関: sinus histiocytosis with

WordNet

an impairment of health or a condition of abnormal functioning
caused by or altered by or manifesting disease or pathology; "diseased tonsils"; "a morbid growth"; "pathologic tissue"; "pathological bodily processes" (同)morbid, pathologic, pathological
large genus of erect or climbing prickly shrubs including roses (同)genus Rosa

PrepTutorEJDIC

(体の)『病気』,疾患 / (精神・道徳などの)病気,病弊
女性の話術芸人 =diseur
病気にかかった / 病的な,不健全な(morbid)

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出典(authority):フリー百科事典『ウィキペディア（Wikipedia）』「2014/11/12 19:13:06」(JST)

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Rosai–Dorfman disease, also known as sinus histiocytosis with massive lymphadenopathy, is a rare disorder of unknown etiology that is characterized by abundant histiocytes in the lymph nodes throughout the body.^[1]^,^[2]

Presentation

Lymphadenopathy of the neck is the most common place of histiocyte accumulation, although accumulation outside of lymph nodes may occur, as well. The most common sites of accumulation outside of the lymph nodes are skin, upper respiratory tract, and the sinuses.^[3]^[4] The disease can be also diagnosed in thyroid gland.^[5]

The symptoms of this disease vary with the site of accumulation similar to other regional tumors. For instance, accumulation in closed spaces such as the cranium can lead to poor outcomes compared to growth in the dermis of an extremity where surgical excision is possible.

The disease is usually non-progressive and self-limited, but patients can manifest autoimmune hemolytic anemia. It can rarely present with massive hemoptysis. ^[6] Extra nodal sites such as skin, mucosae, spinal cord and pancreas may be involved.^[1]

History

This condition has been named after Ronald F. Dorfman and Juan Rosai. An alternative eponym of this condition is known as Destombes-Rosai-Dorfman syndrome, part of which is named after Pierre-Paul Louis Lucien Destombes.

References

^ ^a ^b Riyaz, Najeeba; Khader A (2005). "Rosai Dorfman Syndrome". Indian Journal of Dermatology, Venerology and Leprology 71 (5): 342–344. doi:10.4103/0378-6323.16786. PMID 16394460. Retrieved 2 December 2013.
^ James, William D.; Berger, Timothy G.; et al. (2006). Andrews' Diseases of the Skin: clinical Dermatology. Saunders Elsevier. ISBN 0-7216-2921-0.
^ Foucar E, Rosai J, Dorfman R (1990). "Sinus histiocytosis with massive lymphadenopathy (Rosai-Dorfman disease): review of the entity". Semin Diagn Pathol 7 (1): 19–73. PMID 2180012. |accessdate= requires |url= (help)
^ Walid MS, Grigorian AA (2010). "Ethmo-spheno-intracranial Rosai-Dorfman disease". Indian J Cancer 47 (1): 80–81. doi:10.4103/0019-509X.58870. PMID 20071801.
^ Lee FY, Jan YJ, Chou G, Wang J, Wang CC. (2007). "Thyroid involvement in Rosai-Dorfman disease.". Thyroid 17 (5): 471–6. doi:10.1089/thy.2006.0192. PMID 17542678.
^ Journal, Chest; Lakshmi Varadarajalu, MD; Sunder Thirugnanasambandan, MS; Paul Jude Thangaraj, MS; Ashok Parameswaran, MD; Meghena Mathew*, MBBS (October 2012). "A Rare Presentation of Rosai Dorfman Disease". Chest. 4 142 (meeting abstracts): 998A–998A. doi:10.1378/chest.1389638. Cite uses deprecated parameters (help)

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1. ランゲルハンス細胞組織球症の臨床症状、病理学的特徴、および診断 clinical manifestations pathologic features and diagnosis of langerhans cell histiocytosis
2. 小児における末梢のリンパ節腫脹 peripheral lymphadenopathy in children etiology
3. 成人における末梢リンパ節腫大の評価 evaluation of peripheral lymphadenopathy in adults
4. ランゲルハンス細胞組織球症の治療 treatment of langerhans cell histiocytosis
5. エルドハイム・チェスター病 erdheim chester disease

English Journal

Rosai-Dorfman Disease Presenting as a Breast Mass and Enlarged Axillary Lymph Node Mimicking Malignancy: A Case Report and Review of the Literature.

Tenny SO, McGinness M, Zhang D, Damjanov I, Fan F.SourceDepartments of Pathology Surgery, University of Kansas Medical Center, Kansas City, Kansas.
The breast journal.Breast J.2011 Jul 15. doi: 10.1111/j.1524-4741.2011.01131.x. [Epub ahead of print]
? Rosai-Dorfman disease (also called sinus histiocytosis with massive lymphadenopathy) involves lymph nodes or lymph nodes with extranodal sites. We present a unique case of a patient presenting with a breast mass and axillary lymphadenopathy, mimicking malignancy clinically and radiographically.
PMID 21762247

Rosai-Dorfman Disease Presenting in the Parotid Gland With Features of IgG4-Related Sclerosing Disease.

