WordNet
- shaped like a ring (同)annulate, annulated, circinate, ringed, ring-shaped, doughnut-shaped
- a large elongated exocrine gland located behind the stomach; secretes pancreatic juice and insulin
PrepTutorEJDIC
- 《文》環状の
- 膵臓(すいぞう)
- 〈法律など〉'を'無効にする;〈命令など〉'を'取り消す(cancel)
Wikipedia preview
出典(authority):フリー百科事典『ウィキペディア(Wikipedia)』「2013/12/08 23:19:06」(JST)
[Wiki en表示]
Annular pancreas |
Classification and external resources |
ICD-10 |
Q45.1 |
ICD-9 |
751.7 |
OMIM |
167750 |
MedlinePlus |
001142 |
Annular pancreas is a rare condition in which the second part of the duodenum is surrounded by a ring of pancreatic tissue continuous with the head of the pancreas. This portion of the pancreas can constrict the duodenum and block or impair the flow of food to the rest of the intestines. It is estimated to occur in 1 out of 12,000 to 15,000 newborns.[1] The ambiguity arises from the fact that not all cases are symptomatic.[2]
Contents
- 1 Causes
- 2 Presentation
- 3 Diagnosis
- 4 Treatment
- 5 References
Causes[edit]
It is typically associated with abnormal embryological development, however adult cases can develop. It can result from growth of a bifid ventral pancreatic bud around the duodenum, where the parts of the bifid ventral bud fuse with the dorsal bud, forming a pancreatic ring. It can also result if the ventral pancreatic bud fails to fully rotate, so it remains on the right or if the dorsal bud rotates in the wrong direction, such that the duodenum is surrounded by pancreatic tissue. Blockage of the duodenum develops if inflammation (pancreatitis) develops in the anular pancreas.
Presentation[edit]
Early signs of abnormality include polyhydramnios (an excess of amniotic fluid), low birth weight, and feeding intolerance immediately after birth.
Diagnosis[edit]
Postnatal diagnostic procedures include abdominal x-ray and ultrasound, CT scan, and upper GI and small bowel series.
Treatment[edit]
Treatment usually is bypassing the obstructed segment of duodenum by duodeno-duodenostomy. Another approach is laparoscopic gastrojejunostomy.[3]
References[edit]
- ^ Lainakis N, Antypas S, Panagidis A et al. (2005). "Annular pancreas in two consecutive siblings: an extremely rare case". European Journal of Pediatric Surgery 15 (5): 364–8. doi:10.1055/s-2005-865838. PMID 16254852.
- ^ Ravitch, MM. (1975). "The pancreas in infants and children". Surg Clin North Am 55 (2): 377–85. PMID 165579.
- ^ De Ugarte DA, Dutson EP, Hiyama DT (2006). "Annular pancreas in the adult: management with laparoscopic gastrojejunostomy". The American surgeon 72 (1): 71–3. PMID 16494188.
Congenital malformations and deformations of digestive system (Q35–Q45, 749–751)
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Upper GI tract |
Tongue, mouth and pharynx |
- Cleft lip and palate
- Van der Woude syndrome
- tongue
- Ankyloglossia
- Macroglossia
- Hypoglossia
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Esophagus |
- EA/TEF
- Esophageal atresia: types A, B, C, and D
- Tracheoesophageal fistula: types B, C, D and E
- esophageal rings
- Esophageal web (upper)
- Schatzki ring (lower)
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Stomach |
- Pyloric stenosis
- Hiatus hernia
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Lower GI tract |
Intestines |
- Intestinal atresia
- Meckel's diverticulum
- Hirschsprung's disease
- Intestinal malrotation
- Dolichocolon
- Enteric duplication cyst
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Rectum/anal canal |
- Imperforate anus
- Vestibular fistula
- Persistent cloaca
- Rectal atresia
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Accessory |
Pancreas |
- Annular pancreas
- Accessory pancreas
- Johanson–Blizzard syndrome
Pancreas divisum
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Bile duct |
- Choledochal cysts
- Biliary atresia
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Liver |
- Alagille syndrome
- Polycystic liver disease
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noco/cofa (c)/cogi/tumr, sysi
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anat (t, g, p)/phys/devp/enzy
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noco/cong/tumr, sysi/epon
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proc, drug (A2A/2B/3/4/5/6/7/14/16), blte
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UpToDate Contents
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- 1. 輪状膵 annular pancreas
- 2. 膵管癒合不全の解剖学および臨床的意義 anatomy and clinical significance of pancreas divisum
- 3. 消化管閉鎖症および閉塞の出生前診断 prenatal diagnosis of gastrointestinal atresia and obstruction
- 4. 成人における胃流出路閉塞 gastric outlet obstruction in adults
- 5. 消化管の発達に関する概要 overview of the development of the gastrointestinal tract
English Journal
- Endoscopic Ultrasonography May Select Subjects Having Asymptomatic Chronic Pancreatic Hyperenzymemia Who Require a More Strict Follow-up.
