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1. クロイツフェルト・ヤコブ病creutzfeldt jakob disease [show details]
… Gerstmann-Straussler-Scheinker syndrome (GSS) Acquired – Kuru, iatrogenic Creutzfeldt-Jakob disease (iCJD), and variant Creutzfeldt-Jakob disease (vCJD) sCJD is the most well-known and accounts for more than 90 …
2. 変異型クロイツフェルト・ヤコブ病variant creutzfeldt jakob disease [show details]
…recognized: Sporadic – Sporadic Creutzfeldt-Jakob disease (sCJD), sporadic fatal insomnia, and variably protease-sensitive prionopathy ; Genetic – Genetic Creutzfeldt-Jakob disease, fatal familial insomnia, …
3. 成人における早期発症の認知症early onset dementia in adults [show details]
…subcortical gray matter diffusion-weighted changes typical of Creutzfeldt-Jakob disease (CJD) Hydrocephalus, as seen in both idiopathic and secondary normal pressure hydrocephalus (NPH) Neuroimaging …
4. 症候性（二次性）ミオクローヌスsymptomatic secondary myoclonus [show details]
… pallidoluysian atrophy (DRPLA) Dementias: Creutzfeldt-Jakob disease (CJD) Alzheimer disease (AD) Dementia with Lewy… cancer in adults. OMS can also occur in the context of infection, or without identifiable cause (idiopathic). Celiac disease has been rarely associated with OMS . The myoclonus in OMS is usually multifocal …
5. プリオンの生物学および遺伝学biology and genetics of prions [show details]
… Five human prion diseases are currently recognized: kuru, Creutzfeldt-Jakob disease (CJD), variant CJD (vCJD, also known as new variant CJD), Gerstmann-Straussler-Scheinker syndrome (GSS), and fatal familial …

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プリオン病(1)クロイツフェルト・ヤコブ病（CJD）（指定難病23 ...

プリオン病の代表的なタイプである孤発性クロイツフェルト・ヤコブ病（Creutzfeldt-Jakob disease：CJD）は、1年間に100万人に1人程度の割合で発症することが知られている。. ヒトのプリオン病は病因により、原因不明の特発性（孤発性CJD（sporadic CJD：sCJD））、プリオン蛋白遺伝子変異による遺伝性（家族性CJD、ゲルストマン・ストロイスラー・シャインカー病（Gerstman ...