Chen TD, Lee LY.SourceDepartment of Pathology, Chang Gung Memorial Hospital, 5 Fuxing St, Guishan Township, Taoyuan County 333, Taiwan. r22068@cgmh.org.tw.
Archives of otolaryngology--head & neck surgery.Arch Otolaryngol Head Neck Surg.2011 Jul;137(7):705-8. Epub 2011 Apr 18.
PMID 21502465

Japanese Journal

症例多彩な炎症細胞浸潤を伴い診断が困難であったCutaneous Rosai-Dorfman Diseaseの1例--病理組織学的所見を中心に

綿貫(工藤) 沙織,石橋正史,山本享子 [他]
皮膚科の臨床 53(1), 125-129, 2011-01
NAID 40017659725

Isolated Intracranial Rosai-Dorfman Disease Without Dural Attachment : —Case Report—

FUKUSHIMA Takao,YACHI Kazunari,OGINO Akiyoshi,OHTA Takashi,WATANABE Takao,YOSHINO Atsuo,KATAYAMA Yoichi
Neurologia medico-chirurgica 51(2), 136-140, 2011
… However, histological examinations yielded a diagnosis of Rosai-Dorfman disease. … Isolated intracranial Rosai-Dorfman disease is very rare, and without dural attachment, as in our case, is exceptional. … Rosai-Dorfman disease should be considered in the differential diagnosis of isolated intraparenchymal tumors. …
NAID 130000442547

Related Pictures

★リンクテーブル★

リンク元	「ロザイ・ドルフマン病」「Rosai-Dorfman病」
関連記事	「disease」「Rosa」

「ロザイ・ドルフマン病」

Rosai-Dorfman disease
	Classification and external resources
	Micrograph of a lymph node involved by Rosai-Dorfman disease showing emperipolesis. H&E stain.
ICD-10	D76.3 (ILDS D76.360)
DiseasesDB	31419

　　[★]

英: Rosai-Dorfman disease
関: 洞組織球症、Rosai-Dorfman病

「Rosai-Dorfman病」

　　[★]

英: Rosai-Dorfman disease
関: ロザイ・ドルフマン病

「disease」

　　[★]

n.

疾患：illnessより厳密な概念。「ある臓器に明確な障害が確認され、それによって症状が出ているとはっきり説明できる場合」 (PSY.9)

特定の原因、病態生理、症状、経過、予後、病理組織所見が全てそろった場合 (PSY.9)

something that is very wrong with people's attitudes, way of life or with society.

関: ail、ailment、disease entity、disorder、ill、illness、malady、sick、sickness

注意

disease ≠ illness ≠ disorder

「Rosa」

　　[★]

バラ属、ローザ属、Rosa属

関: Rosaceae、Rosales、rose

[riyaz-1] Riyaz, Najeeba; Khader A (2005). "Rosai Dorfman Syndrome". Indian Journal of Dermatology, Venerology and Leprology 71 (5): 342–344. doi:10.4103/0378-6323.16786. PMID 16394460. Retrieved 2 December 2013.

[Andrews-2] James, William D.; Berger, Timothy G.; et al. (2006). Andrews' Diseases of the Skin: clinical Dermatology. Saunders Elsevier. ISBN 0-7216-2921-0.

[pmid2180012-3] Foucar E, Rosai J, Dorfman R (1990). "Sinus histiocytosis with massive lymphadenopathy (Rosai-Dorfman disease): review of the entity". Semin Diagn Pathol 7 (1): 19–73. PMID 2180012. |accessdate= requires |url= (help)

[4] Walid MS, Grigorian AA (2010). "Ethmo-spheno-intracranial Rosai-Dorfman disease". Indian J Cancer 47 (1): 80–81. doi:10.4103/0019-509X.58870. PMID 20071801.

[pmid17542678-5] Lee FY, Jan YJ, Chou G, Wang J, Wang CC. (2007). "Thyroid involvement in Rosai-Dorfman disease.". Thyroid 17 (5): 471–6. doi:10.1089/thy.2006.0192. PMID 17542678.

[6] Journal, Chest; Lakshmi Varadarajalu, MD; Sunder Thirugnanasambandan, MS; Paul Jude Thangaraj, MS; Ashok Parameswaran, MD; Meghena Mathew*, MBBS (October 2012). "A Rare Presentation of Rosai Dorfman Disease". Chest. 4 142 (meeting abstracts): 998A–998A. doi:10.1378/chest.1389638. Cite uses deprecated parameters (help)

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案内

Rosai-Dorfman disease