同: FHLH

WordNet

relating to or having the characteristics of a family; "children of the same familial background"; "familial aggregation"
occurring among members of a family usually by heredity; "an inherited disease"; "familial traits"; "genetically transmitted features" (同)genetic, hereditary, inherited, transmitted, transmissible

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家族の,家族特有の / 違伝的な,血統にあらわれる

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1. 血球貪食リンパ組織球の臨床的特徴および診断 clinical features and diagnosis of hemophagocytic lymphohistiocytosis
2. 血球貪食性リンパ組織球症（HLH）の治療および予後 treatment and prognosis of hemophagocytic lymphohistiocytosis
3. 成人スティル病の臨床症状および診断 clinical manifestations and diagnosis of adult stills disease
4. 全身型若年性特発性関節炎：経過、予後、および合併症 systemic juvenile idiopathic arthritis course prognosis and complications
5. 川崎病：合併症 kawasaki disease complications

English Journal

Haploidentical hematopoietic stem cell transplantation for adult patients with Epstein-Barr virus-associated hemophagocytic lymphohistiocytosis.

Li Z1, Wang Y1, Wang J1, Zhang J1, Wang Z1.
Leukemia & lymphoma.Leuk Lymphoma.2018 Jan;59(1):77-84. doi: 10.1080/10428194.2017.1330467. Epub 2017 Jun 2.
PMID 28573910

Comparing hemophagocytic lymphohistiocytosis in pediatric and adult patients.

Wysocki CA1.
Current opinion in allergy and clinical immunology.Curr Opin Allergy Clin Immunol.2017 Dec;17(6):405-413. doi: 10.1097/ACI.0000000000000405.
PMID 28957822

Uterine intravascular lymphoma as a cause of fever of unknown origin.

Hadjadj J1, Nielly H2, Piekarski E3, Cuccuini W4, Deau-Fischer B5, Hourseau M6, Benali K3, Fieschi C1, Aletti M2, Papo T7, Oksenhendler E1, Galicier L1, Boutboul D8.
Annals of hematology.Ann Hematol.2017 Nov;96(11):1891-1896. doi: 10.1007/s00277-017-3117-4. Epub 2017 Aug 29.
PMID 28852831

Japanese Journal

Successful engraftment of unrelated cord blood stem cells for familial erythrophagocytic lymphohistiocytosis

TANAKA Y.
Bone Marrow Transplant 22, 511-513, 1998
NAID 30014040077

Treatment of familial erythrophagocytic lymphohistiocytosis with cyclosporine A.

ABELLA EM
J Pediatr. 130, 467-470, 1997
NAID 30017439475

血球貪食症候群の臨床的検討 : 血清サイトカイン値と臨床病期分類の有用性について

石田也寸志,檜垣晶,横田佳子,田内久道
日本小児血液学会雑誌 9(1), 31-36, 1995-02-28
NAID 10012225517

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血球貪食症候群 - Wikipedia

家族性血球貪食症候群（familial hemophagocytic lymphohistiocytosis; FHL）. 常染色体劣性遺伝による。血球貪食症候群を唯一の表現型として発症する。Perforin、 syntaxin11、Munc13-4、Munc18-2などが原因遺伝子として報告されているが、遺伝子が ...