孤在性線維性腫瘍
WordNet
- (of meat) full of sinews; especially impossible to chew (同)sinewy, stringy, unchewable
- an abnormal new mass of tissue that serves no purpose (同)tumour, neoplasm
PrepTutorEJDIC
- 『ひとりぼっちの』 / 孤独な,一人でする / 人の訪れのまれな,人里離れた / 《名詞の前にのみ用いて》《通例否定・疑問文で》たった一つの,唯一の(single) / 〈C〉独居者,隠者 / 〈U〉《話》=solitary confinement
- 繊維の,繊維状(質)の
Wikipedia preview
出典(authority):フリー百科事典『ウィキペディア（Wikipedia）』「2013/10/04 11:52:04」(JST)
[Wiki en表示]
| Solitary fibrous tumor |
| Classification and external resources |
Micrograph of a solitary fibrous tumor. H&E stain.
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| ICD-O: |
M8815/0 |
| MeSH |
D054364 |
Solitary fibrous tumor (SFT) is a rare mesenchymal tumor originating in the pleura[1] or at virtually any site in the soft tissue. Approximately 78% to 88% of SFT's are benign and 12% to 22% are malignant.[2]
SFT was first mentioned in the scientific literature by Wagner.[3] The first discussion of its clinical and pathological properties was by Klemperer and Rabin.[2][4]
Over the years this entity acquired a number of synonyms, including localized fibrous tumor, benign mesothelioma, localized fibrous mesothelioma, submesothelial fibroma, and pleural fibroma. The use of names that include ‘mesothelioma’ for this tumor is discouraged because of potential confusion with diffuse malignant mesothelioma, a much more serious disease.[1]
About 80% of SFT's originate in the visceral pleura, while 20% arise from parietal pleura.[5] Although they are often very large tumors (up to 40 cm. in diameter), over half are asymptomatic at diagnosis.[5] While some researchers have proposed that a SFT occupying at least 40% of the affected hemithorax be considered a "giant solitary fibrous tumor",[6] no such "giant" variant has yet been recognized within the most widely used pleural tumor classification scheme.[1]
Contents
- 1 Treatment and prognosis
- 2 See also
- 3 Additional images
- 4 References
- 5 External links
Treatment and prognosis[edit]
The treatment of choice for both benign and malignant SFT is complete en bloc surgical resection.
Prognosis in benign SFT's is excellent. About 8% will recur after first resection, with the recurrence usually cured after additional surgery.[2]
The prognosis in malignant SFT's is much more guarded. Approximately 63% of patients will have a recurrence of their tumor, of which more than half will succumb to disease progression within 2 years.[2] Adjuvant chemotherapy and/or radiotherapy in malignant SFT remains controversial.[2]
See also[edit]
- Hemangiopericytoma
- Myopericytoma
Additional images[edit]
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Solitary fibrous tumor - low magnification. H&E stain.
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Solitary fibrous tumor - high magnification. H&E stain.
References[edit]
- ^ a b c Travis WD, Brambilla E, Muller-Hermelink HK, Harris CC (Eds.): World Health Organization Classification of Tumours. Pathology and Genetics of Tumours of the Lung, Pleura, Thymus and Heart. IARC Press: Lyon 2004.
- ^ a b c d e Robinson LA. Solitary fibrous tumor of the pleura. Cancer Control 2006;13:264-9.
- ^ Wagner E. Das tuberkelahnliche lymphadenom (der cytogene oder reticulirte tuberkel). Arch Heilk (Leipig). 1870;11:497.>
- ^ de Perrot M, Fischer S, Brundler MA, et al. Solitary fibrous tumors of the pleura. Ann Thorac Surg. 2002;74:285-293.
- ^ a b Briselli M, Mark EJ, Dickersin GR. Solitary fibrous tumors of the pleura: eight new cases and review of 360 cases in the literature. Cancer 1981;47:2678-89.
