paraneoplastic opsoclonus-myoclonus ataxia

出典: meddic

傍腫瘍性眼球クローヌス・ミオクローヌス運動失調

opsoclonus myoclonus ataxiaopsoclonus-myoclonus syndromePOMA

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英文文献

  • Acute Cerebellar Ataxia, Acute Cerebellitis, and Opsoclonus-Myoclonus Syndrome.
  • Desai J, Mitchell WG.AbstractAcute cerebellar ataxia and acute cerebellitis represent a process characterized by parainfectious, postinfectious, or postvaccination cerebellar inflammation. There is considerable overlap between these entities. The mildest cases of acute cerebellar ataxia represent a benign condition that is characterized by acute truncal and gait ataxia, variably with appendicular ataxia, nystagmus, dysarthria, and hypotonia. It occurs mostly in young children, presents abruptly, and recovers over weeks. Neuroimaging is normal. Severe cases of cerebellitis represent the other end of the spectrum, presenting with acute cerebellar signs often overshadowed by alteration of consciousness, focal neurological deficits, raised intracranial pressure, hydrocephalus, and even herniation. Neuroimaging is abnormal and the prognosis is less favorable than in acute cerebellar ataxia. Acute disseminated encephalomyelitis may be confused with acute cerebellitis when the clinical findings are predominantly cerebellar, but lesions on neuroimaging are usually widespread. Paraneoplastic opsoclonus-myoclonus syndrome is often initially misdiagnosed as acute cerebellar ataxia, but has very specific features, course, and etiopathogensis.
  • Journal of child neurology.J Child Neurol.2012 Jul 17. [Epub ahead of print]
  • Acute cerebellar ataxia and acute cerebellitis represent a process characterized by parainfectious, postinfectious, or postvaccination cerebellar inflammation. There is considerable overlap between these entities. The mildest cases of acute cerebellar ataxia represent a benign condition that is char
  • PMID 22805251
  • Whole-body magnetic resonance imaging in a patient with an occult abdominal neuroblastoma and opsoclonus-myoclonus syndrome.
  • Miras Azcón F, Culiañez Casas M, Pastor Pons E.SourceServicio de Radiodiagnóstico, Hospital Universitario Virgen de las Nieves, Granada, España.
  • Radiologia.Radiologia.2012 Jul 17. [Epub ahead of print]
  • Opsoclonus-myoclonus syndrome is a rare neurological disorder. In children, the etiology varies, although it is a paraneoplastic manifestation (mainly of neuroblastoma) in 40% to 80% of cases. Whole-body MRI promises to be a powerful tool in the search for a possible primary tumor in this condition
  • PMID 22818898

和文文献

  • めまいで発症した傍腫瘍性オプソクローヌス・ミオクローヌス症候群
  • 坂 直樹,瀬尾 徹,島野 宏一,樫葉 恵子,阪上 雅史
  • 耳鼻咽喉科臨床 102(7), 523-526, 2009-07-01
  • … A case of paraneoplastic opsoclonus-myoclonus syndrome with an onset of vertigo is reported. … Since neurological examination showed opsoclonus of the eye movement, ataxia and adiadochokinesis, disequilibrium due to a central nervous system disorder was strongly suggested. …
  • NAID 10025096557
  • Opsoclonus-myoclonus-ataxiaを契機に発見された神経芽腫の1例
  • 三宅 岳,浜田 吉則,渡邉 健太郎,棚野 晃秀,徳原 克治,高田 晃平,上山 泰男,中野 崇秀
  • 日本小児外科学会雑誌 42(1), 28-34, 2006-02-20
  • Opsoclonus-myoclonus-ataxia (OMA)症候群が発見の契機となった神経芽腫の1例を経験したので報告する.症例は2歳0カ月の女児.約4カ月前からの起立時, 歩行時のふらつき, 上肢の振戦のため近医を受診し, 腹部腫瘍を指摘され当院に紹介された.尿中HVA, 尿中VMA, 血清NSEは高値を示し, 腹部超音波, CT, MRIにて径約4cmの右副腎腫瘍を認めた.全身骨シンチ, MIBGシンチ, 骨髄生検の結果遠隔転移は認め …
  • NAID 110004078411

関連リンク

Other names for OMS include: Opsoclonus-Myoclonus-Ataxia (OMA); Paraneoplastic Opsoclonus-Myoclonus Ataxia (POMA); Kinsbourne syndrome; Myoclonic Encephalopathy of Infants; Dancing Eyes-Dancing Feet syndrome; Dancing Eyes ...
15 Sep 2009 ... Opsoclonus is usually associated with myoclonus of the limbs and trunk, and sometimes encephalopathy; these symptoms cannot be clinically differentiated from those caused by non-paraneoplastic etiologies. Ataxia ...

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★リンクテーブル★
リンク元傍腫瘍性眼球クローヌス・ミオクローヌス運動失調」「opsoclonus myoclonus ataxia」「opsoclonus-myoclonus syndrome」「POMA
関連記事ataxia」「myoclonus」「paraneoplastic

傍腫瘍性眼球クローヌス・ミオクローヌス運動失調」

  [★]

paraneoplastic opsoclonus-myoclonus ataxiaPOMA
眼球クローヌス・ミオクローヌス症候群眼球クローヌス・ミオクローヌス運動失調

opsoclonus myoclonus ataxia」

  [★]

眼球クローヌス・ミオクローヌス運動失調

opsoclonus-myoclonus syndromeparaneoplastic opsoclonus-myoclonus ataxia


opsoclonus-myoclonus syndrome」

  [★]

眼球クローヌス・ミオクローヌス症候群

opsoclonus myoclonus ataxiaparaneoplastic opsoclonus-myoclonus ataxia


POMA」

  [★]

傍腫瘍性眼球クローヌス・ミオクローヌス運動失調

paraneoplastic opsoclonus-myoclonus ataxia

ataxia」

  [★] 運動失調

WordNet   license wordnet

「inability to coordinate voluntary muscle movements; unsteady movements and staggering gait」
ataxy, dyssynergia, motor ataxia

myoclonus」

  [★] ミオクローヌス

WordNet   license wordnet

「a clonic spasm of a muscle or muscle group」


paraneoplastic」

  [★]

  • adj.
  • 腫瘍随伴の、傍腫瘍性の、傍腫瘍の




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