally as part of left-sided isomerism. Epidemiology Polysplenia is seen predominantly in female patients. It ...
- polysplenia 多脾症 polysplenia syndrome 多脾症候群 polytetrafluoroethylene (PTFE) graft ポリテトラフルオロエチレン人工血管(グラフト) polyuria 多尿[症] POMC (pro-opiomelanocortin) プロオピオメラノコルチン Pompe's disease ポンペ病 ...
★リンクテーブル★
[★]
- 英
- polysplenia syndrome
- 関
- 無脾症、無脾症候群。多脾症 polysplenia
概念
病態
- 肺 ：両肺ともに左型
- 大血管：大静脈系の異常
- 心臓：心房が左型