- Antonini F1, Belfiori V, Pagano N, Buscarini E, De Minicis S, Lo Cascio M, Marraccini B, Piergallini S, Rossetti P, Andrenacci E, Macarri G, Pezzilli R.
- Pancreas.Pancreas.2017 Feb 14. doi: 10.1097/MPA.0000000000000796. [Epub ahead of print]
- OBJECTIVES: We have previously shown that at least 50% of patients having asymptomatic chronic pancreatic hyperenzymemia (ACPH) may develop morphological pancreatic alterations. Endoscopic ultrasonography (EUS) may detect small lesions, and its sensitivity seems to be higher than other imaging techn
- PMID 28196017
- Circumportal Pancreas-a Must Know Pancreatic Anomaly for the Pancreatic Surgeon.
- Luu AM1, Braumann C2, Herzog T2, Janot M2, Uhl W2, Chromik AM3.
- Journal of gastrointestinal surgery : official journal of the Society for Surgery of the Alimentary Tract.J Gastrointest Surg.2017 Feb;21(2):344-351. doi: 10.1007/s11605-016-3315-8. Epub 2016 Nov 8.
- PURPOSE: Circumportal pancreas is a rare congenital pancreatic anomaly with encasement of the portal vein and/or the superior mesenteric vein by pancreatic tissue. It is often overlooked on cross-sectional imaging studies and can be encountered during pancreatic surgery. Pancreatic head resection wi
- PMID 27826941
- Portal Annular Pancreas: A Rare and Overlooked Anomaly.
- Mittal P1, Gupta R1, Mittal A1, Ahmed A2.
- Polish journal of radiology.Pol J Radiol.2017 Jan 24;82:38-40. doi: 10.12659/PJR.899733. eCollection 2017.
- BACKGROUND: Portal annular pancreas is a rare pancreatic developmental anomaly which is often overlooked at imaging, and often diagnosed retrospectively when it is detected incidentally at the time of surgery. Although the anomaly itself is asymptomatic, it becomes important in cases where pancreati
- PMID 28203311
Japanese Journal
- 門脈輪状膵にreplaced―右肝動脈を伴った十二指腸乳頭部癌の1例
Related Links
- Annular pancreas is a rare congenital abnormality characterized by a ring of pancreatic tissue surrounding the descending portion of the duodenum. It is thought to originate from incomplete rotation of the ventral pancreatic bud. This ...
- Annular pancreas is problem present at birth (congenital defect). Symptoms occur when the ring of pancreas squeezes and narrows the small intestine so that food cannot pass easily or at all. Newborns may have symptoms of ...
Related Pictures
★リンクテーブル★
[★]
- 英
- annular pancreas
- ラ
- pancreas annulare
- 同
- 環状膵
- 関
- 先天奇形
概念
- 膵頭部の一部が十二指腸下行脚を部分的または全周にわたり輪状に取り囲む、稀な先天奇形である。
- 腹側膵原基が腸を伴い回転する際に、右葉の遊離端に異常を生じ、腸の全面に癒着固定されるとするレッコ説(Lecco theory)が有力である。
検査
- 立位での腹部単純X線像において、胃泡に加えて十二指腸拡張部にもガスを認めるdouble bubble sign(二泡像, ダブルバブル徴候)を認める。
- 内視鏡的逆行性胆管膵管造影(ERCP)で十二指腸を取り囲む輪状膵管を描出すれば確診がつく
- 無症候性から腹部膨満・嘔吐、ないし消化性潰瘍・膵炎・黄疸を呈するものから様々である。
- 発症時期により新生児型、小児型、成人型に分けられている。
治療
- 十二指腸十二指腸吻合(ダイアモンド型吻合)が第一選択
- 十二指腸空腸吻合は盲管症候群を来すため、あまりやられない。
- 胃空腸吻合
- 輪状膵を直接切除は膵管を損傷するため、あまりやられない。膵瘻のリスクがある。
参考
- http://www.nurs.or.jp/~academy/igaku/s5/s5651.htm
[★]
- 関
- circular、cyclic、cyclo、orbicular、orbicularis