WordNet
- an abnormal condition in which a normal opening or tube in the body (as the urethra) is closed or absent
Wikipedia preview
出典(authority):フリー百科事典『ウィキペディア（Wikipedia）』「2014/07/23 10:55:10」(JST)
[Wiki en表示]
| Intestinal atresia |
| Classification and external resources |
| ICD-10 |
Q41, Q42 |
| ICD-9 |
751.1 751.2 |
| OMIM |
223400 243600 |
| DiseasesDB |
31514 33000 |
Intestinal atresia is a malformation where there is a narrowing or absence of a portion of the intestine. This defect can either occur in the small or large intestine.
Contents
- 1 Types of intestinal atresia
- 2 Cause
- 3 Diagnosis
- 4 Treatment
- 5 See also
- 6 References
- 7 External links
Types of intestinal atresia
The different types of intestinal atresia are named after their location:
- Duodenal atresia - malformation of the duodenum, part of the intestine that empties from the stomach
- Jejunal atresia - malformation of the jejunum, the second part of the intestine extending from the duodenum to the ileum
- Ileal atresia - malformation of the ileum, the lower part of the small intestine
- Colon atresia - malformation of the colon
Duodenal atresia has a strong association with Down syndrome.[1] It is the most common type, followed by ileal atresia.
Cause
The most common cause of non-duodenal intestinal atresia is a vascular accident in utero that leads to decreased intestinal perfusion and ischemia of the respective segment of bowel. This leads to narrowing, or in the most severe cases, complete obliteration of the intestinal lumen.
In the case that the superior mesenteric artery, or another major intestinal artery, is occluded, large segments of bowel can be entirely underdeveloped. Classically, the affected area of bowel assumes a spiral configuration and is described to have an "apple peel" like appearance; this is accompanied by lack of a dorsal mesentery. Ileal atresia can also result as a complication of meconium ileus.
Diagnosis
Intestinal atresias are often discovered before birth: either during a routine sonogram which shows a dilated intestinal segment due to the blockage, or by the development of polyhydramnios (the build up of too much amniotic fluid in the uterus). These abnormalities are indications that the fetus may have a bowel obstruction which a more detailed ultrasound study can confirm.
Some fetuses with bowel obstruction have abnormal chromosomes. An amniocentesis is recommended because it can determine not only the sex of the baby, but whether or not there is a problem with the chromosomes.
Treatment
Fetal and neonatal intestinal atresia are treated using laparotomy after birth. If the area affected is small, the surgeon may be able to remove the damaged portion and join the intestine back together. In instances where the narrowing is longer, or the area is damaged and cannot be used for period of time, a temporary Stoma (medicine) may be placed.
See also
- Bowel obstruction
- Ileus
- Atresia
- Pediatric surgery
References
- ^ Le, Tao (2013). First Aid for the USMLE STEP. New York: Mc Graw Hill. p. 308. ISBN 978-0-07-180232-1.
External links
- UCSF Fetal Treatment Center: Bowel Obstructions
- Information about congenital malformations of the gastrointestinal tract in premature babies - The Hospital for Sick Children
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Congenital malformations and deformations of digestive system (Q35–Q45, 749–751)
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| Upper GI tract |
| Tongue, mouth and pharynx |
- Cleft lip and palate
- Van der Woude syndrome
- tongue
- Ankyloglossia
- Macroglossia
- Hypoglossia
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| Esophagus |
- EA/TEF
- Esophageal atresia: types A, B, C, and D
- Tracheoesophageal fistula: types B, C, D and E
- esophageal rings
- Esophageal web (upper)
- Schatzki ring (lower)
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| Stomach |
- Pyloric stenosis
- Hiatus hernia
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| Lower GI tract |
| Intestines |
- Intestinal atresia
- Meckel's diverticulum
- Hirschsprung's disease
- Intestinal malrotation
- Dolichocolon
- Enteric duplication cyst
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| Rectum/anal canal |
- Imperforate anus
- Vestibular fistula
- Persistent cloaca
- Rectal atresia
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| Accessory |
| Pancreas |
- Annular pancreas
- Accessory pancreas
- Johanson–Blizzard syndrome
- Pancreas divisum
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| Bile duct |
- Choledochal cysts
- Biliary atresia
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| Liver |
- Alagille syndrome
- Polycystic liver disease
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noco/cofa (c)/cogi/tumr, sysi
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anat (t, g, p)/phys/devp/enzy
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noco/cong/tumr, sysi/epon
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proc, drug (A2A/2B/3/4/5/6/7/14/16), blte
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UpToDate Contents
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English Journal
- Roux-en-Y hepatico-jejunostomy for a left segmental graft: Do not twist the loop, stick it!
- Nadalin S1, Monti L, Grimaldi C, di Francesco F, Tozzi AE, de Ville de Goyet J.
- Pediatric transplantation.Pediatr Transplant.2015 Jun;19(4):358-65. doi: 10.1111/petr.12474. Epub 2015 Apr 16.
- Biliary complications remain a major challenge for long-term success after LT, as it is, as a rule, the most common technical - early and late - complication that occurs, and because these complications contribute to a significant number of late graft losses and retransplantations. In the pediatric
- PMID 25879299
- Belgian multicenter experience with intestinal transplantation.
- Ceulemans LJ1, Monbaliu D1, De Roover A2, Detry O2, Troisi RI3, Rogiers X3, Raymond R4, Lerut JP4, Ysebaert D5, Chapelle T5, Pirenne J1.
- Transplant international : official journal of the European Society for Organ Transplantation.Transpl Int.2015 May 30. doi: 10.1111/tri.12615. [Epub ahead of print]
- Intestinal transplantation (ITx) has evolved from an experimental procedure towards a clinical reality but remains a challenging procedure. The aim of this survey was to analyze the multicenter Belgian ITx-experience. From 1999-2014, 24 ITx in 23 patients were performed in Belgium, divided over 5 ce
- PMID 26033472
Japanese Journal
- Apple-peel 型小腸閉鎖に空腸・回腸捻転壊死を合併した1 例
- 胎児上部消化管閉鎖症における羊水中膵酵素濃度の解析
Related Links
- Important It is possible that the main title of the report Jejunal Atresia is not the name you expected. Please check the synonyms listing to find the alternate name(s) and disorder subdivision(s) covered by this report. ...
- Jejunal atresia is a birth defect that occurs when the membrane that attaches the small intestines to the abdominal wall (called the mesentery) is partially or completely absent. As a result, a portion of the small ...
★リンクテーブル★
[★]
- 英
- jejunal atresia, jejunal occlusion
[★]
- (ギリシャ語 trēsis(perforation))
[★]
- 関
- jejuni、jejunum