sinus histiocytosis

洞組織球症

WordNet

1. commit a sin; violate a law of God or a moral law (同)transgress, trespass
2. violent and excited activity; "they began to fight like sin" (同)hell
3. estrangement from god (同)sinfulness, wickedness
4. an act that is regarded by theologians as a transgression of Gods will (同)sinning
5. the 21st letter of the Hebrew alphabet
6. any of various air-filled cavities especially in the bones of the skull
7. a blood disease characterized by an abnormal multiplication of macrophages

PrepTutorEJDIC

1. 〈U〉(宗教・道徳上の)『罪』 / 〈C〉(宗教・道徳上の)『罪の行為』,罪悪 / 〈C〉《特におどけて》違反(過失)の行為 / (宗教・道徳上の)おきてを破る,罪を犯す / (…に)違反(過失)をする,背く《+『against』+『名』》
2. sine
3. 洞(どう)(骨や組織の中の穴・くぼみなど);静脈洞

Wikipedia preview

出典(authority):フリー百科事典『ウィキペディア（Wikipedia）』「2015/04/25 23:10:06」(JST)

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Rosai-Dorfman disease
Micrograph of a lymph node involved by Rosai-Dorfman disease showing emperipolesis. H&E stain.
Classification and external resources
ICD-10	D76.3 (ILDS D76.360)
DiseasesDB	31419

Rosai–Dorfman disease, also known as sinus histiocytosis with massive lymphadenopathy, is a rare disorder of unknown etiology that is characterized by abundant histiocytes in the lymph nodes throughout the body.^,

Presentation

Lymphadenopathy of the neck is the most common place of histiocyte accumulation, although accumulation outside of lymph nodes may occur, as well. The most common sites of accumulation outside of the lymph nodes are skin, upper respiratory tract, and the sinuses. The disease can be also diagnosed in thyroid gland.

The symptoms of this disease vary with the site of accumulation similar to other regional tumors. For instance, accumulation in closed spaces such as the cranium can lead to poor outcomes compared to growth in the dermis of an extremity where surgical excision is possible.

The disease is usually non-progressive and self-limited, but patients can manifest autoimmune hemolytic anemia. It can rarely present with massive hemoptysis. Extra nodal sites such as skin, mucosae, spinal cord and pancreas may be involved.

History

This condition has been named after Ronald F. Dorfman and Juan Rosai. An alternative eponym of this condition is known as Destombes-Rosai-Dorfman syndrome, part of which is named after Pierre-Paul Louis Lucien Destombes.

See also

• List of cutaneous conditions

References

UpToDate Contents

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• 1. ランゲルハンス細胞組織球症の臨床症状、病理学的特徴、および診断 clinical manifestations pathologic features and diagnosis of langerhans cell histiocytosis
• 2. 小児における末梢のリンパ節腫脹 peripheral lymphadenopathy in children etiology
• 3. ランゲルハンス細胞組織球症の治療 treatment of langerhans cell histiocytosis
• 4. 鼻症状の原因：概要 etiologies of nasal symptoms an overview
• 5. 副鼻腔癌 paranasal sinus cancer

English Journal

• 18F-FDG PET/CT Follow-up of Rosai-Dorfman Disease.

• Albano D1, Bosio G, Bertagna F.
• Clinical nuclear medicine.Clin Nucl Med.2015 Aug;40(8):e420-2. doi: 10.1097/RLU.0000000000000853.
• Rosai-Dorfman disease (RDD) or sinus histiocytosis is a rare histiocytic disorder characterized by massive lymphadenopathy and with extranodal involvement in 25% to 43% of cases. The clinical course of RDD is unpredictable with episodes of exacerbation and remissions that can last many years, and tr
• PMID 26053720

• Rosai-Dorfman disease with atypical intrascrotal involvement.

• Rodríguez Torres C1, Riazuelo Fantova G1, Escartín Martínez I1, Castillo Escudero JJ1, Del Agua Arias C2.
• International journal of urology : official journal of the Japanese Urological Association.Int J Urol.2015 Aug;22(8):794-6. doi: 10.1111/iju.12805. Epub 2015 May 18.
• We describe two new cases of Rosai-Dorfman disease with intrascrotal involvement. Also known as sinus histiocytosis with massive lymphadenopathy, this is a rare entity, usually presenting with massive bilateral cervical lymphadenopathy. It is associated with extranodal involvement in up to 40% of ca
• PMID 25988924

• An unusual presentation of extranodal Rosai-Dorfman disease threatening the airway.

• Swain SK1, Das A2, Sahoo S3, Baisakh MR4, Sahu MC5.
• Auris, nasus, larynx.Auris Nasus Larynx.2015 Jul 15. pii: S0385-8146(15)00165-0. doi: 10.1016/j.anl.2015.06.007. [Epub ahead of print]
• Rosai-Dorfman disease (RDD) is a rare benign systemic histiocytic proliferation, characterized by massive lymph node enlargement and sometimes associated with extranodal involvement. Even though it is considered as a benign disease, fatalities can occur due to its unusually large size and its locati
• PMID 26188562

Japanese Journal

• 症例報告 皮膚Rosai-Dorfman病の1例

• 佐藤 真美,植田 郁子,南 路子 [他]
• 臨床皮膚科 68(2), 155-159, 2014-02
• NAID 40019973306

• ランゲルハンス細胞組織球症117例の臨床像と長期予後および画像所見の特徴について

• 塩田 曜子,中澤 温子,宮嵜 治 [他],恒松 由記子,大澤 真木子
• 東京女子医科大学雑誌 83(E1), E178-E193, 2013-01-31
• … 類似した画像所見を呈した良性の病態として Dermoid cyst、Infantile hemangioma、Sinus pericranii、Arachnoid granulation、Fibrous dysplasiaが経験され、発症部位や慢性の経過を示す辺縁の骨硬化の有無などがLCHとの鑑別点となった。 …
• NAID 110009559395

• 症例報告 皮膚Rosai-Dorfman病の1例

• 池田 大志,高橋 玲子,箭原 弘典 [他]
• 臨床皮膚科 66(11), 904-908, 2012-10
• NAID 40019456995

Related Links

• Sinus histiocytosis | definition of sinus histiocytosis by ...

sinus histiocytosis A nonspecific term for an increase in benign histiocytes in peripheral and medullary sinuses of lymph nodes. Aetiology Reaction to tumours or ... Disclaimer All content on this website, including dictionary ...

• What is Sinus Histiocytosis? (with pictures)

Sinus histiocytosis is a rare condition in which a person's lymph nodes accumulate a specific type of cell. Though there is no... ... Sinus histiocytosis with massive lymphadenopathy (SHML) is also called Rosai-Dorfman disease ...

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★リンクテーブル★

リンク元

「洞組織球症」

「洞組織球症」

　　[★]

英

sinus histiocytosis

関

ロザイ・ドルフマン病