- ^ Pinedo-Onofre JA, Robles-Pérez E, Peña-Mirabal ES, Hernández-Carrillo JA, Téllez-Becerra JL. [Giant solitary fibrous tumor of the pleura.] Cir Cir 2010;78:31-43. [Article in Spanish].
External links[edit]
- [1] World Health Organization Classification of Tumours. Pathology and Genetics of Tumours of the Lung, Pleura, Thymus and Heart. (Download Page)
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Tumors: Mediastinal tumors/Thoracic neoplasm/respiratory neoplasia (C30–C34/D14, 160–163/212.0–212.4)
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| Upper RT |
- Nasal cavity
- Esthesioneuroblastoma
- Nasopharynx
- Nasopharyngeal carcinoma
- Nasopharyngeal angiofibroma
- Larynx
- Laryngeal cancer
- Laryngeal papillomatosis
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| Lower RT |
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Trachea
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Lung
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Non-small-cell lung carcinoma
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- Squamous cell carcinoma
- Adenocarcinoma of the lung (Mucinous cystadenocarcinoma)
- Large-cell lung carcinoma
- Rhabdoid carcinoma
- Sarcomatoid carcinoma
- Carcinoid
- Salivary gland-like carcinoma of the lung
- Adenosquamous carcinoma
- Papillary adenocarcinoma
- Giant cell carcinoma
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Small-cell carcinoma
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- Combined small-cell carcinoma
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Non-carcinoma
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- Sarcoma
- Lymphoma
- Immature teratoma
- Melanoma
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By location
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- Pancoast tumor
- Solitary pulmonary nodule
- Central lung
- Peripheral lung
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| Pleura |
- Mesothelioma
- Malignant solitary fibrous tumor
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anat (n, x, l, c)/phys/devp
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noco (c, p)/cong/tumr, sysi/epon, injr
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proc, drug (R1/2/3/5/6/7)
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Connective/soft tissue tumors and sarcomas (ICD-O 8800–9059) (C45–C49/D17–D21, 171/214–215)
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| Not otherwise specified (8800–8809) |
Soft tissue sarcoma · Desmoplastic small round cell tumor
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| Connective tissue neoplasm |
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Fibromatous (8810–8839)
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Fibroma/fibrosarcoma: Dermatofibrosarcoma · Dermatofibrosarcoma protuberans · Desmoplastic fibroma
Fibroma/fibromatosis: Aggressive infantile fibromatosis · Aponeurotic fibroma · Collagenous fibroma · Diffuse infantile fibromatosis · Familial myxovascular fibromas · Fibroma of tendon sheath · Fibromatosis colli · Infantile digital fibromatosis · Juvenile hyaline fibromatosis · Plantar fibromatosis · Pleomorphic fibroma · Oral submucous fibrosis
Histiocytoma/histiocytic sarcoma: Benign fibrous histiocytoma · Malignant fibrous histiocytoma · Atypical fibroxanthoma
Solitary fibrous tumor
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Myxomatous (8840–8849)
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Myxoma/myxosarcoma (Cutaneous myxoma, Superficial acral fibromyxoma) · Angiomyxoma · Ossifying fibromyxoid tumour
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Fibroepithelial (9000–9039)
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Brenner tumour · Fibroadenoma · Phyllodes tumor
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Synovial-like (9040–9049)
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Synovial sarcoma · Clear-cell sarcoma
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| Lipomatous (8850–8889) |
Lipoma/liposarcoma (Myelolipoma, Myxoid liposarcoma) · PEComa (Angiomyolipoma)
Chondroid lipoma · Intradermal spindle cell lipoma · Pleomorphic lipoma · Benign lipoblastomatosis · Spindle cell lipoma · Hibernoma
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| Myomatous (8890–8929) |
general: Myoma/myosarcoma
smooth muscle: Leiomyoma/leiomyosarcoma
skeletal muscle: Rhabdomyoma/rhabdomyosarcoma: Embryonal rhabdomyosarcoma (Sarcoma botryoides) · Alveolar rhabdomyosarcoma
Leiomyoma · Angioleiomyoma · Angiolipoleiomyoma · Genital leiomyoma · Leiomyosarcoma · Multiple cutaneous and uterine leiomyomatosis syndrome · Multiple cutaneous leiomyoma · Neural fibrolipoma · Solitary cutaneous leiomyoma · STUMP
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| Complex mixed and stromal (8930–8999) |
Adenomyoma · Pleomorphic adenoma · Mixed Müllerian tumor · Mesoblastic nephroma · Wilms' tumor · Rhabdoid tumour · Clear-cell sarcoma of the kidney · Hepatoblastoma · Pancreatoblastoma · Carcinosarcoma
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| Mesothelial (9050–9059) |
Mesothelioma · Adenomatoid tumor
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see also Template:Connective tissue
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anat (h/n, u, t/d, a/p, l)/phys/devp/hist
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noco (m, s, c)/cong (d)/tumr, sysi/epon, injr
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UpToDate Contents
全文を閲覧するには購読必要です。 To read the full text you will need to subscribe.
