出典: meddic

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  • Pharmacokinetics and Pharmacodynamics of Afamelanotide and its Clinical Use in Treating Dermatologic Disorders.
  • Minder EI1, Barman-Aksoezen J2, Schneider-Yin X2.
  • Clinical pharmacokinetics.Clin Pharmacokinet.2017 Aug;56(8):815-823. doi: 10.1007/s40262-016-0501-5.
  • PMID 28063031
  • Cimetidine/lactulose therapy ameliorates erythropoietic protoporphyria-related liver injury.
  • Fujimori N1, Komatsu M1, Tanaka N2, Iwaya M3, Nakano H4, Sugiura A1, Yamazaki T1, Shibata S1, Iwaya Y1, Muraki T1, Ichikawa Y1, Kimura T1, Joshita S1, Umemura T1, Matsumoto A1, Tanaka E1.
  • Clinical journal of gastroenterology.Clin J Gastroenterol.2017 Jul 4. doi: 10.1007/s12328-017-0760-1. [Epub ahead of print]
  • PMID 28676994
  • Clinical, Biochemical, and Genetic Characterization of North American Patients With Erythropoietic Protoporphyria and X-linked Protoporphyria.
  • Balwani M1, Naik H1, Anderson KE2, Bissell DM3, Bloomer J4, Bonkovsky HL5, Phillips JD6, Overbey JR7, Wang B3, Singal AK4, Liu LU8, Desnick RJ1.
  • JAMA dermatology.JAMA Dermatol.2017 Jun 14. doi: 10.1001/jamadermatol.2017.1557. [Epub ahead of print]
  • PMID 28614581



Erythropoietic protoporphyria (EPP) is a relatively mild form of porphyria, although very painful, which arises from a deficiency in the enzyme ferrochelatase, leading to abnormally high levels of protoporphyrin in the tissue. : 525 The severity ...
20 Jun 2012 ... Protoporphyria. The term protoporphyria now encompasses 2 clinically similar but distinct disorders that most often result from hereditary mutations in 2 different genes.


Erythropoietic protoporphyriaالترجمة الفورية للصفحةErythropoietic protoporphyriaprotoporphyria of blood porphyriaErythropoietic protoporphyriaErythropoietic protoporphyria