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1. ミオクローヌスの分類および評価classification and evaluation of myoclonus [show details]
… disorders that have a characteristic myoclonus physiology, and guide treatment options that may be useful for some physiologic types of myoclonus but not others . Cortical myoclonus originates with a focal discharge …
2. 症候性（二次性）ミオクローヌスsymptomatic secondary myoclonus [show details]
… amplitude "jerky postural tremor" was reported in 20 and 55 percent of cases, respectively . These reports focused on the action myoclonus of the parkinsonian type. Stimulus-sensitive myoclonus of the upper …
3. ミオクローヌスの治療treatment of myoclonus [show details]
… classification of the myoclonus in question. This topic will review the treatment of myoclonus. The treatment of myoclonic epilepsy is discussed separately. Other clinical aspects of myoclonus are reviewed elsewhere …
4. 遺伝性運動失調の概要overview of the hereditary ataxias [show details]
… Ataxia and myoclonus can be produced by a variety of mitochondrial lesions.… triggers that include physical activity or exercise, stress, environmental temperature, startle, postural change, emotion, hunger, alcohol, intercurrent illness, or caffeine . Most affected individuals …
5. 小児における運動過多な運動障害hyperkinetic movement disorders in children [show details]
… differential diagnosis of myoclonus is myoclonus-dystonia (DYT11) caused by mutations of the SGCE gene . Benign neonatal sleep myoclonus occurs in the first month after birth.… dystonia may be erroneously attributed to a postural deformity that results from common musculoskeletal or…

English Journal

A novel exaggerated "spino-bulbo-spinal like" reflex of lower brainstem origin.

Merchant SH, Vial F, Leodori G, Fahn S, Pullman SL, Hallett M.
Parkinsonism & related disorders. 2019 Apr;61()34-38.
Many different oligosynaptic reflexes are known to originate in the lower brainstem which share phenomenological and neurophysiological similarities. To evaluate and discuss the differences and aberrancies among these reflexes, which are hard to discern clinically using neurophysiological investigat
PMID 30316728

Movement disorders in cerebrotendinous xanthomatosis.

Stelten BML, van de Warrenburg BPC, Wevers RA, Verrips A.
Parkinsonism & related disorders. 2019 Jan;58()12-16.
Cerebrotendinous xanthomatosis (CTX) is an inborn error of cholesterol and bile acid metabolism, leading to neuropsychiatric and systemic manifestations. Movement disorders have rarely been reported in CTX, while a detailed appreciation of the full phenotypic spectrum is required in order to prevent
PMID 30054180

[Low-dose perampanel improved cortical myoclonus and basophobia in a patient with Unverricht-Lundborg disease: a case report].

Oi Y, Kobayashi K, Hitomi T, Matsumoto R, Ikeda A, Takahashi R.
Rinsho shinkeigaku = Clinical neurology. 2018 Oct;58(10)622-625.
We report a 32-year-old female who presented myoclonus and generalized tonic-clonic seizure since she was 9 year-old. Thereafter, she was diagnosed as Unverricht-Lundborg disease by gene analysis. Although the epileptic seizures were controlled by multiple antiepileptic drugs, her cortical myoclonus
PMID 30270337

Japanese Journal

皮質ミオクローヌスと歩行恐怖症に低容量ペランパネルが著効したUnverricht-Lundborg病の1例

大井由貴,小林勝哉,人見健文,松本理器,池田昭夫,髙橋良輔
臨床神経学, 2018
<p>32歳女性．9歳時にミオクローヌスと全般強直間代発作が出現し，遺伝子検査でUnverricht-Lundborg病と診断された．内服により全般強直間代発作は抑制されたが，ミオクローヌスは治療抵抗性であり認知機能障害，構音障害，ミオクローヌス，協調運動障害，高度の起立歩行障害と強い歩行恐怖症がみられた．ペランパネルを1 mg/日から漸増後，2 mg/日でミオクローヌスは著明に改善し …
NAID 130007492812

ビデオでみる不随意運動の基礎

宇川義一
臨床神経学 52(11), 827-831, 2012
… The most rhythmic one is tremor and most irregular one is myoclonus. … Conditions inducing involuntary movement: resting, postural, during movement, emotional stress, sensory trick or others. …
NAID 130004505177

Spinal Segmental Myoclonus during Postural Maintenance in a Patient with Cervical Spondylosis: A Case Report

Kobayashi Junpei,Yokochi Fusako,Takasu Miwako,Tobisawa Shinsuke,Shimizu Toshio
Internal Medicine 50(17), 1839-1841, 2011
… Spinal segmental myoclonus is defined as a rare involuntary movement characterized by myoclonic jerks of spinal origin. … We describe the case of a 62-year-old woman who developed spinal segmental myoclonus 4 months after undergoing cervical laminoplasty for ossification of the posterior longitudinal ligament. … The myoclonus was refractory to medication but improved with the use of a soft neck brace.<br> …
NAID 130002063079