カルバモイルリン酸合成酵素、カルバモイルリン酸シンターゼ
- 関
- carbamoyl-phosphate synthetase、carbamoyl-phosphate synthetase I
WordNet
- a salt of phosphoric acid (同)orthophosphate, inorganic_phosphate
- carbonated drink with fruit syrup and a little phosphoric acid
PrepTutorEJDIC
- 〈U〉リン酸塩 / 《複数形で》リン酸肥料
UpToDate Contents
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English Journal
- Purification of carbamoyl phosphate synthetase 1 (CPS1) from wood frog (Rana sylvatica) liver and its regulation in response to ice-nucleation and subsequent whole-body freezing.
- Green SR, Storey KB.
- Molecular and cellular biochemistry. 2019 May;455(1-2)29-39.
- Carbamoyl phosphate synthetase I (CPS1) represents an important regulatory enzyme of the urea cycle that mediates the ATP-driven reaction ligating ammonium, carbonate, and phosphate to form carbamoyl phosphate. The freeze-tolerant wood frog (Rana sylvatica or Lithobates sylvaticus) accumulates high
- PMID 30421312
- TMEM70 deficiency: Novel mutation and hypercitrullinemia during metabolic decompensation.
- Staretz-Chacham O, Wormser O, Manor E, Birk OS, Ferreira CR.
- American journal of medical genetics. Part A. 2019 Apr;().
- Respiratory chain disorders comprise a heterogeneous group of diseases that are the result of mutations in nuclear or mitochondrial genes. TMEM70 encodes a nuclear protein involved in the assembly of respiratory chain complex V. Although mutations in various genes can result in isolated complex V de
- PMID 30950220
- Overexpression of carbamoyl-phosphate synthase 1 significantly improves ureagenesis of human liver HepaRG cells only when cultured under shaking conditions.
- Adam AAA, van der Mark VA, Ruiter JPN, Wanders RJA, Oude Elferink RPJ, Chamuleau RAFM, Hoekstra R.
- Mitochondrion. 2019 Feb;().
- Hyperammonemia is an important contributing factor to hepatic encephalopathy in end-stage liver failure patients. Therefore reducing hyperammonemia is a requisite of bioartificial liver support (BAL). Ammonia elimination by human liver HepaRG cells occurs predominantly through reversible fixation in
- PMID 30802674
Japanese Journal
- バルプロ酸誘発高アンモニア血症に対するCPS1 4217C>A遺伝子多型の影響
- 八木 麻理子,NAKAMURA Tsutomu,OKIZUKA Yo,OYAZATO Yoshinobu,KAWASAKI Yoko,TSUNEISHI Shuichi,SAKAEDA Toshiyuki,MATSUO Masafumi,OKUMURA Katsuhiko,OKAMURA Noboru
- Pediatrics international : official journal of the Japan Pediatric Society 52(5), 744-748, 2010-10-01
- NAID 10028184232
- A case of carbamoyl phosphate synthetase 1 deficiency presenting symptoms at one month of age
- ONO Hiroaki,SUTO Tetsushi,KINOSHITA Yoshihisa,SAKANO Takashi,FURUE Takeki,OHTA Toshiyuki
- Brain & development 31(10), 779-781, 2009-11-01
- NAID 10026413113
Related Links
- Carbamoyl phosphate synthetase I deficiency is an inherited disorder that causes ammonia to accumulate in the blood (hyperammonemia). Ammonia, which is formed when proteins are broken down in the body, is toxic ...
- P31327 - CPSM_HUMAN Basket 0 (max 400 entries) x Your basket is currently empty. Select item(s) and click on "Add to basket" to create your own collection here (400 entries max) UniProtKB (0) UniRef (0) UniParc (0) Align ...
Related Pictures
★リンクテーブル★
[★]
- 英
- carbamoyl-phosphate synthetase、carbamoyl-phosphate synthase, carbamyl phosphate synthetase CPS
- 関
- カルバモイルリン酸シンテターゼ、カルバモイルリン酸合成酵素I、カルバモイルリン酸シンターゼ
[show details]
carbamylphosphate synthetase : 約 80,400 件
carbamoylphosphate synthetase : 約 16,200 件
carbamylphosphate synthetase : 30 件
carbamoylphosphate synthetase : 67 件
[★]
- 英
- carbamoyl-phosphate synthase
- 関
- カルバモイルリン酸合成酵素
[★]
グルタミン加水分解性カルバモイルリン酸合成酵素、グルタミン加水分解性カルバモイルリン酸シンターゼ
[★]
カルバモイルリン酸合成酵素I、カルバモイルリン酸シンターゼI
- 関
- carbamoyl-phosphate synthetase I
[★]
カルバモイルリン酸合成酵素I欠損症、カルバモイルリン酸シンターゼI欠損症
[★]
カルバモイルリン酸合成酵素II、カルバモイルリン酸シンターゼII
[★]
- 関
- inorganic phosphate、orthophosphate、orthophosphoric acid、phospho、phosphoester、phosphoric、phosphoric acid、phosphoric acid ester、phosphorus
[★]
- 関
- lyase、synthetase、transferase