カルバモイルリン酸合成酵素、カルバモイルリン酸シンターゼ
- 関
- carbamoyl-phosphate synthetase、carbamoyl-phosphate synthetase I
WordNet
- a salt of phosphoric acid (同)orthophosphate, inorganic_phosphate
- carbonated drink with fruit syrup and a little phosphoric acid
PrepTutorEJDIC
- 〈U〉リン酸塩 / 《複数形で》リン酸肥料
UpToDate Contents
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English Journal
- Purification of carbamoyl phosphate synthetase 1 (CPS1) from wood frog (Rana sylvatica) liver and its regulation in response to ice-nucleation and subsequent whole-body freezing.
- Green SR, Storey KB.
- Molecular and cellular biochemistry. 2019 May;455(1-2)29-39.
- Carbamoyl phosphate synthetase I (CPS1) represents an important regulatory enzyme of the urea cycle that mediates the ATP-driven reaction ligating ammonium, carbonate, and phosphate to form carbamoyl phosphate. The freeze-tolerant wood frog (Rana sylvatica or Lithobates sylvaticus) accumulates high
- PMID 30421312
- TMEM70 deficiency: Novel mutation and hypercitrullinemia during metabolic decompensation.
- Staretz-Chacham O, Wormser O, Manor E, Birk OS, Ferreira CR.
- American journal of medical genetics. Part A. 2019 Apr;().
- Respiratory chain disorders comprise a heterogeneous group of diseases that are the result of mutations in nuclear or mitochondrial genes. TMEM70 encodes a nuclear protein involved in the assembly of respiratory chain complex V. Although mutations in various genes can result in isolated complex V de
- PMID 30950220
- Overexpression of carbamoyl-phosphate synthase 1 significantly improves ureagenesis of human liver HepaRG cells only when cultured under shaking conditions.
- Adam AAA, van der Mark VA, Ruiter JPN, Wanders RJA, Oude Elferink RPJ, Chamuleau RAFM, Hoekstra R.
- Mitochondrion. 2019 Feb;().
- Hyperammonemia is an important contributing factor to hepatic encephalopathy in end-stage liver failure patients. Therefore reducing hyperammonemia is a requisite of bioartificial liver support (BAL). Ammonia elimination by human liver HepaRG cells occurs predominantly through reversible fixation in
- PMID 30802674
Japanese Journal
- バルプロ酸誘発高アンモニア血症に対するCPS1 4217C>A遺伝子多型の影響
- 八木 麻理子,NAKAMURA Tsutomu,OKIZUKA Yo,OYAZATO Yoshinobu,KAWASAKI Yoko,TSUNEISHI Shuichi,SAKAEDA Toshiyuki,MATSUO Masafumi,OKUMURA Katsuhiko,OKAMURA Noboru
- Pediatrics international : official journal of the Japan Pediatric Society 52(5), 744-748, 2010-10-01
- NAID 10028184232
- A case of carbamoyl phosphate synthetase 1 deficiency presenting symptoms at one month of age
- ONO Hiroaki,SUTO Tetsushi,KINOSHITA Yoshihisa,SAKANO Takashi,FURUE Takeki,OHTA Toshiyuki
- Brain & development 31(10), 779-781, 2009-11-01
- NAID 10026413113
Related Links
- Carbamoyl phosphate synthetase I deficiency is an inherited disorder that causes ammonia to accumulate in the blood (hyperammonemia). Ammonia, which is formed when proteins are broken down in the body, is toxic ...
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★リンクテーブル★
[★]
- 英
- carbamoyl-phosphate synthetase、carbamoyl-phosphate synthase, carbamyl phosphate synthetase CPS
- 関
- カルバモイルリン酸シンテターゼ、カルバモイルリン酸合成酵素I、カルバモイルリン酸シンターゼ
[show details]
carbamylphosphate synthetase : 約 80,400 件
carbamoylphosphate synthetase : 約 16,200 件
carbamylphosphate synthetase : 30 件
carbamoylphosphate synthetase : 67 件
[★]
- 英
- carbamoyl-phosphate synthase
- 関
- カルバモイルリン酸合成酵素
[★]
グルタミン加水分解性カルバモイルリン酸合成酵素、グルタミン加水分解性カルバモイルリン酸シンターゼ
[★]
カルバモイルリン酸合成酵素I、カルバモイルリン酸シンターゼI
- 関
- carbamoyl-phosphate synthetase I
[★]
カルバモイルリン酸合成酵素I欠損症、カルバモイルリン酸シンターゼI欠損症
[★]
カルバモイルリン酸合成酵素II、カルバモイルリン酸シンターゼII
[★]
- 関
- inorganic phosphate、orthophosphate、orthophosphoric acid、phospho、phosphoester、phosphoric、phosphoric acid、phosphoric acid ester、phosphorus
[★]
- 関
- lyase、synthetase、transferase