WordNet

German conductor and composer of romantic operas (1786-1826) (同)Carl Maria von Weber, Baron Karl Maria Friedrich Ernst von Weber
German physiologist who studied sensory responses to stimuli and is considered the father of psychophysics (1795-1878) (同)E. H. Weber, Ernst Heinrich Weber
German sociologist and pioneer of the analytic method in sociology (1864-1920) (同)Max Weber
United States abstract painter (born in Russia) (1881-1961) (同)Max Weber
German physicist and brother of E. H. Weber; noted for his studies of terrestrial magnetism (1804-1891) (同)Wilhelm Eduard Weber
a pattern of symptoms indicative of some disease
a complex of concurrent things; "every word has a syndrome of meanings"
a unit of magnetic flux equal to 100,000,000 maxwells (同)Wb

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(疾患の徴候となる一群の)症徴候,症候群 / (事件・社会的状態などのパターンを示す)徴候形態

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1. スタージウェーバー症候群sturge weber syndrome [show details]
…lesion are identified when neurologic problems develop. SWS should be distinguished from Klippel-Trenaunay-Weber syndrome in which extensive capillary angiomata associated with dysplastic veins involve the …
2. 毛細血管奇形（ポートワイン母斑）とそれに関連する症候群capillary malformations port wine stains and associated syndromes [show details]
…until the end of puberty The diagnosis and management of Klippel-Trenaunay syndrome are discussed in detail separately. Parkes-Weber syndrome is characterized by a large capillary malformation on an …
3. 新生児における血管病変vascular lesions in the newborn [show details]
…named vessels; Vascular malformations associated with other anomalies, which include Sturge-Weber syndrome, Klippel-Trenaunay syndrome, macrocephaly-capillary malformation, Proteus syndrome, and congenital …
4. クリッペル・トレノネー・ウェーバー症候群：臨床症状、診断、マネージメントklippel trenaunay syndrome clinical manifestations diagnosis and management [show details]
… experts have used a variety of broad definitions for Klippel-Trenaunay syndrome (KTS). The term "Klippel-Trenaunay-Weber" was once used to describe… may be present Parkes Weber syndrome and KTS can be difficult to distinguish in younger patients. Clues to the diagnosis of Parkes Weber syndrome include brighter pink…
5. 食道輪および食道ウェブesophageal rings and webs [show details]
…known as the phrenic ampulla. Esophageal web – An esophageal web is a thin (<2 mm) eccentric membrane that protrudes into the esophageal lumen. Esophageal webs are covered with squamous epithelium and …

English Journal

A 17-year-old girl with Klippel-Weber syndrome complicated with a pulmonary thromboembolism and RV thrombus.

Yamada T, Ohba T, Yamamoto T, Kimata N, Inami T, Munakata R, Murakami D, Maruyama M, Takano M, Ibuki C, Hata N, Seino Y, Mizuno K.Author information Division of Cardiology, Nippon Medical School Chiba Hokusoh Hospital, Japan.AbstractA 17-year-old girl with multiple areas of skin hemangiomas that had been present since birth was referred to our institution complaining of sudden onset of dyspnea. Enhanced CT demonstrated a pulmonary thromboembolism and transthoracic echocardiogram showed a thrombus-like echo in the right ventricle. CT further revealed thrombi in the inferior vena cava (IVC) and peripheral vein. The thrombi, especially those in the RV, were highly life-threatening; therefore, immediate thrombectomy was performed and an IVC filter was placed. Because no major complications occurred, the patient was discharged 34 days after admission. In such young women, carefully using anticoagulation therapy and planning pregnancy are recommended.
Internal medicine (Tokyo, Japan).Intern Med.2013;52(12):1337-40.
A 17-year-old girl with multiple areas of skin hemangiomas that had been present since birth was referred to our institution complaining of sudden onset of dyspnea. Enhanced CT demonstrated a pulmonary thromboembolism and transthoracic echocardiogram showed a thrombus-like echo in the right ventricl
PMID 23774543

Re: Giant multilevel thoracic hemangioma with spinal cord compression in a patient with Klippel-Weber-Trenaunay syndrome: case report.

López-Gutiérrez JC, Perez-Grueso FJ.
Spine.Spine (Phila Pa 1976).2009 Dec 1;34(25):2834. doi: 10.1097/BRS.0b013e3181c092af.
PMID 19940743

Giant multilevel thoracic hemangioma with spinal cord compression in a patient with Klippel-Weber-Trenaunay syndrome: case report.

Grau SJ, Holtmannspoetter M, Seelos K, Tonn JC, Siefert A.Author information Department of Neursurgery, Klinikum Grosshadern, Ludwig-Maximilian-University Munich, Germany. Stefan.grau@med.uni-muenchen.deAbstractSTUDY DESIGN: Case report and clinical discussion.
Spine.Spine (Phila Pa 1976).2009 Jun 15;34(14):E498-500. doi: 10.1097/BRS.0b013e3181a4e4b8.
STUDY DESIGN: Case report and clinical discussion.OBJECTIVE: We intend to report a very rare case of a giant spinal hemangioma causing myelopathy.SUMMARY OF BACKGROUND DATA: Multilevel symptomatic spinal hemangiomas causing acute neurologic symptoms are rare disorders. We found only sporadic reports
PMID 19525830

Japanese Journal

A 17-year-old Girl with Klippel-Weber Syndrome Complicated with a Pulmonary Thromboembolism and RV Thrombus

Yamada Toshimasa,Ohba Takayoshi,Yamamoto Teppei,Kimata Nakahisa,Inami Toru,Munakata Ryo,Murakami Daisuke,Maruyama Mitsunori,Takano Masamichi,Ibuki Chikao,Hata Noritake,Seino Yoshihiko,Mizuno Kyoichi
Internal Medicine 52(12), 1337-1340, 2013
A 17-year-old girl with multiple areas of skin hemangiomas that had been present since birth was referred to our institution complaining of sudden onset of dyspnea. Enhanced CT demonstrated a pulmonar …
NAID 130003365672

Klippel-Weber 症候群に合併した先天性下大静脈欠損症の1例

城島久美子,小池洋介,新見正則
日本外科系連合学会誌 36(5), 884-890, 2011-10-30
NAID 10030231816

Klippel-Weber syndrome による下肢片側過成長に対して健肢の脚延長を行った1例

高田宗知,土屋弘行,松原秀憲,富田勝郎
日本創外固定・骨延長学会雑誌 = The journal of the Japanese Association of External Fixation and Limb Lengthening 21, 157, 2010-01-13
NAID 10027253071

「クリッペル・ウェーバー症候群」

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英: Klippel-Weber syndrome
同: クリッペル・トレノーニイ症候群 Klippel-Trenaunay syndrome、クリッペル・トレノーニイ・ウェーバー症候群クリッペル-トレノネー-ウェーバー症候群 Klippel-Trenaunay-Weber syndrome KTWS、骨肥大性動静脈瘤性母斑、血管拡張性肥大症 hemangiectatic hypertrophy 血管骨過形成症候群 angio-osteohypertrophy syndrome

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クリッペル・トレノネー症候群 : 18 件
クリッペル・トレノーネイ症候群 : 15 件
クリッペル・トレノーニイ症候群 : 6 件
クリッペル・ウェーバー症候群 : 95 件
クリッペル-トレノネー-ウェーバー症候群 : 16 件
Klippel-Trenaunay-Weber syndrome : 約 25,100 件
Klippel-Trenaunay syndrome : 約 20,100 件
Klippel-Weber syndrome : 61 件