第一次硝子体過形成遺残 persistent hyperplastic primary vitreous
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出典(authority):フリー百科事典『ウィキペディア(Wikipedia)』「2013/05/09 18:34:29」(JST)
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Persistent hyperplastic primary vitreous |
Classification and external resources |
Falciform fold of detached dysplastic retina encircles the persistent hyaloid artery that extends from the optic nerve head to the retrolental mass. |
ICD-10 |
GroupMajor.minor |
ICD-9 |
xxx |
Persistent hyperplastic primary vitreous (PHPV) is a rare congenital developmental anomaly of the eye that results following failure of the embryological, primary vitreous and hyaloid vasculature to regress.[1] It can be present in three forms: purely anterior (persistent tunica vasculosa lentis and persistent posterior fetal fibrovascular sheath of the lens), purely posterior (falciform retinal septum and ablatio falcicormis congentia) and a combination of both.[1]
Contents
- 1 Causes/association of bilateral PHPV
- 2 Symptoms
- 3 See also
- 4 References
- 5 External links
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Causes/association of bilateral PHPV [edit]
- Trisomy 13 (Patau's syndrome)
- Norrie disease
- Walker Warburg syndrome
Symptoms [edit]
The primary vitreous used in formation of the eye during fetal development remains in the eye upon birth and is hazy and scarred.[2]
See also [edit]
- Persistent tunica vasculosa lentis
References [edit]
- ^ a b Silbert, Mira; Gunvood, Andrew S. (2000). "Clinical review, Persistent hyperplastic primary vitreous". Clinical Eye and Vision Care (Ireland: Elsevier Science Ireland Ltd.) 12 (3-4): 131–137. doi:10.1016/S0953-4431(00)00054-0. PMID 11137427. Retrieved 2009-05-11.
- ^ Young, Jane. "Persistent Hyperplastic Primary Vitreous". Retrieved 2009-05-11.
External links [edit]
- GeneReviews/NIH/NCBI/UW entry on NDP-Related Retinopathies
- Persistent Hyperplastic Primary Vitreous Involving the Anterior Eye report by Mauricio Castillo, David K. Wallace, and Suresh K. Mukherji
UpToDate Contents
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English Journal
- [Persistent Hyperplastic Primary Vitreous: case report and literature review.]
- Grenga R1, Komaiha C1, Bianchi G1, Carnevale C1, Andreoli C2, Gualdi G2.Author information 1Dipartimento Organi di Senso, UOC Oftalmologia B, Università Sapienza, Policlinico Umberto I, Roma, Italia.2Dipartimento di Scienze Radiologiche, Università Sapienza, Policlinico Umberto I, Roma, Italia.AbstractPersistent hyperplastic primary vitreous (PHPV) is a congenital developmental anomaly of the eye caused by the incomplete regression of primary vitreous with the abnormal persistence of hyaloid vasculature. Aim of this work is to report the case of unilateral PHPV in a 4-week-old child presented to our Department with microphtalmia and leukocoria in the right eye. We will describe the main ocular, echographic and magnetic resonance findings that are essential to conduct a right differential diagnosis.
- La Clinica terapeutica.Clin Ter.2013 Nov-Dec;164(6):e497-e503. doi: 10.7417/CT.2013.1644.
- Persistent hyperplastic primary vitreous (PHPV) is a congenital developmental anomaly of the eye caused by the incomplete regression of primary vitreous with the abnormal persistence of hyaloid vasculature. Aim of this work is to report the case of unilateral PHPV in a 4-week-old child presented to
- PMID 24424230
- Bilateral ocular anomalies in a South African fur seal (Arctocephalus pusillus pusillus).
- Colitz CM, Rudnick JC, Heegaard S.Author information All Animal Eye Care, Inc, Jupiter, FL, 33458, USA.AbstractA female South African fur seal (Arctocephalus pusillus pusillus) began having obvious clinical ophthalmologic problems by 8 weeks of age. The initial clinical sign was diffuse corneal edema, which progressed to bullae formation and ulcers; the underlying cause of corneal edema and bullous keratopathy was not identified antemortem. An ophthalmological evaluation was performed when the fur seal was approximately 6 months of age, but due to the diffuse corneal edema, intraocular structures could not be easily evaluated. An underlying infectious etiology was suspected; therefore, appropriate diagnostics were pursued, but did not identify a cause. Initial improvement was noted, but the fur seal then became blind and eventually became very painful. Due to decreased quality of life and aggressive behavior, the fur seal was euthanized. Histopathological diagnoses were persistent tunica vasculosa lentis and persistent hyperplastic primary vitreous with bilateral hypermature resorbed cataracts and retinal detachments with rosette formation.
- Veterinary ophthalmology.Vet Ophthalmol.2013 Oct 8. doi: 10.1111/vop.12100. [Epub ahead of print]
- A female South African fur seal (Arctocephalus pusillus pusillus) began having obvious clinical ophthalmologic problems by 8 weeks of age. The initial clinical sign was diffuse corneal edema, which progressed to bullae formation and ulcers; the underlying cause of corneal edema and bullous keratopa
- PMID 24283987
- Clinical characteristics and treatment of 22 eyes of morning glory syndrome associated with persistent hyperplastic primary vitreous.
- Fei P, Zhang Q, Li J, Zhao P.Author information Department of Ophthalmology, Xinhua Hospital, affiliated to Shanghai Jiaotong University School of Medicine, , Shanghai, China.AbstractPURPOSE: To describe the clinical manifestations and treatment outcomes in a retrospective case series of morning glory syndrome (MGS) associated with persistent hyperplastic primary vitreous (PHPV).
- The British journal of ophthalmology.Br J Ophthalmol.2013 Oct;97(10):1262-7. doi: 10.1136/bjophthalmol-2013-303565. Epub 2013 Jul 22.
- PURPOSE: To describe the clinical manifestations and treatment outcomes in a retrospective case series of morning glory syndrome (MGS) associated with persistent hyperplastic primary vitreous (PHPV).METHODS: The medical records of 85 eyes/74 patients referred for ophthalmology consultation diagnosed
- PMID 23878133
Japanese Journal
- 超音波検査により病態分類を試みた水晶体血管膜過形成遺残/第一次硝子体過形成遺残の犬の1例
- 金井 一享,堀 泰智,村田 佳瑛子,島村 俊介,星 史雄,伊藤 直之,樋口 誠一
- 日本獣医師会雑誌 = Journal of the Japan Veterinary Medical Association 62(9), 720-723, 2009-09-20
- NAID 10025576092
Related Links
- 無事に1ヶ月検診を終え、創太、恭平も新しい環境に慣れ始めほっとしていたころ、 いつものように友理をあやしていると、なんとなく友理の瞳の奥が光ることに気づいた。 「照明のあたり具合のせいかな。 太陽の光のせいかな。
- PHPV(第一次硝子体過形成遺残)は、Amebaグルっぽのコミュニティです。PHPVはネット上で見ても情報が少なくて戸惑ってしまいました・・・ 病状や程度もさまざまなこの病について色々情報交換などできたらいいな~って思います 入会された ...
Related Pictures
★リンクテーブル★
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- 英
- persistent hyperplastic primary vitreous PHPV
- 関
- 第1次硝子体過形成遺残、原発性硝子体過形成遺残
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- 英
- hypoplasia of the portal vein
- 関
- 原発性門脈低形成 primary hypoplasia of the portal vein PHPV
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第一次硝子体過形成遺残 PHPV
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参考
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肺高血圧症 pulmonary hypertension