WordNet
- the univalent radical CH3- derived from methane (同)methyl_group, methyl radical
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English Journal
- The first case in Asia of 2-methyl-3-hydroxybutyryl-CoA dehydrogenase deficiency (HSD10 disease) with atypical presentation.
- Fukao T1, Akiba K2, Goto M3, Kuwayama N4, Morita M4, Hori T4, Aoyama Y5, Venkatesan R6, Wierenga R6, Moriyama Y7, Hashimoto T7, Usuda N7, Murayama K8, Ohtake A9, Hasegawa Y10, Shigematsu Y11, Hasegawa Y3.
- Journal of human genetics.J Hum Genet.2014 Nov;59(11):609-14. doi: 10.1038/jhg.2014.79. Epub 2014 Sep 18.
- 2-Methyl-3-hydroxybutyryl-CoA dehydrogenase (2M3HBD) deficiency (HSD10 disease) is a rare inborn error of metabolism, and <30 cases have been reported worldwide. This disorder is typically characterized by progressive neurodegenerative disease from 6 to 18 months of age. Here, we report the first
- PMID 25231369
- NADPH-dependent reductive biotransformation with Escherichia coli and its pfkA deletion mutant: influence on global gene expression and role of oxygen supply.
- Siedler S1, Bringer S, Polen T, Bott M.
- Biotechnology and bioengineering.Biotechnol Bioeng.2014 Oct;111(10):2067-75. doi: 10.1002/bit.25271. Epub 2014 Jun 4.
- An Escherichia coli ΔpfkA mutant lacking the major phosphofructokinase possesses a partially cyclized pentose phosphate pathway leading to an increased NADPH per glucose ratio. This effect decreases the amount of glucose required for NADPH regeneration in reductive biotransformations, such as the c
- PMID 24771245
- Metabolic encephalopathy in beta-ketothiolase deficiency: the first report from India.
- Akella RR1, Aoyama Y2, Mori C3, Lingappa L1, Cariappa R4, Fukao T5.
- Brain & development.Brain Dev.2014 Jun;36(6):537-40. doi: 10.1016/j.braindev.2013.07.007. Epub 2013 Aug 16.
- Beta-ketothiolase deficiency, or mitochondrial acetoacetyl-CoA thiolase (T2) deficiency, is a rare autosomal recessive disorder affecting isoleucine catabolism and ketone body metabolism. A patient from South India presented with acute ketoacidosis at 11 months of age. During the acute crisis the C5
- PMID 23958592
Japanese Journal
- Purification and Properties of an Asymmetric Reduction Enzyme of 2-Methyl-3-oxobutyrate in Bakers Yeast
- FURUICHI Akiya,AKITA Hiroyuki,MATSUKURA(nee KOSHIJI) Hiroko,OISHI Takeshi,HORIKOSHI Koki
- Agricultural and Biological Chemistry 49(9), 2563-2570, 1985
- … The benzyl 2-methyl-3-hydroxybutyrate dehydrogenase was purified from the cells of bakers yeast by streptomycin treatment, Sephadex G-50 gel filtration, SP-Sephadex C-50 chromatography, and Toyopearl HW-60F gel filtration. …
- NAID 130000026064
Related Links
- Methyl (R)-3-hydroxybutyrate 99% SDS Similar Products CAS Number 3976-69-0 Linear Formula CH 3 CH(OH)CH 2 CO 2 CH 3 Molecular Weight 118.13 Beilstein Registry Number 3648161 EC Number 223-610-0 Peer-Reviewed ...
- Beil. 3,III,569 Aldrich MSDS 1, 1259:D / Corp MSDS 1 (2), 2365:D / FT-IR 1 (1), 660:D / FT-IR 2 (1), 1082:D / FT-NMR 1 (1), 1036:B / NMR-Reference 2 (1), 557:B / ... Technical Service: Our team of scientists has experience in all ...
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