WordNet

of or relating to the medulla of any body part
containing or consisting of or resembling bone marrow
of or relating to the medulla oblongata
either of two bean-shaped excretory organs that filter wastes (especially urea) from the blood and excrete them and water in urine; "urine passes out of the kidney through ureters to the bladder"
of or relating to or resembling a cyst
of or relating to a normal cyst (as the gallbladder or urinary bladder)
the inner part of an organ or structure in plant or animal
a closed sac that develops abnormally in some body structure

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1. 常染色体優性間質性腎臓病（髄質嚢胞性腎疾患） autosomal dominant interstitial kidney disease medullary cystic kidney disease
2. 嚢胞性腎疾患の胎児超音波診断 prenatal sonographic diagnosis of cystic renal disease
3. 常染色体優性多発性嚢胞腎の診断およびスクリーニング diagnosis of and screening for autosomal dominant polycystic kidney disease
4. 成人における単純性および複雑性腎嚢胞 simple and complex renal cysts in adults
5. ネフロン癆の臨床症状、診断、および治療 clinical manifestations diagnosis and treatment of nephronophthisis

Long-Term Follow-Up of Kidney Transplant Recipients With Polycystic Kidney Disease.

Mehrabi A1, Golriz M, Maier J, Fonouni H, Garoussi C, Hafezi M, Fard N, Faridar A, Rezaei N, Wiesel M, Mieth M, Morath C, Büchler MW, Tönshoff B, Zeier M, Schmidt J, Schemmer P.
Experimental and clinical transplantation : official journal of the Middle East Society for Organ Transplantation.Exp Clin Transplant.2015 Oct;13(5):413-20.
OBJECTIVES: Patients with polycystic kidney disease are candidates for kidney transplant. We report the results of our single center study of 250 first transplant recipients with polycystic kidney disease (autosomal dominant [64%], medullary cystic [16%], autosomal recessive [6%], and nonspecified [
PMID 26450465

Autosomal dominant tubulointerstitial kidney disease: diagnosis, classification, and management-A KDIGO consensus report.

Eckardt KU1, Alper SL2, Antignac C3,4, Bleyer AJ5, Chauveau D6, Dahan K7, Deltas C8, Hosking A9, Kmoch S10, Rampoldi L11, Wiesener M1, Wolf MT12, Devuyst O13.
Kidney international.Kidney Int.2015 Oct;88(4):676-83. doi: 10.1038/ki.2015.28. Epub 2015 Mar 4.
Rare autosomal dominant tubulointerstitial kidney disease is caused by mutations in the genes encoding uromodulin (UMOD), hepatocyte nuclear factor-1β (HNF1B), renin (REN), and mucin-1 (MUC1). Multiple names have been proposed for these disorders, including 'Medullary Cystic Kidney Disease (MCKD) t
PMID 25738250

Rajagopal M1, Wallace DP.
Current opinion in nephrology and hypertension.Curr Opin Nephrol Hypertens.2015 Sep;24(5):444-9. doi: 10.1097/MNH.0000000000000148.
PURPOSE OF REVIEW: Renal collecting ducts maintain NaCl homeostasis by fine-tuning urinary excretion to balance dietary salt intake. This review focuses on recent studies on transcellular Cl secretion by collecting ducts, its regulation and its role in cyst growth in autosomal dominant polycystic ki
PMID 26125646

杉本圭相
日本小児腎臓病学会雑誌 30(2), 112-118, 2017
<p>ネフロン癆(nephronophthisis: NPH)は，腎髄質に囊胞形成を認める進行性の囊胞性腎疾患の代表であり，小児期の末期腎不全の約5％を占める。組織学的には，進行性の硬化，硝子化糸球体を伴う尿細管間質性腎炎像を呈する。遺伝形式は主として常染色体劣性遺伝を示す。NPH の初期症状は，多飲，多尿，尿最大濃縮能の低下，二次性の遺尿や成長障害であるが，病勢がかなり進行した末期腎 …
NAID 130006201492

加藤翔子,後藤康友,湯浅典博,竹内英司,三宅秀夫,宮田完志,波多野寿,藤野雅彦
日本消化器外科学会雑誌 50(7), 587-595, 2017
<p>　症例は31歳の女性で，2011年5月に下肢の痺れを主訴に当院を受診した．MRIで多発脊髄腫瘍，CTで右副腎，後腹膜腫瘍，多発膵腫瘍を指摘された．尿中ノルメタネフリンが高値であり，褐色細胞腫，膵内分泌腫瘍（pancreatic neuroendocrine tumor；以下，P-NETと略記）を伴うvon Hippel-Lindau病（以下，VHL病と略記）と診断し右副腎，後腹膜 …
NAID 130005865163