WordNet
- (of meat) full of sinews; especially impossible to chew (同)sinewy, stringy, unchewable
- abnormal development (of organs or cells) or an abnormal structure resulting from such growth
PrepTutorEJDIC
- 繊維の,繊維状(質)の
Wikipedia preview
出典(authority):フリー百科事典『ウィキペディア（Wikipedia）』「2017/04/14 04:30:04」(JST)
[Wiki en表示]
| Polyostotic fibrous dysplasia |
| Synonyms |
Albright's disease[1]:578 |
| Classification and external resources |
| Specialty |
Osteology |
| ICD-10 |
Q78.1 |
| ICD-9-CM |
756.54 |
| DiseasesDB |
7880 |
| MeSH |
D005359 |
|
[edit on Wikidata]
|
Polyostotic fibrous dysplasia is a form of fibrous dysplasia affecting more than one bone.[2]
McCune-Albright syndrome includes polyostotic fibrous dysplasia as part of its presentation.[3]
One treatment that has been used is bisphosphonates.[4]
See also
- Fibrous dysplasia of bone
- List of radiographic findings associated with cutaneous conditions
References
- ^ James, William; Berger, Timothy; Elston, Dirk (2005). Andrews' Diseases of the Skin: Clinical Dermatology. (10th ed.). Saunders. ISBN 0-7216-2921-0.
- ^ "Fibrous Dysplasia: Overview - eMedicine Radiology". Retrieved 2009-02-23.
- ^ Lee, Peter A. (5 December 1986). "McCune-Albright Syndrome: Long-term Follow-up". JAMA: The Journal of the American Medical Association. 256 (21): 2980. doi:10.1001/jama.1986.03380210076028.
- ^ Khadilkar VV, Khadilkar AV, Maskati GB (September 2003). "Oral bisphosphonates in polyostotic fibrous dysplasia". Indian Pediatr. 40 (9): 894–6. PMID 14530553.
|
Bone and joint disease (M80–M94, 730–733)
|
|
| Bone |
| Inflammation |
| endocrine: |
|
|
| infection: |
- Osteomyelitis
- Sesamoiditis
- Brodie abscess
- Periostitis
- Vertebral osteomyelitis
|
|
|
| Metabolic |
- Bone density
- Osteoporosis
- Osteopenia
- Osteomalacia
- Paget's disease of bone
|
|
| Bone resorption |
- Osteolysis
- Hajdu-Cheney syndrome
- Ainhum
|
|
| Other |
- Ischaemia
- Avascular necrosis
- Osteonecrosis of the jaw
- Algoneurodystrophy
- Hypertrophic pulmonary osteoarthropathy
- Nonossifying fibroma
- Pseudarthrosis
- Stress fracture
- Fibrous dysplasia
- Skeletal fluorosis
- bone cyst
- Hyperostosis
- Infantile cortical hyperostosis
- Osteosclerosis
- Pycnodysostosis
|
|
|
| Joint |
|
|
| Combined |
| Osteochondritis |
- Osteochondritis dissecans
|
|
| Child |
| leg: |
- hip
- Legg–Calvé–Perthes syndrome
- tibia
- Osgood-Schlatter disease
- Blount's disease
- foot
- Köhler disease
- Sever's disease
|
|
| spine |
|
|
| arm: |
|
|
|
|
Osteochondrodysplasia (Q77–Q78, 756.4–756.5)
|
|
Osteodysplasia//
osteodystrophy |
| Diaphysis |
- Camurati–Engelmann disease
|
|
| Metaphysis |
- Metaphyseal dysplasia
- Jansen's metaphyseal chondrodysplasia
- Schmid metaphyseal chondrodysplasia
|
|
| Epiphysis |
- Spondyloepiphyseal dysplasia congenita
- Multiple epiphyseal dysplasia
- Otospondylomegaepiphyseal dysplasia
|
|
| Osteosclerosis |
- Raine syndrome
- Osteopoikilosis
- Osteopetrosis
|
|
| Other/ungrouped |
- FLNB
- Opsismodysplasia
- Polyostotic fibrous dysplasia
|
|
|
Chondrodysplasia/
chondrodystrophy
(including dwarfism) |
| Osteochondroma |
- osteochondromatosis
- Hereditary multiple exostoses
|
|
| Chondroma/enchondroma |
- enchondromatosis
- Ollier disease
- Maffucci syndrome
|
|
| Growth factor receptor |
| FGFR2: |
|
|
| FGFR3: |
- Achondroplasia
- Thanatophoric dysplasia
|
|
|
| COL2A1 collagen disease |
- Achondrogenesis
- Hypochondrogenesis
|
|
| SLC26A2 sulfation defect |
- Achondrogenesis
- Autosomal recessive multiple epiphyseal dysplasia
- Atelosteogenesis, type II
- Diastrophic dysplasia
|
|
| Chondrodysplasia punctata |
- Rhizomelic chondrodysplasia punctata
- Conradi–Hünermann syndrome
|
|
| Other dwarfism |
- Fibrochondrogenesis
- Short rib – polydactyly syndrome
- Majewski's polydactyly syndrome
- Léri–Weill dyschondrosteosis
|
|
UpToDate Contents
全文を閲覧するには購読必要です。 To read the full text you will need to subscribe.
English Journal
- Osteosarcoma of the Mandible Arising in Fibrous Dysplasia-A Case Report.
- Pack SE1, Al Share AA2, Quereshy FA3, Baur DA4.
- Journal of oral and maxillofacial surgery : official journal of the American Association of Oral and Maxillofacial Surgeons.J Oral Maxillofac Surg.2016 Nov;74(11):2229.e1-2229.e4. doi: 10.1016/j.joms.2016.06.174. Epub 2016 Jun 21.
- Fibrous dysplasia (FD) is a benign fibro-osseous lesion that typically behaves as a painless, slowly expanding tumor. On rare occasion, FD will undergo malignant transformation. When sarcomatous change occurs, osteosarcoma is the typical variant, followed by chondrosarcoma and fibrosarcoma. The inci
- PMID 27425882
- Malignant transformation of polyostotic fibrous dysplasia with aberrant keratin expression.
- Zreik RT1, Littrell LA2, Jin L3, Oliveira AM3, Fritchie KJ3.
- Human pathology.Hum Pathol.2016 Oct 19. pii: S0046-8177(16)30255-6. doi: 10.1016/j.humpath.2016.09.030. [Epub ahead of print]
- Malignant transformation of fibrous dysplasia (FD) is exceedingly rare, occurring in <1% of all FD cases, and has been described in both monostotic and polyostotic forms of this entity. We report a case of a large proximal femur mass arising in a 45-year-old man. The biopsy revealed a high-grade
- PMID 27771377
Japanese Journal
- 臨床室 特徴的な内反股変形から大腿骨転子下病的骨折にいたったMcCune-Albright症候群の1例
- 大腿骨近位部に発生した線維性骨異形成による病的骨折の治療
Related Links
- Polyostotic fibrous dysplasia (also known as "Albright's disease" :578) is a form of fibrous dysplasia affecting more than one bone. The McCune-Albright syndrome includes polyostotic fibrous dysplasia as part of its presentation. One treatment ...
Related Pictures
★リンクテーブル★
[★]
オールブライト症候群、オルブライト症候群、Albright症候群
- 関
- Albright syndrome、McCune-Albright syndrome、polyostotic fibrous dysplasia
[★]
- 英
- polyostotic fibrous dysplasia
- 同
- 多骨性線維性骨形成異常
- 関
- マッキューン・オルブライト症候群、オールブライト症候群
[★]
- 関
- fibrotic、filamentous