良性家族性好中球減少症
WordNet
- not dangerous to health; not recurrent or progressive (especially of a tumor)
- pleasant and beneficial in nature or influence; "a benign smile"; "the benign sky"; "the benign influence of pure air" (同)benignant
- kindness of disposition or manner; "the benign ruler of millions"; "benign intentions"
- relating to or having the characteristics of a family; "children of the same familial background"; "familial aggregation"
- occurring among members of a family usually by heredity; "an inherited disease"; "familial traits"; "genetically transmitted features" (同)genetic, hereditary, inherited, transmitted, transmissible
- leukopenia in which the decrease is primarily in number of neutrophils (the chief phagocytic leukocyte)
PrepTutorEJDIC
- (心・表情などが)親切な,優しい / (事情・環境・気候などが)好適な,好都合な / 悪性でない
- 家族の,家族特有の / 違伝的な,血統にあらわれる
UpToDate Contents
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English Journal
- [Peripheral neuropathy, myelopathy, cerebellar ataxia, and subclinical optic neuropathy associated with copper deficiency occurring 23 years after total gastrectomy].
- Inaba M1, Torii T, Shinoda K, Yamasaki R, Ohyagi Y, Kira J.
- Rinshō shinkeigaku = Clinical neurology.Rinsho Shinkeigaku.2011 Jun;51(6):412-6.
- We report a 61-year-old man with slowly progressive gait disturbance and paresthesia in the lower extremities following a total gastrectomy for gastric cancer 23 years previously. The patient presented with hyperreflexia, peripheral sensory neuropathy, and cerebellar ataxia. Magnetic resonance imagi
- PMID 21735733
- Case report of a family with benign familial neutropenia and the implications for the general dental practitioner.
- Casey C1, Brooke T, Davies R, Franklin D.
- Dental update.Dent Update.2011 Mar;38(2):106-8, 110.
- Benign familial neutropenia (BFN) is a condition where there is a decrease in circulating neutrophils in the blood and patients suffer from oral manifestations which include: persistant periodontal disease, recurrent neutropenic ulceration and candidal infections. This report discusses a family affe
- PMID 21500620
- Detection of anti-neutrophil antibodies in autoimmune neutropenia of infancy: a multicenter study.
- Sella R1, Flomenblit L, Goldstein I, Kaplinsky C.
- The Israel Medical Association journal : IMAJ.Isr Med Assoc J.2010 Feb;12(2):91-6.
- BACKGROUND: Autoimmune neutropenia of infancy is caused by neutrophil-specific autoantibodies. Primary AIN is characterized by neutrophil count < 500 ml and a benign self-limiting course. Detecting specific antibodies against the polymorphic human neutrophil antigen usually confirms the diagnosis
- PMID 20550032
Japanese Journal
- 壊疽性膿瘡を合併した先天性好中球減少症に対するrhG-CSFの治療効果
- 柴田 優,窪田 容子,橋本 和子,吉田 裕慈,今中 康文,高橋 幸博,佐道 俊幸,島本 太香子,下山 丈人,藤村 吉博,大野 治彦,吉岡 章
- 日本小児血液学会雑誌 10(1), 46-50, 1996-02-29
- NAID 10012225257
- Successful Treatment of Ecthyma Gangrenosum in a Neonate with Congenital Neutropenia using Recombinant Human Granulocyte Colony Stimulating Factor.
- 柴田 優,窪田 容子,橋本 和子,吉田 裕慈,今中 康文,高橋 幸博,佐道 俊幸,島本 太香子,下山 丈人,藤村 吉博,大野 治彦,吉岡 章
- 日本小児血液学会雑誌 10(1), 46-50, 1996
- … Using the recombinant human granulocyte colony stimulating factor (rhG-CSF), ecthyma gangrenosum in a neonate with congenital neutropenia was successfully treated. … He had severe neutropenia (200/, μl), and was treated with rhG-CSF in combination with intensive antibiotics. … His mother also had had moderate neutropenia (200-500/μl) for a long time without severe infections. …
- NAID 130004117831
- Oral features of a family with benign familial neutropenia
Related Links
- References 1) Bernini JC. Diagnosis and management of chronic neutropenia during childhood. Pediatr Clin North Am 1996;43:773–792. 2) Cutting HO, Lang JE. Familial benign chronic neutropenia. Blood 1964;61:876–887. 3) Holmes ...
- ABSTRACT Benign hereditary leukopenia-neutropenia has been reported in several ethnic groups, including Yemenite Jews, Blacks of South African extraction, West Indians and Arab Jordanians. The subjects with BFL were shown ...
★リンクテーブル★
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- 英
- benign familial neutropenia
- 同
- 家族性良性慢性好中球減少症 familial benign chronic neutropenia
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- 関
- family、family member、household、kindred
[★]
- 関
- benignant、mild、mildly