パラ血友病、血友病類似症
- 関
- factor V deficiency
- 関
- coagulation factors, fac tor V deficiency
English Journal
- Platelets and platelet-derived factor Va confer hemostatic competence in complete factor V deficiency.
- Bouchard BA1, Chapin J1, Brummel-Ziedins KE1, Durda P2, Key NS3, Tracy PB1.
- Blood.Blood.2015 Jun 4;125(23):3647-50. doi: 10.1182/blood-2014-07-589580. Epub 2015 Apr 20.
- Whole genome sequencing of an individual completely devoid of plasma- and platelet-derived factor V (FV) identified 167 variants in his F5 gene including previously identified and damaging missense mutations at rs6027 and Leu90Ser. Because the administration of fresh frozen plasma (FFP) prevents gas
- PMID 25896652
- Recurrent hemoperitoneum secondary to haemorrhage from the corpus luteum unmasks factor V deficiency.
- Badyal RK1, Jain K, Mandrelle K, John MJ, Kakkar N, Bose SK, Kumar N, Ahluwalia J.
- Blood coagulation & fibrinolysis : an international journal in haemostasis and thrombosis.Blood Coagul Fibrinolysis.2015 Apr 17. [Epub ahead of print]
- Factor V deficiency is a rare autosomal recessive coagulation disorder. We report a case with inherited factor V deficiency presenting as life-threatening recurrent hemoperitoneum, following bleeding from ruptured corpus haemorrhagicum. Prolonged prothrombin and activated partial thromboplastin time
- PMID 25886835
- Acquired factor V deficiency in myeloproliferative neoplasms: a Mayo Clinic series of 33 patients.
- Ashrani AA1, Tefferi A, Pruthi RK, Pardanani A.
- British journal of haematology.Br J Haematol.2015 Apr 8. doi: 10.1111/bjh.13438. [Epub ahead of print]
- PMID 25854415
Japanese Journal
- 坂田 好史,三島 秀雄,山口 和哉,平林 直樹
- 日本消化器外科学会雑誌 36(11), 1626-1629, 2003-11-01
- 症例は71歳の女性で.1999年4月頃から近医で貧血症と便潜血陽性を指摘され当科へ紹介された.両親がいとこ同士の結婚であった.注腸造影検査で肝彎曲部に陰影欠損像を認めた.大腸内視鏡検査では肝彎曲節に1型腫瘍を認めた.入院時検査所見ではプロトロンビン時間(PT)22.8秒(23.5%),活性化部分トロンボプラステン時間(APTT)58.1秒と延長していた.出血時間は2分,ヘパプラスチンテストは98. …
- NAID 110001294749
- A Case of Colon Cancer with Congenital Factor V Deficiency
- 坂田 好史,三島 秀雄,山口 和哉,平林 直樹
- 日本消化器外科学会雑誌 36(11), 1626-1629, 2003
- … We found the patient had congenital factor V deficiency (parahemophilia), so we transfused 6 units of fresh frozen plasma (FFP) preoperatively to improve PT and APTT. …
- NAID 130004343876
- 先天性第5因子欠之症(Parahemophilia)の1例
Related Links
- parahemophilia par·a·he·mo·phil·i·a (pār'ə-hē'mə-fĭl'ē-ə, -fēl'yə) n. A congenital deficiency of factor V characterized by abnormally slow blood coagulation. Also called Owren's disease.
- parahemophilia [par″ah-he″mo-fil´e-ah] a hereditary hemorrhagic tendency due to deficiency of coagulation factor V. Called also Owren's disease. See also clotting. parahemophilia /para·he·mo·phil·ia/ (-he″mo-fil´e-ah) a hereditary ...
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- 英
- parahemophilia
- 関
- 血友病類似症
-先天性第V因子欠乏症
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- 英
- parahemophilia
- 関
- 第V因子欠乏症、パラ血友病