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1. 肥大型心筋症：臨床症状、診断および評価hypertrophic cardiomyopathy clinical manifestations diagnosis and evaluation [show details]
…the majority of patients with HCM, LVH is not progressive, and HCM is compatible with normal longevity in the vast majority with a 1 percent annual mortality rate among non-referral based cohorts. A small …
2. 肥大型心筋症：左心室流出路閉塞の形態変異と病態生理hypertrophic cardiomyopathy morphologic variants and the pathophysiology of left ventricular outflow tract obstruction [show details]
…that apical HCM is particularly common in East Asian populations, having been reported to represent 41 percent of Chinese patients with HCM and 15 percent of Japanese patients with HCM . In non-Asian populations …
3. 肥大型心筋症：内科的治療hypertrophic cardiomyopathy medical therapy [show details]
…the majority of patients with HCM, LVH is not progressive, and HCM is compatible with normal longevity in the vast majority with a 1 percent annual mortality rate among non-referral based cohorts. A small …
4. 肥大型心筋症：自然経過および予後hypertrophic cardiomyopathy natural history and prognosis [show details]
… of the deaths (133 out of 149) were non-HCM related, with HCM-related mortality of only 0.6 percent per year . In addition, a substantial proportion of elderly HCM patients also had ≥1 conventional risk …
5. 小児の肥大型心筋症：マネージメントと予後hypertrophic cardiomyopathy in children management and prognosis [show details]
… of diuretics may be attempted only in non-obstructed HCM patients with persistent HF and evidence of volume overload. Digoxin – Digoxin is generally avoided in HCM given that the function is hyperdynamic …

English Journal

Heart failure in cardiomyopathies: a position paper from the Heart Failure Association of the European Society of Cardiology.

Seferović PM, Polovina M, Bauersachs J, Arad M, Gal TB, Lund LH, Felix SB, Arbustini E, Caforio ALP, Farmakis D, Filippatos GS, Gialafos E, Kanjuh V, Krljanac G, Limongelli G, Linhart A, Lyon AR, Maksimović R, Miličić D, Milinković I, Noutsias M, Oto A, Oto Ö, Pavlović SU, Piepoli MF, Ristić AD, Rosano GMC, Seggewiss H, Ašanin M, Seferović JP, Ruschitzka F, Čelutkiene J, Jaarsma T, Mueller C, Moura B, Hill L, Volterrani M, Lopatin Y, Metra M, Backs J, Mullens W, Chioncel O, de Boer RA, Anker S, Rapezzi C, Coats AJS, Tschöpe C.
European journal of heart failure. 2019 May;21(5)553-576.
Cardiomyopathies are a heterogeneous group of heart muscle diseases and an important cause of heart failure (HF). Current knowledge on incidence, pathophysiology and natural history of HF in cardiomyopathies is limited, and distinct features of their therapeutic responses have not been systematicall
PMID 30989768

Novel phenotype-genotype correlations of hypertrophic cardiomyopathy caused by mutation in α-actin and myosin-binding protein genes in three unrelated Chinese families.

Yang QL, Bian YY, Wang B, Zuo L, Zhou MY, Shao H, Zhang YM, Liu LW.
Journal of cardiology. 2019 May;73(5)438-444.
The correlations between genotype and phenotype in hypertrophic cardiomyopathy (HCM) have not been established. Mutation of α-actin gene (ACTC1) is a rare cause of HCM. This study aimed to explore novel genotype-phenotype correlations in HCM patients with the variants in ACTC1 and myosin-binding pr
PMID 30600190

Big heart, no longer a big problem: using catecholamine-based quantifications may be an effective means to prescribe exercise to non-obstructive hypertrophic cardiomyopathy patients.

Spector S, Debi R, Shin J.
The Journal of physiology. 2019 May;597(9)2329-2330.
PMID 30891752

Japanese Journal

Prognostic Impact of Left Atrial Minimal Volume on Clinical Outcome in Patients with Non-Obstructive Hypertrophic Cardiomyopathy

Shin Sung-Hee,Jang Ji-Hoon,Baek Yong-Soo,Kwon Sung-Woo,Park Sang-don,Woo Seong-Ill,Kim Dae-Hyeok,Kwan Jun
International Heart Journal 59(5), 991-995, 2018
… <p>Maximal left atrial volume (LAVmax) has been suggested to be an important indicator of left ventricular (LV) diastolic function and a prognosticator in patients with hypertrophic cardiomyopathy (HCM). …
NAID 130007490595

Prognostic Impact of Left Atrial Minimal Volume on Clinical Outcome in Patients with Non-Obstructive Hypertrophic Cardiomyopathy

Shin Sung-Hee,Jang Ji-Hoon,Baek Yong-Soo,Kwon Sung-Woo,Park Sang-don,Woo Seong-Ill,Kim Dae-Hyeok,Kwan Jun
International Heart Journal, 2018
… <p>Maximal left atrial volume (LAVmax) has been suggested to be an important indicator of left ventricular (LV) diastolic function and a prognosticator in patients with hypertrophic cardiomyopathy (HCM). …
NAID 130007471698

One of Six Patients with Non-Ischemic Heart Disease Exhibit Provoked Coronary Spasms: Non-Ischemic Heart Disease Associated with Ischemia?

Sueda Shozo,Miyoshi Toru,Sasaki Yasuhiro,Sakaue Tomoki,Habara Hirokazu,Kohno Hiroaki
Internal Medicine 54(3), 281-286, 2015
… The majority of cardiologists do not perform spasm provocation tests in patients with non-ischemic heart disease (non-IHD) or non-obstructive coronary artery disease (non-ob-CAD). …
NAID 130004903024