成年性浮腫性硬化症
WordNet
- a skin disease marked by hard edema of the tissue usually beginning in the face
Wikipedia preview
出典(authority):フリー百科事典『ウィキペディア(Wikipedia)』「2015/02/19 09:46:31」(JST)
[Wiki en表示]
Not to be confused with Scleroderma.
Scleredema |
Classification and external resources |
ICD-10 |
M34.8, P83.0 |
DiseasesDB |
31361 |
eMedicine |
article/1066175 |
MeSH |
D012592 |
Scleredema, also known as Buschke disease, scleredema of Buschke, and scleredema adultorum,[1][2] is a rare, self-limiting skin condition defined by progressive thickening and hardening of the skin, usually on the areas of the upper back, neck, shoulders and face.[3] The skin may also change color to red or orange. The disease was discovered by Abraham Buschke. Although the cause of scleredema is unknown, it is usually associated with a disease, usually diabetes,[4] a viral illness or strep throat.[5] It is usually not fatal, but it may cause death if the disease spreads to the internal organs.[3] It may also cause an infection.[5]
Contents
- 1 Diagnosis
- 2 Treatment
- 3 See also
- 4 References
Diagnosis
The scleredema is usually proposed as a diagnosis based on the appearance of the skin and the patient's medical history. To confirm the diagnosis, the doctor performs a skin biopsy, in which hematoxylin and eosin staining will show a thick reticular dermis with thick collagen bundles separated by clear spaces.[6] The patient's blood may be examined for diseases that may appear after the onset of symptoms, such as multiple myeloma.[5]
Treatment
Although many types of medications have been tried as treatments, none of them have been proven effective in treating scleredema. Those treatments, such as corticosteroids, may benefit the patient, but will not cure their condition. If the affected area is infected, it is usually treated immediately. The symptoms of the condition usually resolve within six months to two years after onset. However, patients whose condition was associated to diabetes may suffer for longer periods of time.[5]
Myocarditis resulting as a complication from the disease has been successfully treated with penicillin and steroids.[7]
See also
References
- ^ Turchin I, Adams SP, Enta T (September 2003). "Dermacase. Scleredema adultorum, or Bushke disease". Can Fam Physician 49: 1089, 1093. PMC 2214291. PMID 14526859.
- ^ Pegum JS (June 1972). "Scleredema of Buschke". Proc. R. Soc. Med. 65 (6): 528. PMC 1643957. PMID 5044976.
- ^ a b "Scleredema". Retrieved 2009-05-18.
- ^ Meguerditchian, C; Jacquet P, Béliard S et al. (November 2006). "Scleredema adultorum of Buschke: an under recognized skin complication of diabetes". Diabetes and Metabolism 32 (5): 481–484. doi:10.1016/S1262-3636(07)70307-5. PMID 17110904.
- ^ a b c d "Scleredema". Retrieved 2009-05-18.
- ^ Schmults CA (October 2003). "Scleredema". Dermatol. Online J. 9 (4): 11. PMID 14594584.
- ^ "Buschke's Sclerema with right-sided heart failure.". Retrieved 2009-05-18.
UpToDate Contents
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English Journal
- Neck Pain, Stiffness, and Periorbital Edema in a Man With Diabetes.
- Chatterjee S1.
- JAMA.JAMA.2016 Mar 15;315(11):1159-60. doi: 10.1001/jama.2016.1770.
- PMID 26978211
- A case of scleredema adultorum successfully treated with narrow-band ultraviolet B phototherapy.
- Yoshimura J1, Asano Y1, Takahashi T1, Uwajima Y1, Kagami S1, Honda H2, Idezuki T2, Igarashi A2, Sato S1.
- Modern rheumatology / the Japan Rheumatism Association.Mod Rheumatol.2016 Mar;26(2):302-6. doi: 10.3109/14397595.2013.875640. Epub 2014 Feb 5.
- Scleredema adultorum, also known as scleredema of Buschke, is a rare connective tissue disease with unknown etiology, which is characterized by diffuse skin induration of face, neck, upper chest, back, shoulders and arms. Although there is no established treatment for this disease, the efficacy of p
- PMID 24499427
- Scleredema adultorum of Buschke with prominent periorbital edema in a Tunisian patient with diabetes mellitus: a case report.
- Mohamed M1, Belhadjali H1, Béchir AB1, Moussa A2, Zili J1.
- International journal of dermatology.Int J Dermatol.2016 Feb;55(2):e100-2. doi: 10.1111/ijd.13128. Epub 2015 Nov 4.
- PMID 26536602
Japanese Journal
- Scleredema adultorum treated with narrow-band ultraviolet B phototherapy
- XIAO Ting,YANG Zhen-Hai,HE Chun-Di,CHEN Hong-Duo
- Journal of dermatology 34(4), 270-272, 2007-04-01
- NAID 10020116214
- Successful UVA1 phototherapy in a patient with scleredema adultorum
- EBERLEIN-KONIG B
- J Eur Acad Dermatol Venereol 19, 203-204, 2005
- NAID 30010612483
- Scleredema adultorum due to streptococcal infection
- ALP HANDAN,ORBAK ZERRIN,AKTAS AKIN
- Pediatrics international : official journal of the Japan Pediatric Society 45(1), 101-103, 2003-02-01
- NAID 10011916778
Related Links
- Scleredema adultorum information including symptoms, diagnosis, misdiagnosis, treatment, causes, patient stories, videos, forums, prevention, and prognosis. ... Scleredema adultorum: Introduction Scleredema adultorum: A rare ...
- scleredema adultorum scleredema ad·ul·to·rum (ād'ŭl-tôr'əm) n. A benign spreading induration of the skin and subcutaneous tissue, possibly streptococcal in origin.
Related Pictures
![occasionally called scleredema adultorum](https://1mg.info/0/g/1/2320.jpg)
![Scleredema](https://1mg.info/0/g/1/2321.jpg)
![scleredema adultorum is a rare self](https://1mg.info/0/g/1/2322.jpg)
![Scleredema Adultorum](https://1mg.info/0/g/1/2323.jpg)
![Scleredema adultorum](https://1mg.info/0/g/1/2324.jpg)
★リンクテーブル★
[★]
- 英
- benigns scleredema of adult
- ラ
- scleredema adultorum, scleredema adultorum Buschke
- 関
- 浮腫性硬化症