English Journal
- Immunohistochemical Staining for TLE1 Distinguishes Synovial Sarcoma From Histologic Mimics.
- Foo WC, Cruise MW, Wick MR, Hornick JL.SourceDept of Pathology, Brigham and Women's Hospital, 75 Francis St, Boston, MA 02115.
- American journal of clinical pathology.2011 Jun;135(6):839-44.
- Transducer-like enhancer of split 1 (TLE1) is overexpressed in synovial sarcomas. We investigated TLE1 expression by immunohistochemical analysis in a well-characterized series of synovial sarcomas and other mesenchymal tumors most commonly considered in the differential diagnosis. Whole tissue sect
- PMID 21571956
- An immunohistochemical study of sinonasal hemangiopericytoma.
- Yokoi H, Arakawa A, Kuribayashi K, Inoshita A, Haruyama T, Ikeda K.SourceDepartment of Otorhinolaryngology, Juntendo University School of Medicine, Tokyo, Japan; Department of Otolaryngology, Head and Neck Surgery, Kyorin University School of Medicine, Japan.
- Auris, nasus, larynx.2011 May 19. [Epub ahead of print]
- We present herein the imaging and pathological features of a 28-year-old male with a sinonasal hemangiopericytoma-like tumor occupying the left nasal meatus. At the initial visit, a nasal polyp was suspected, but, as the patient was bleeding readily, an angiomatoid lesion was also regarded as a poss
- PMID 21601390
Japanese Journal
- 症例 肝臓solitary fibrous tumorの1例 (特集 消化器最新情報2011)
- 重光 希公生,中島 治典,白木 晶,安部 崇,安藤 守秀,進藤 丈
- 肺癌 51(2), 99-103, 2011
- … 背景．胸膜孤立性線維性腫瘍（solitary fibrous tumor of the pleura：SFTP）は中皮下組織由来の稀な腫瘍である．症例．57歳，男性．脳塞栓症に対しワーファリンを内服していた．咳と呼吸困難感を主訴に当院を受診した．左特発性血胸と診断され，胸腔ドレーンを留置されたが，保存的治療では改善が見られず，開胸術が施行された．術中，左下葉に破裂した大きな壊死性の腫瘤が認めら …
- NAID 130000653640
Related Links
- 孤在性線維性腫瘍 solitary fibrous tumor - 様々な脳腫瘍や脳神経の病気について説明しています。さわむら脳神経クリニックで診療しています。Eメールによる相談や手術治療も受け付けています。
- Solitary fibrous tumor (SFT) is a rare mesenchymal neoplasm which may be found everywhere in the body. It is now distinguished into two forms, pleural and extrapleural, which morphologically resemble each other. Abdominal ...
★リンクテーブル★
[★]
- 英
- solitary fibrous tumor
- 関
- 胸膜線維腫
[★]
- 関
- fibrotic、filamentous
[★]