Shulman syndrome

好酸球性筋膜炎

WordNet

1. a pattern of symptoms indicative of some disease
2. a complex of concurrent things; "every word has a syndrome of meanings"

PrepTutorEJDIC

1. (疾患の徴候となる一群の)症徴候,症候群 / (事件・社会的状態などのパターンを示す)徴候形態

UpToDate Contents

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• 1. 好酸球性筋膜炎 eosinophilic fasciitis
• 2. 特定臓器の好酸球性疾患 diseases with eosinophilic involvement of specific organs
• 3. 成人における限局性強皮症の病因、臨床症状、および診断 pathogenesis clinical manifestations and diagnosis of morphea localized scleroderma in adults
• 4. 成人における全身性硬化症（強皮症）の診断および鑑別診断 diagnosis and differential diagnosis of systemic sclerosis scleroderma in adults
• 5. 浮腫性硬化症 scleredema

English Journal

• [Eosinophilic fasciitis, morphea and vitiligo in a single patient].

• Lakjiri S1, Meziane M2, Benani A3, Harmouch T3, Amarti A3, Mernissi FZ2.
• Annales de dermatologie et de vénéréologie.Ann Dermatol Venereol.2014 Oct;141(10):598-602. doi: 10.1016/j.annder.2014.06.019. Epub 2014 Aug 7.
• BACKGROUND: Fasciitis with eosinophilia (FE), or Shulman syndrome, is a rare disease of unknown origin for which the nosological profile has not been clearly defined. It is clinically characterised by oedema and induration of the limbs with hypereosinophilia. It may be associated with morphea, in wh
• PMID 25288063

• Thrombotic thrombocytopenic purpura: 2012 American Society for Apheresis (ASFA) consensus conference on classification, diagnosis, management, and future research.

• Sarode R1, Bandarenko N, Brecher ME, Kiss JE, Marques MB, Szczepiorkowski ZM, Winters JL.
• Journal of clinical apheresis.J Clin Apher.2014 Jun;29(3):148-67. doi: 10.1002/jca.21302. Epub 2013 Oct 17.
• The American Society for Apheresis (ASFA) conducted a 1 day consensus conference on Thrombotic Thrombocytopenic Purpura (TTP) during its annual meeting in Atlanta, GA, on April 10, 2012. The authors of this article, a subcommittee of ASFA's Clinical Applications Committee, developed several question
• PMID 24136342

• Linear depressions and progressive tightening of the extremities.

• Mitchum M, Spillane E1, Meyerle J, Galeckas K.
• Cutis.Cutis.2013 Dec;92(6):E11-3.
• PMID 24416750

Japanese Journal

• Successful treatment of severe Shulman's syndrome by allogeneic bone marrow transplantation

• CETKOVSKY P
• Bone Marrow Transplant 21, 637-639, 1998
• NAID 30014038074

• Diffuse fasciitisの炎症病態に関する免疫組織化学的検討

• 高野 明美,本田 仁,犬飼 晃,高御堂 弘,高橋 昭
• 臨床神経学 35(5), 492-499, 1995-05-01
• NAID 10008312777

Related Links

• M725 好酸球性筋膜炎

M725 好酸球性筋膜炎 Eosinophilic Fasciitis, Shulman syndrome EF （検索用語句： Shulman症候群 ） 激しい運動や外傷を契機として急速に、皮膚の硬化と関節の運動制限 をきたす疾患で、病変部の好酸球浸潤又は末梢血好酸球増 ...

• Shulman's syndrome - RightDiagnosis.com - Right Diagnosis

Shulman's syndrome symptoms, causes, diagnosis, and treatment information for Shulman's syndrome (Eosinophilic fasciitis) with alternative diagnoses, full-text book chapters, misdiagnosis, research treatments, prevention, and ...

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★リンクテーブル★

リンク元	「好酸球性筋膜炎」「輸血後紫斑病」「シャルマン症候群」
関連記事	「syndrome」

「好酸球性筋膜炎」

　　[★]

英

eosinophilic fasciitis

同

シャルマン症候群 Shulman syndrome Shulman's syndrome

好酸球性びまん性筋膜炎 好酸球増加を伴うびまん性筋膜炎 diffuse fasciitis with eosinophilia、

関

全身性強皮症

概念

• 強皮症類似疾患
• 激しい運動、労作の後に数日以内に急激に発症
• 四肢に対称性有痛性腫脹　→　硬化(orange peel sign)
• 近位関節の運動制限と拘縮。
• 顔面に皮膚硬化が及ぶことはまれ
• レイノー現象を伴わない

病理

• 四肢の強皮症様の皮膚硬化
• 末梢血好酸球の増加
• 筋膜の著明な肥厚

検査

• 末梢血好酸球増加、高γグロブリン血症
• 自己抗体陰性

診断

• 血算、皮膚生検(筋膜、筋を含めた生検。筋膜肥厚、好酸球浸潤)

治療

• ステロイド良好が著効

「輸血後紫斑病」

　　[★]

英

posttransfusion purpura, post-transfusion purpura

同

シュルマン症候群 Shulman syndrome

関

輸血後合併症

• Sabiston Textbook of Surgery, 18th ed.
• Table 6-4 -- Categories and Management of Adverse Transfusion Reactions

Delayed (>24 Hours) Transfusion Reactions?Immunologic
TYPE	INCIDENCE	ETIOLOGY	MANIFESTATION	DIAGNOSTIC TESTING	THERAPEUTIC/PROPHYLACTIC APPROACH
Post-transfusion purpura	Rare	Recipient platelet antibodies (apparent alloantibody, usually anti? HPA-1) destroy autologous platelets	Thrombocytopenic purpura, bleeding 8-10 days after transfusion	Platelet antibody screen and identification	IGIV|HPA-1?negative platelets|Plasmapheresis

「シャルマン症候群」

　　[★]

英

Shulman syndrome

• 1. 輸血後紫斑病
• 2. 好酸球性筋膜炎 eosinophilic fasciitis

「syndrome」

　　[★]

• n.

• 症候群