好酸球性筋膜炎
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- 1. 好酸球性筋膜炎eosinophilic fasciitis [show details]
… Eosinophilic fasciitis (EF, also called Shulman syndrome) is an uncommon disorder of unknown etiology and poorly understood pathogenesis . EF is characterized in its early phase by limb or trunk erythema …
- 2. 好酸球の生物学および好酸球増多症の原因eosinophil biology and causes of eosinophilia [show details]
…cetirizine , radiotherapy , topical tacrolimus , and thalidomide . Eosinophilic fasciitis – Eosinophilic fasciitis, also known as Shulman syndrome, is characterized by symmetrical induration of the skin. The …
- 3. 学会が公開する診療ガイドラインのリンク:好酸球性筋膜炎society guideline links eosinophilic fasciitis [show details]
…Dermatology Society (PCDS): Clinical guidance on eosinophilic fasciitis (2015) Diagnostic criteria, severity classification and guidelines of eosinophilic fasciitis (2018)…
- 4. 成人における限局性強皮症の病因、臨床症状、および診断pathogenesis clinical manifestations and diagnosis of morphea localized scleroderma in adults [show details]
…represent the atrophic stage of plaque-type morphea, or may be a separate disorder. Eosinophilic fasciitis, or Shulman syndrome, is a disorder that is characterized by the rapid onset of symmetric, painful, …
- 5. 悪性腫瘍およびリウマチ性疾患malignancy and rheumatic disorders [show details]
…cancer, other testing such as further imaging or checking tumor markers may be performed. Eosinophilic fasciitis (EF) is an uncommon condition, typically characterized by woody induration, which most often …
English Journal
- Eosinophilic fasciitis: From pathophysiology to treatment.
- , I I, H H, H H, .
- Allergology international : official journal of the Japanese Society of Allergology. 2019 Mar;().
- Eosinophilic fasciitis is a disease originally proposed as "diffuse fasciitis with eosinophilia" by Shulman in 1974. The patients with this disease often have history of strenuous exercise or labor a few days to 1-2 weeks before the onset. The chief symptoms are symmetrical, full-circumference swell
- PMID 30910631
- Morphoea profunda and its relationship to eosinophilic fasciitis.
- Wlodek C, Korendowych E, McHugh N, Lovell CR.
- Clinical and experimental dermatology. 2018 Apr;43(3)306-310.
- In this small case series, all eight patients were women in their fifth and sixth decades. This is similar to the female predominance in morphoea and less in keeping with eosinophilic fasciitis (EF). All cases had diffuse induration of their limbs with both proximal and distal patterns of distributi
- PMID 29277925
- FOSB is a Useful Diagnostic Marker for Pseudomyogenic Hemangioendothelioma.
- Hung YP, Fletcher CD, Hornick JL.
- The American journal of surgical pathology. 2017 May;41(5)596-606.
- Pseudomyogenic (epithelioid sarcoma-like) hemangioendothelioma is a distinctive vascular neoplasm of intermediate biological potential with a predilection for young adults and frequent multifocal presentation. Pseudomyogenic hemangioendothelioma is characterized by loose fascicles of plump spindled
- PMID 28009608
Japanese Journal
- Fasciitis in Mixed Connective Tissue Disease Successfully Treated with High-dose Intravenous Immunoglobulin
- MATSUDA Masayuki,MIKI Jun,OGUCHI Kenya,TABATA Kenichi,IKEDA Shu-ichi
- Internal medicine 42(9), 910-911, 2003-09-01
- NAID 130000766898
- 坂尾 佳久,浦野 芳夫,滝脇 弘嗣,内田 尚之,荒瀬 誠治,武田 己広
- 西日本皮膚科 = The Nishinihon journal of dermatology 60(1), 6-10, 1998-02-01
- 65歳の男性。重い荷物の運搬後, 四肢に瀰漫性の皮膚硬化が生じ, 次第に躯幹にも拡大し, 硬化部にほぼ一致して紅斑, 鱗屑が出現した。四肢末梢には異常なく, レイノー現象, 内臓病変もなかった。末梢血好酸球増多, 赤沈亢進, 高<I>γ</I>グロブリン血症, 病理組織学的にリンパ球の浸潤をともなう筋膜の肥厚が認められた。以上の所見より好酸球性筋膜炎と診断した。 …
- NAID 10019106157
- Diffuse fasciitisの1例とそのMRI所見
Related Links
- 1. Trans Assoc Am Physicians. 1975;88:70-86. Diffuse fasciitis with eosinophilia: a new syndrome? Shulman LE. PMID: 1224441 [PubMed - indexed for MEDLINE] Publication Types: Case Reports MeSH Terms Adolescent
- Eosinophilic Fasciitis (Shulman Disease, Diffuse Fasciitis with Eosinophilia) Are You Confident of the Diagnosis? What you should be alert for in the history Patients with eosinophilic fasciitis (EF) typically give a history of progressive ...
- Eosinophilic fasciitis is sometimes confused with eosinophilia-myalgia syndrome and scleroderma. ... Eosinophilic fasciitis causes inflammation of the tissues beneath the skin as well as sometimes in the skin. This leads topain ...
★リンクテーブル★
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- 英
- eosinophilic fasciitis
- 同
- シャルマン症候群 Shulman syndrome Shulman's syndrome
- 好酸球性びまん性筋膜炎 好酸球増加を伴うびまん性筋膜炎 diffuse fasciitis with eosinophilia、
- 関
- 全身性強皮症
概念
- 強皮症類似疾患
- 激しい運動、労作の後に数日以内に急激に発症
- 四肢に対称性有痛性腫脹 → 硬化(orange peel sign)
- 近位関節の運動制限と拘縮。
- 顔面に皮膚硬化が及ぶことはまれ
- レイノー現象を伴わない
病理
- 四肢の強皮症様の皮膚硬化
- 末梢血好酸球の増加
- 筋膜の著明な肥厚
検査
- 末梢血好酸球増加、高γグロブリン血症
- 自己抗体陰性
診断
- 血算、皮膚生検(筋膜、筋を含めた生検。筋膜肥厚、好酸球浸潤)
治療
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- 関
- diffusely、diffusion、diffusional、diffusive、disseminated、pervasive、spread、widespread