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Taussig–Bing syndrome
Specialty
Cardiac surgery
Taussig–Bing syndrome is a cyanotic congenital heart defect[1] in which the patient has both double outlet right ventricle (DORV) and subpulmonic ventricular septal defect (VSD).[2]
In DORV, instead of the normal situation where blood from the left ventricle (LV) flows out to the aorta and blood from the right ventricle (RV) flows out to the pulmonary artery, both aorta and pulmonary artery are connected to the RV, and the only path for blood from the LV is across the VSD. When the VSD is subpulmonic (sitting just below the pulmonary artery), the LV blood then flows preferentially to the pulmonary artery. Then the RV blood, by default, flows mainly to the aorta.
The clinical manifestations of a Taussig-Bing anomaly, therefore, are much like those of dextro-Transposition of the great arteries (but the surgical repair is different). It can be corrected surgically also with the arterial switch operation (ASO).
It is managed with Rastelli procedure. It is named after Helen B. Taussig and Richard Bing.
References
^Konstantinov, Igor E. (2009). "Taussig-Bing Anomaly". Texas Heart Institute Journal. 36 (6): 580–585. ISSN 0730-2347. PMC 2801930. PMID 20069085.
^Ramrakha, Punit S.; Ramrakha, Punit; Hill, Jonathan (2012). Oxford Handbook of Cardiology. OUP Oxford. p. 707. ISBN 9780199643219.
External links
Classification
D
ICD-10: Q20.1
ICD-9-CM: 745.11
OMIM: 217095
MeSH: D004310
DiseasesDB: 32215
External resources
eMedicine: ped/2509 ped/2508
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Congenital heart defects (Q20–Q24, 745–746)
Cardiac shunt/ heart septal defect
Aortopulmonary septal defect
R→L: Double outlet right ventricle
Taussig–Bing syndrome
Transposition of the great vessels
dextro
levo
Persistent truncus arteriosus
Aortopulmonary window
Atrial septal defect
L→R: Sinus venosus atrial septal defect
Lutembacher's syndrome
Ventricular septal defect
L→R and R→L: Eisenmenger's syndrome
R→L, with other conditions: Tetralogy of Fallot
Atrioventricular septal defect
L→R: Ostium primum
Valvular heart disease/ heart chambers
Right
pulmonary valves
stenosis
insufficiency
absence
tricuspid valves
stenosis
atresia
Ebstein's anomaly
Hypoplastic right heart syndrome
Uhl anomaly
Left
aortic valves
stenosis
insufficiency
bicuspid
mitral valves
stenosis
regurgitation
Hypoplastic left heart syndrome
Other
Dextrocardia
Levocardia
Cor triatriatum
Crisscross heart
Brugada syndrome
Coronary artery anomaly
Anomalous aortic origin of a coronary artery
Ventricular inversion
This article about a medical condition affecting the circulatory system is a stub. You can help Wikipedia by expanding it.
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UpToDate Contents
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…evaluation of patients with symptoms suggestive of infiltration of the central nervous system (ie, Bing Neel syndrome) should include an assessment of the cerebral spinal fluid as well as magnetic resonance imaging …
…splenomegaly. Rarely, the plasmacytoid lymphocytes may infiltrate the central nervous system (ie, Bing-Neel syndrome) or meninges. During the course of their disease, patients with WM can develop symptoms …
… Branch pulmonary stenosis are a potential sequelae of prior Blalock-Thomas-Taussig shunts (commonly called Blalock-Taussig shunt) and both main and branch pulmonary stenosis may result from the arterial…
…catheterization or operation (eg, absent radial pulse in patients with prior Blalock-Thomas-Taussig shunt [commonly called Blalock-Taussig shunt]). Perioperative death related to cardiac reoperation is a significant…
…aspects of anesthetic management include: Blalock-Thomas-Taussig shunt – A classical Blalock-Thomas-Taussig shunt (also commonly called the Blalock-Taussig [BT] shunt) is a surgical connection between the subclavian …
English Journal
Sudden death in transposition of the great arteries with atrial switch surgery: Autopsy evidence of acute myocardial ischemia despite normal coronary arteries.
Chaix MA, Chergui M, Leduc C, Khairy P.
International journal of cardiology. 2019 Aug;288()65-67.
Sudden death is the leading cause of mortality in patients with transposition of the great arteries (TGA) and atrial switch surgery. Understanding underlying mechanisms could contribute to identifying high-risk patients and preventing such catastrophic deaths. A total of 144 adults (≥18 years) w
Anatomical correction of atrioventricular discordance using three-dimensional replica.
Fuchigami T, Nishioka M, Akashige T, Nakayashiro M, Nagata N.
General thoracic and cardiovascular surgery. 2019 Jun;67(6)554-557.
Surgical experience with {S,L,D} segmental anatomy of atrioventricular discordance with double-outlet right ventricle is extremely rare. In addition to ordinary cardiac examination, we reviewed electrophysiological studies and a three-dimensional cardiac replica (crossMedical, Inc., Kyoto, Japan). C
Criss-cross heart with double-outlet right ventricle, subpulmonary ventricular septal defect, and bicuspid pulmonary valve.
Ren S, Ma C, Li S.
Journal of clinical ultrasound : JCU. 2019 Jun;47(5)315-318.
Criss-cross heart (CCH) is an extremely rare complex congenital heart malformation. It accounts for less than 0.1% of congenital heart diseases. Here, we describe a unique case of CCH with double-outlet right ventricle, huge subpulmonary ventricular septal defect, bicuspid pulmonary valve, and right
A heart malformation known as Taussig-Bing anomaly (also called Taussig-Bing syndrome, heart, or malformation) consists of transposition of the aorta to the right ventricle and malposition of the pulmonary artery with ...
Looking for online definition of Taussig-Bing syndrome in the Medical Dictionary? Taussig-Bing syndrome explanation free. What is Taussig-Bing syndrome? Meaning of Taussig-Bing syndrome medical term. What does Taussig ...