hemiconvulsion-hemiplegia-epilepsy syndrome

片側痙攣片麻痺てんかん症候群

WordNet

1. a pattern of symptoms indicative of some disease
2. a complex of concurrent things; "every word has a syndrome of meanings"
3. paralysis of one side of the body (同)unilateral paralysis
4. a disorder of the central nervous system characterized by loss of consciousness and convulsions

PrepTutorEJDIC

1. (疾患の徴候となる一群の)症徴候,症候群 / (事件・社会的状態などのパターンを示す)徴候形態
2. てんかん

UpToDate Contents

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• 1. 国際抗てんかん連盟（ILAE）によるてんかん発作およびてんかんの分類 ilae classification of seizures and epilepsy
• 2. 点頭てんかんのマネージメントおよび予後 management and prognosis of infantile spasms
• 3. 脳性麻痺の臨床的特徴 clinical features of cerebral palsy
• 4. 局在関連（部分）てんかん：原因および臨床的特徴 localization related partial epilepsy causes and clinical features
• 5. スタージウェーバー症候群 sturge weber syndrome

English Journal

• Survival following decompressive hemicraniectomy for hemiconvulsion-hemiplegia-epilepsy syndrome: case report.

• Beier AD1, Jannotta GE1, Sandler ED2, Abram HS3, Sheth RD3, Aldana PR1.
• Journal of neurosurgery. Pediatrics.J Neurosurg Pediatr.2016 Sep;18(3):344-9. doi: 10.3171/2016.3.PEDS15677. Epub 2016 May 13.
• Hemiconvulsion-hemiplegia-epilepsy (HHE) is an uncommon epileptic syndrome that affects young children. Typical management includes early initiation of benzodiazepines to abate the initial seizure activity quickly. Patients in whom epilepsy develops require prolonged use of antiepileptic agents. Her
• PMID 27176609

• Manifestations and characteristics of congenital adrenal hyperplasia-associated encephalopathy.

• Abe Y1, Sakai T2, Okumura A3, Akaboshi S4, Fukuda M5, Haginoya K6, Hamano S7, Hirano K8, Kikuchi K9, Kubota M10, Lee S11, Maegaki Y12, Sanefuji M13, Shimozato S14, Suzuki M15, Suzuki Y16, Takahashi M17, Watanabe K18, Mizuguchi M19, Yamanouchi H2.
• Brain & development.Brain Dev.2016 Aug;38(7):638-47. doi: 10.1016/j.braindev.2016.01.007. Epub 2016 Feb 15.
• BACKGROUND: This study aimed to clarify the characteristics of acute encephalopathic episodes in patients with congenital adrenal hyperplasia (CAH), which we termed "CAH-associated encephalopathy (CAHE)."METHODS: This retrospective study was conducted using a questionnaire as a nationwide survey of
• PMID 26898804

• Stroke-Like Presentation Following Febrile Seizure in a Patient with 1q43q44 Deletion Syndrome.

• Robinson JE1, Wolfe SM2, Kaiser-Rogers K3, Greenwood RS2.
• Frontiers in neurology.Front Neurol.2016 May 4;7:67. doi: 10.3389/fneur.2016.00067. eCollection 2016.
• Hemiconvulsion-hemiplegia-epilepsy syndrome (HHE) is a rare outcome of prolonged hemiconvulsion that is followed by diffuse unilateral hemispheric edema, hemiplegia, and ultimately hemiatrophy of the affected hemisphere and epilepsy. Here, we describe the case of a 3-year-old male with a 1;3 translo
• PMID 27199890

Japanese Journal

• Focal encephalopathy with recurrent episodes of epileptic status and cluster mimicking hemiconvulsion-hemiplegia-epilepsy syndrome

• MIYATA Rie,TANUMA Naoyuki,HAYASHI Masaharu,TAKAHASHI Yukitoshi
• Brain & development 34(5), 360-363, 2012-05-01
• NAID 10031050713

• Acute encephalopathy in two cases with severe congenital hydrocephalus

• TANOUE Koji,MATSUI Kiyoshi,OHSHIRO Akiko,YAMAMOTO Atsuko,HAYASHI Takuya,FUJIMOTO Junichi,OSAKA Hitoshi
• Brain & development 33(7), 616-619, 2011-08-01
• NAID 10031121964

• 臨床研究・症例報告 アデノウイルスが原因と考えられた急性小児片麻痺の1例

• 土井 政明,柴田 真理,新川 友子 [他]
• 小児科臨床 62(5), 947-952, 2009-05-00
• NAID 40016535444

Related Links

• Hemiconvulsion-Hemiplegia Epilepsy Syndrome | Epilepsy ...

Prevalence Negligible today because of improved emergency care for status epilepticus. 0.06% in the American Collaborative Perinatal Project. Age at onset 5 months to 4 years; peak at 6 months to 2 years. Sex Males = females.

• Hemiconvulsion-hemiplegia-epilepsy syndrome (HHE), the ...

Hemiconvulsion-hemiplegia-epilepsy syndrome is a neurological disorder, which presents itself as a febrile illness at the onset. Fevers and convulsions are only reduced/stopped via medications. The patient is left with a resulting ...

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★リンクテーブル★

リンク元	「片側痙攣片麻痺てんかん症候群」
関連記事	「hemiplegia」「epilepsy」「syndrome」

「片側痙攣片麻痺てんかん症候群」

　　[★]

英

hemiconvulsion-hemiplegia-epilepsy syndrome, HHE syndrome

関

急性小児片麻痺、急性小児片麻痺症候群

「hemiplegia」

　　[★] 片麻痺 =hemi + plegia

関

haemiparesis、haemiplegia、haemiplegic、hemiparesis、hemiplegic、infantile hemiplegia、monoplegia、spastic hemiplegia、transient hemiplegia

　

「epilepsy」

　　[★] てんかん epilepsy

関

てんかん発作 seizure

　 　

「syndrome」

　　[★]

• n.

• 症候群