nephrogenic fibrosing syndrome

出典: meddic

  • nephrogenic fibrosing dermatopathyと同義?
  • 全身性強皮症の鑑別疾患としてあげられる。


  • Harrison's Principles
Table 316-1 Conditions Associated with Scleroderma-Like Induration
  • Nephrogenic systemic fibrosis: a review of the new conundrum.
Goenka AH, Das CJ, Sharma R.
Nephrogenic systemic fibrosis is an idiopathic, sclerosing condition that occurs only in patients who have impaired renal function. Although its most conspicuous manifestation is in the skin, the condition involves multiple organ systems and is potentially fatal. Its postulated association with gadolinium-based magnetic resonance contrast agents has attracted attention. The distinctive clinical features of this entity include a prodromal systemic inflammatory syndrome followed by a chronic course of fibrosis that has a predilection for the skin and subcutaneous tissues of the extremities. The progressive systemic fibrosing process involves multiple organs and contributes to the morbidity and the increased mortality. Appropriate preventive action, prompt recognition and timely reporting of cases may enable better management of this condition.
PMID 20384019

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  • Morphological clues in the diagnosis of sclerodermiform dermatitis.
  • Fernandez-Flores A1, Gatica-Torres M, Ruelas-Villavicencio AL, Saeb-Lima M.
  • The American Journal of dermatopathology.Am J Dermatopathol.2014 Jun;36(6):449-64. doi: 10.1097/DAD.0000000000000049.
  • In this report, we review 5 sclerodermiform cutaneous conditions: eosinophilic fasciitis, systemic nephrogenic fibrosis, scleredema, scleromyxedema, and toxic oil syndrome. We emphasize the morphological differences between the conditions and some morphological clues that are important to differenti
  • PMID 24423930
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  • A 56-year-old woman with hypertension-induced end stage renal disease presented with skin thickening and mottled discoloration. Cutaneous biopsy showed increased dermal fibroblasts embedded in fibromyxoid stroma with scattered perivascular and interstitial mononuclear cells. Immunohistochemistry rev
  • PMID 24809889
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  • Identification of serious adverse drug reactions (sADRS) associated with commonly used drugs can elude detection for years. Reye's syndrome (RS), nephrogenic systemic fibrosis (NSF), and pure red cell aplasia (PRCA) among chronic kidney disease (CKD) patients were recognized in 1951, 2000, and 1998,
  • PMID 22692632


Nephrogenic Fibrosing Dermopathy: Legs Description: This patient with end-stage renal disease has shiny, discolored skin of the lower legs with brawny induration. ...
Abstract: Nephrogenic fibrosing dermopathy (NFD) is a disorder characterized by dramatic thickening and hardening of skin in the extremities and trunk, which occurs in individuals on dialysis for renal disease. The pathophysiology is ...
... nephrogenic fibrosing dermopathy gadolinium systemic sclerosis fibrosing syndrome raynaud's Photo Details Title: Nephrogenic Fibrosing Dermopathy: Thigh Description: MRI from a 52-year-old woman shows the thickened ...


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  • n.

WordNet   license wordnet

「a pattern of symptoms indicative of some disease」

WordNet   license wordnet

「a complex of concurrent things; "every word has a syndrome of meanings"」

PrepTutorEJDIC   license prepejdic

「(疾患の徴候となる一群の)症徴候,症候群 / (事件・社会的状態などのパターンを示す)徴候形態」



  • adj.
  • 腎発生の、腎形成の